2026 ICD-10-CM Diagnosis Code Q87.5Other congenital malformation syndromes with other skeletal changes

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q87

ICD-10-CM Q87.5
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q87.5 is a billable ICD-10-CM diagnosis code for other congenital malformation syndromes with other skeletal changes. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q87.5
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital malformation syndromes with other skeletal changes
Short Description
Oth congenital malformation syndromes w oth skeletal changes
Parent Code
Q87
Other specified congenital malformation syndromes affecting multiple systems

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ87Other specified congenital malformation syndromes affecting multiple systems
This CodeQ87.5Other congenital malformation syndromes with other skeletal changes

Present on Admission (POA)Billing

Q87.5 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • 3-M syndrome
  • Acromegaloid phenotype with cutis verticis gyrata and corneal leukoma
  • Anophthalmia and megalocornea with cardiopathy and skeletal anomalies syndrome
  • Antley-Bixler syndrome
  • Arachnodactyly
  • Arachnodactyly with abnormal ossification and intellectual disability syndrome
  • Autosomal recessive distal osteolysis syndrome
  • Baller-Gerold syndrome
  • Beemer Ertbruggen syndrome
  • BRESEK syndrome
  • Cardiospondylocarpofacial syndrome
  • CLOVE syndrome
  • Combined immunodeficiency with faciooculoskeletal anomalies syndrome
  • Conductive deafness, ptosis, skeletal anomalies syndrome
  • Congenital abnormal fusion of humerus
  • Congenital abnormal shape of clavicle
  • Congenital anomaly of subcutaneous tissue
  • Congenital atresia of external auditory canal
  • Congenital atrophy of optic nerve
  • Congenital bowing of femur
  • Congenital corneal leukoma
  • Congenital deformity of clavicle
  • Congenital deformity of shoulder
  • Congenital dysplasia of radius
  • Congenital insufficiency of mitral valve
  • Corneal leukoma
  • Cutis verticis gyrata
  • Dacryocystitis and osteopoikilosis syndrome
  • FG syndrome
  • Humeroradial synostosis
  • Idiopathic osteolyses
  • Intellectual disability, seizures, hypotonia, ophthalmologic, skeletal anomalies syndrome
  • Jarcho-Levin syndrome
  • Male hypergonadotropic hypogonadism, intellectual disability, skeletal anomaly syndrome
  • Mandibuloacral dysostosis
  • Mandibuloacral dysplasia with type A lipodystrophy
  • Mandibuloacral dysplasia with type B lipodystrophy
  • Metaphyseal dysostosis, intellectual disability, conductive deafness syndrome
  • Multicentric carpotarsal osteolysis syndrome
  • Osteopoikilosis
  • Otopalatodigital syndrome spectrum disorder
  • Otospondylomegaepiphyseal dysplasia
  • Parieto-occipital craniosynostosis
  • Primary testicular failure
  • Retinal pigment epithelial dystrophy
  • Richieri Costa-da Silva syndrome
  • Saldino-Mainzer dysplasia
  • Scalp defect postaxial polydactyly syndrome
  • Short stature, auditory canal atresia, mandibular hypoplasia, skeletal anomalies syndrome
  • Spondylodysplasia
  • Stenosis of lacrimal canaliculi
  • X-linked intellectual disability, craniofacioskeletal syndrome

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Malformation(congenital)
      • affecting multiple systems with skeletal changes NEC

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Arachnodactyly

    an abnormal bone development that is characterized by extra long and slender hands and fingers, such that the clenched thumb extends beyond the ulnar side of the hand. arachnodactyly can include feet and toes. arachnodactyly has been associated with several gene mutations and syndromes.

  • Osteopoikilosis

    an asymptomatic, autosomal dominant trait in which pea-sized sclerotic spots, prominent in the metaphyseal area, are accompanied by unique cutaneous lesions. these are yellowish papules or plaques with increased elastin content. (from cecil textbook of medicine, 19th ed, pp1434-35)

  • Osteopoikilosis

    a rare autosomal dominant inherited disorder characterized by the presence of small areas of increased density throughout the bones.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q87.5 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.89 Specfied cong anomal NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q87.5Overview

Is Q87.5 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformation syndromes with other skeletal changes on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q87.5 group to?

When other congenital malformation syndromes with other skeletal changes is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q87.5 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformation syndromes with other skeletal changes on inpatient claims.

What is the ICD-9 equivalent of Q87.5?

Under the General Equivalence Mappings, other congenital malformation syndromes with other skeletal changes converts to ICD-9-CM 759.89 (specfied cong anomal NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.