2026 ICD-10-CM Diagnosis Code Q87.43Marfan syndrome with skeletal manifestation

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q87

ICD-10-CM Q87.43
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q87.43 is a billable ICD-10-CM diagnosis code for marfan syndrome with skeletal manifestation. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 306 through 307. The code is exempt from POA reporting. Coders also document this condition as arachnodactyly. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q87.43
Billable Status
Yes — Valid for Submission
Code Describes
Marfan syndrome with skeletal manifestation
Short Description
Marfan syndrome with skeletal manifestation
Same as the full description in the CMS dataset.
Parent Code
Q87.4
Marfan syndrome

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ87Other specified congenital malformation syndromes affecting multiple systems
This CodeQ87.43Marfan syndrome with skeletal manifestation

Present on Admission (POA)Billing

Q87.43 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Arachnodactyly
  • Congenital contractural arachnodactyly
  • Congenital dolichostenomelia
  • Disorder of skeletal system co-occurrent and due to Marfan syndrome
  • Hypermobility syndrome
  • Laxity of ligament
  • Marfanoid joint hypermobility syndrome
  • Marfan's syndrome

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Syndrome
      • Marfan
        • with
          • skeletal manifestations

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Arachnodactyly

    an abnormal bone development that is characterized by extra long and slender hands and fingers, such that the clenched thumb extends beyond the ulnar side of the hand. arachnodactyly can include feet and toes. arachnodactyly has been associated with several gene mutations and syndromes.

Patient EducationClinical

Marfan Syndrome

Marfan syndrome is a disorder that affects connective tissue. Connective tissues are proteins that support skin, bones, blood vessels, and other organs. One of these proteins is fibrillin. A problem with the fibrillin gene causes Marfan syndrome.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q87.43 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.82 Marfan syndrome
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2023No changes
FY 2024RevisedCode revised
FY 2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q87.43Overview

Is Q87.43 (Marfan syndrome) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report marfan syndrome with skeletal manifestation on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q87.43 group to?

When marfan syndrome with skeletal manifestation is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9132 to 1.5758 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q87.43 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for marfan syndrome with skeletal manifestation on inpatient claims.

What is the ICD-9 equivalent of Q87.43?

Under the General Equivalence Mappings, marfan syndrome with skeletal manifestation converts to ICD-9-CM 759.82 (marfan syndrome). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.