2027 ICD-10-CM Diagnosis Code Q85Phakomatoses, not elsewhere classified

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q85

ICD-10-CM Q85
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q85 is a non-billable ICD-10-CM category code for phakomatoses, not elsewhere classified, so it cannot be submitted on claims. Use a more specific code from this category instead, such as Q85.00, Q85.01, Q85.02, and Q85.03.

Code Identity

ICD-10-CM Code
Q85
Billable Status
No — Non-Billable Category
Code Describes
Phakomatoses, not elsewhere classified
Short Description
Phakomatoses, not elsewhere classified
Same as the full description in the CMS dataset.
Chapter
Q80-Q89
Other congenital malformations

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ85Phakomatoses, not elsewhere classified
This CodeQ85Phakomatoses, not elsewhere classified

Specific Coding for Phakomatoses, not elsewhere classifiedOverview

Non-specific codes like Q85 require more characters. Use one of these billable codes instead:

  • Q85.0 for Neurofibromatosis (nonmalignant)

  • Use Q85.00 for Neurofibromatosis, unspecified

  • Use Q85.01 for Neurofibromatosis, type 1

  • Use Q85.02 for Neurofibromatosis, type 2

  • Use Q85.03 for Schwannomatosis

  • Use Q85.09 for Other neurofibromatosis

  • Use Q85.1 for Tuberous sclerosis

  • Q85.8 for Other phakomatoses, not elsewhere classified

  • Use Q85.81 for PTEN hamartoma tumor syndrome

  • Use Q85.82 for Other Cowden syndrome

  • Use Q85.83 for Von Hippel-Lindau syndrome

  • Use Q85.89 for Other phakomatoses, not elsewhere classified

  • Use Q85.9 for Phakomatosis, unspecified

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q85: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

  • ataxia telangiectasia [Louis-Bar] (G11.3)
  • familial dysautonomia [Riley-Day] (G90.1)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Clinical InformationClinical

  • Neurocutaneous Syndromes

    a group of disorders characterized by ectodermal-based malformations and neoplastic growths in the skin, nervous system, and other organs.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q85Overview

What is the ICD-10 code for phakomatoses, not elsewhere classified?

Q85 is the ICD-10-CM category for phakomatoses, not elsewhere classified, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is Q85 (Phakomatoses, not elsewhere classified) a billable code?

No. This is a category header that groups the codes for phakomatoses, not elsewhere classified, and headers cannot be submitted on claims. Claims for phakomatoses, not elsewhere classified need a more specific code from this category, such as Q85.00, Q85.01, and Q85.02.

Can Q85 be reported with G11.3?

Not as a rule. The Excludes1 note on Q85 lists "ataxia telangiectasia [Louis-Bar] (G11.3)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).