2026 ICD-10-CM Diagnosis Code Q87.42Marfan syndrome with ocular manifestations
ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q87
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q87.42 is a billable ICD-10-CM diagnosis code for marfan syndrome with ocular manifestations. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 306 through 307. The code is exempt from POA reporting. Coders also document this condition as disorder of eye co-occurrent and due to Marfan syndrome. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q87.42 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Disorder of eye co-occurrent and due to Marfan syndrome
- Marfan's syndrome
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- Syndrome - See Also: Disease;
- with
- ocular manifestations - Q87.42
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Syndrome
- Marfan
- with
- ocular manifestations
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Marfan Syndrome
an autosomal dominant disorder of connective tissue with abnormal features in the heart, the eye, and the skeleton. cardiovascular manifestations include mitral valve prolapse; aortic aneurysm; and aortic dissection. other features include lens displacement (ectopia lentis), disproportioned long limbs and enlarged dura mater (dural ectasia). marfan syndrome (type 1) is associated with mutations in the gene encoding fibrillin-1 (fbn1), a major element of extracellular microfibrils of connective tissue. mutations in the gene encoding type ii tgf-beta receptor (tgfbr2) are associated with marfan syndrome type 2.
Patient EducationClinical
Marfan Syndrome
Marfan syndrome is a disorder that affects connective tissue. Connective tissues are proteins that support skin, bones, blood vessels, and other organs. One of these proteins is fibrillin. A problem with the fibrillin gene causes Marfan syndrome.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q87.42 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q87.42Overview
Is Q87.42 (Marfan syndrome) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report marfan syndrome with ocular manifestations on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does Q87.42 group to?
When marfan syndrome with ocular manifestations is the principal diagnosis on an inpatient stay, it groups to MS-DRG 306, 307, with relative weights from 0.9132 to 1.5758 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q87.42 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for marfan syndrome with ocular manifestations on inpatient claims.
What is the ICD-9 equivalent of Q87.42?
Under the General Equivalence Mappings, marfan syndrome with ocular manifestations converts to ICD-9-CM 759.82 (marfan syndrome). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.
