2027 ICD-10-CM Diagnosis Code Q87.5Other congenital malformation syndromes with other skeletal changes
ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q87
- Billable — Valid for Submission
- CC — Complication or Comorbidity
- POA Exempt
- Chronic Condition
Q87.5 is a billable ICD-10-CM diagnosis code for other congenital malformation syndromes with other skeletal changes. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 46 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q87.5 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations (Q80-Q89).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- 3-M syndrome
- Acromegaloid phenotype with cutis verticis gyrata and corneal leukoma
- Anophthalmia and megalocornea with cardiopathy and skeletal anomalies syndrome
- Antley-Bixler syndrome
- Arachnodactyly
- Arachnodactyly with abnormal ossification and intellectual disability syndrome
- Autosomal recessive distal osteolysis syndrome
- Baller-Gerold syndrome
- Beemer Ertbruggen syndrome
- BRESEK syndrome
- Cardiospondylocarpofacial syndrome
- CLOVE syndrome
- Combined immunodeficiency with faciooculoskeletal anomalies syndrome
- Conductive deafness, ptosis, skeletal anomalies syndrome
- Congenital abnormal fusion of humerus
- Congenital abnormal shape of clavicle
- Congenital anomaly of subcutaneous tissue
- Congenital atresia of external auditory canal
- Congenital atresia of external ear
- Congenital atrophy of optic nerve
- Congenital bowing of femur
- Congenital corneal leukoma
- Congenital deformity of clavicle
- Congenital deformity of shoulder
- Congenital dysplasia of radius
- Congenital insufficiency of mitral valve
- Corneal leukoma
- Cutis verticis gyrata
- Dacryocystitis and osteopoikilosis syndrome
- FG syndrome
- Humeroradial synostosis
- Idiopathic osteolysis
- Intellectual disability, seizures, hypotonia, ophthalmologic, skeletal anomalies syndrome
- Jarcho-Levin syndrome
- Male hypergonadotropic hypogonadism, intellectual disability, skeletal anomaly syndrome
- Mandibuloacral dysostosis
- Mandibuloacral dysplasia associated to MTX2
- Mandibuloacral dysplasia with type A lipodystrophy
- Mandibuloacral dysplasia with type B lipodystrophy
- Metaphyseal dysostosis, intellectual disability, conductive deafness syndrome
- Multicentric carpotarsal osteolysis syndrome
- Osteopoikilosis
- Otopalatodigital syndrome spectrum disorder
- Otospondylomegaepiphyseal dysplasia
- Parieto-occipital craniosynostosis
- Primary testicular failure
- Retinal pigment epithelial dystrophy
- Richieri Costa-da Silva syndrome
- Saldino-Mainzer dysplasia
- Scalp defect postaxial polydactyly syndrome
- Short stature, auditory canal atresia, mandibular hypoplasia, skeletal anomalies syndrome
- Spondylodysplasia
- Stenosis of lacrimal canaliculi
- X-linked intellectual disability, craniofacioskeletal syndrome
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q87.5: its own notes plus those printed at Q87 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Use Additional Code
Add a second code, after this one, to fully describe the condition.
- code(s) to identify all associated manifestations
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q87.5, its category, or a range that includes it.
Excludes1 3
These codes carry an Excludes1 note naming Q87.5: they are not reported together with it, unless the two conditions are unrelated.
- Q67 Congenital musculoskeletal deformities of head, face, spine and chestcongenital malformation syndromes classified to Q87.- names Q87.-, which includes this code
- Q75 Other congenital malformations of skull and face bonescongenital malformation syndromes classified to Q87.- names Q87.-, which includes this code
- Q89.7 Multiple congenital malformations, not elsewhere classifiedcongenital malformation syndromes affecting multiple systems (Q87.-) names Q87.-, which includes this code
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Malformation (congenital) See Also: Anomaly;
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
The full article covers:
- What are birth defects?
- What causes birth defects?
- Who is at risk of having a baby with birth defects?
- How are birth defects diagnosed?
- What are the treatments for birth defects?
- Can birth defects be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q87.5 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q87.5Overview
What is the ICD-10 code for other congenital malformation syndromes with other skeletal changes?
The ICD-10-CM code for other congenital malformation syndromes with other skeletal changes is Q87.5 (sometimes written as Q875). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q87.5 a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report other congenital malformation syndromes with other skeletal changes on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q87.5 group to?
When other congenital malformation syndromes with other skeletal changes is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q87.5 a CC or MCC?
CMS lists Q87.5 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 46 closely related codes in its exclusion list.
Is Q87.5 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for other congenital malformation syndromes with other skeletal changes on inpatient claims. The code appears in the Other congenital malformations (Q80-Q89) range of the CMS exempt list.