2026 ICD-10-CM Diagnosis Code Q99.811Usher syndrome, type 1

ICD-10-CM Codes›Q00-Q99›Q90-Q99›Q99

ICD-10-CM Q99.811
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q99.811 is a billable ICD-10-CM diagnosis code for usher syndrome, type 1. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting.

Code Identity

ICD-10-CM Code
Q99.811
Billable Status
Yes — Valid for Submission
Code Describes
Usher syndrome, type 1
Short Description
Usher syndrome, type 1
Same as the full description in the CMS dataset.
Parent Code
Q99.81
Usher syndrome

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ90-Q99Chromosomal abnormalities, not elsewhere classified
CategoryQ99Other chromosome abnormalities, not elsewhere classified
This CodeQ99.811Usher syndrome, type 1

Present on Admission (POA)Billing

Q99.811 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Syndrome
      • usher
        • type 1

Clinical InformationClinical

  • Usher Syndrome Type 1

    a syndrome characterized by congenital, bilateral, severe sensorineural hearing loss, abnormalities in the vestibular system, and adolescent-onset retinitis pigmentosa.

Code History & ChangesHistory

New Code Q99.811 was added to the ICD-10-CM code set for FY 2026, effective October 1, 2025.

Replacement Q99.811 replaces the following previously assigned code(s):

  • Q99.8 - Other specified chromosome abnormalities
FY 2026AddedAdded to the ICD-10-CM code setEffective October 1, 2025.
FY 2026CurrentRevised in the current code setEffective October 1, 2025 through September 30, 2026.

Questions About Q99.811Overview

Is Q99.811 (Usher syndrome) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report usher syndrome, type 1 on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q99.811 group to?

When usher syndrome, type 1 is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q99.811 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for usher syndrome, type 1 on inpatient claims.