2026 ICD-10-CM Diagnosis Code Q84.0Congenital alopecia
ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q84
- Billable — Valid for Submission
- POA Exempt
- Not Chronic
Q84.0 is a billable ICD-10-CM diagnosis code for congenital alopecia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 606 through 607. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q84.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Absence of teeth
- Acroosteolysis
- Alopecia and intellectual disability with hypergonadotropic hypogonadism syndrome
- Alopecia universalis
- Alopecia, contracture, dwarfism, intellectual disability syndrome
- Alopecia, epilepsy, intellectual disability syndrome Moynahan type
- Alopecia, nail dystrophy, ophthalmic complications, thyroid dysfunction, hypohidrosis, ephelides, enteropathy and respiratory tract infections
- Alopecia, progressive neurological defect, endocrinopathy syndrome
- Alopecia, psychomotor epilepsy, periodontal pyorrhea, intellectual disability syndrome
- Atrichia congenita
- Atrichia with papular lesions
- Autosomal dominant palmoplantar keratoderma and congenital alopecia
- Autosomal recessive palmoplantar keratoderma and congenital alopecia syndrome
- Choroidal atrophy and alopecia syndrome
- Congenital alopecia
- Congenital alopecia with keratin cysts
- Congenital dysplasia of nail unit
- Congenital generalized alopecia
- Congenital hypotrichia
- Congenital ichthyosis with hypotrichosis syndrome
- Congenital localized alopecia
- Congenital retrognathism
- Cutaneous syndrome with ichthyosis
- Cutis laxa, autosomal recessive
- Developmental anomaly of periodontal tissue
- Dwarfism, alopecia, pseudoanodontia, cutis laxa
- False anodontia
- Frontonasal dysplasia sequence
- Frontonasal dysplasia with alopecia and genital anomaly syndrome
- GAPO syndrome
- Hereditary acroosteolysis
- Hypotrichosis and intellectual disability syndrome Lopes type
- Hypotrichosis with juvenile macular degeneration syndrome
- Hypotrichosis with keratosis pilaris and lentiginosis
- Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
- Hypotrichosis, osteolysis, periodontitis, palmoplantar keratoderma syndrome
- Ichthyosis follicularis with alopecia and photophobia
- Ichthyosis, alopecia, eclabion, ectropion, intellectual disability syndrome
- Keratosis pilaris
- Lamellar ichthyosis
- MACS syndrome
- Mandibulofacial dysostosis with alopecia
- Marie Unna syndrome
- Neonatal sclerosing cholangitis, ichthyosis, hypotrichosis syndrome
- Odonto onycho dysplasia with alopecia syndrome
- Odonto-onychial dysplasia with alopecia
- Periodontitis co-occurrent with genetic disorder
- Poikiloderma, alopecia, retrognathism, cleft palate syndrome
- Recession of bone
- Sclerosing cholangitis
- Severe T-cell immunodeficiency, congenital alopecia, nail dystrophy syndrome
- Short stature, onychodysplasia, facial dysmorphism, hypotrichosis syndrome
- Spondyloepimetaphyseal dysplasia, hypotrichosis syndrome
- Sutural alopecia
- Taurodontia with absent teeth and sparse hair syndrome
- Thumb deformity, alopecia, pigmentation anomaly syndrome
- Tooth absent
- Triangular alopecia
- Vertical alopecia
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- Congenital atrichosis
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Agenesis
- hair
- Alopecia(hereditaria) (seborrheica)
- congenital, congenitalis
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Congenital Alopecia
a congenital condition characterized by the absence of hair on the scalp or entire body. the lack of hair is rarely absolute and is usually accompanied by incompletely grown, lanugo-like hair. it affects males twice as much as females and a familial tendency is common.Nevoid Congenital Alopecia|Nevoid congenital alopecia
alopecia that is present at birth in a localized, circumscribed area with highly pigmented, nevus-like areas.ABCA12 wt Allele|ABC12|ARCI4A|ARCI4B|ATP Binding Cassette Subfamily A Member 12 wt Allele|ATP-Binding Cassette, Sub-Family A (ABC1), Member 12 Gene|ATP-Binding Cassette, Subfamily A, Member 12 Gene|DKFZP434G232|ICR2B|Ichthyosis Congenita II, Lamellar Ichthyosis B Gene|LI2
human abca12 wild-type allele is located in the vicinity of 2q35 and is approximately 207 kb in length. this allele, which encodes glucosylceramide transporter abca12 protein, plays a role in both the membrane localization of glucosylceramide and other lipids in lamellar granules and in cholesterol transport. mutation of the gene is associated with autosomal recessive congenital ichthyosis (arci) types 4a and 4b (harlequin).Lamellar Ichthyosis
a very rare, autosomal recessive inherited skin disorder present at birth. it is characterized by the presence of a transparent membrane encasing the newborn. this membrane sheds in about two weeks after birth to reveal generalized scaling and skin erythema.Acroosteolysis
a condition that is characterized by degeneration of the distal phalanges.
Patient EducationClinical
Hair Problems
The average person has 5 million hairs. Hair grows all over your body except on your lips, palms, and the soles of your feet. It takes about a month for healthy hair to grow half an inch. Most hairs grow for up to six years and then fall out. New hairs grow in their place.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q84.0 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q84.0Overview
Is Q84.0 (Other congenital malformations of integument) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report congenital alopecia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does Q84.0 group to?
When congenital alopecia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 606, 607, with relative weights from 0.9064 to 1.5132 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q84.0 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital alopecia on inpatient claims.
What is the ICD-9 equivalent of Q84.0?
Under the General Equivalence Mappings, congenital alopecia converts to ICD-9-CM 757.4 (hair anomalies NEC). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.
