2026 ICD-10-CM Diagnosis Code Q85Phakomatoses, not elsewhere classified

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q85

ICD-10-CM Q85
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q85 is a non-billable ICD-10-CM category code for phakomatoses, not elsewhere classified, so it cannot be submitted on claims. Use a more specific code from this category instead, such as Q85.00, Q85.01, Q85.02, and Q85.03.

Code Identity

ICD-10-CM Code
Q85
Billable Status
No — Non-Billable Category
Code Describes
Phakomatoses, not elsewhere classified
Chapter
Q80-Q89
Other congenital malformations

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ85Phakomatoses, not elsewhere classified
This CodeQ85Phakomatoses, not elsewhere classified

Specific Coding for Phakomatoses, not elsewhere classifiedOverview

Non-specific codes like Q85 require more characters. Use one of these billable codes instead:

  • Q85.0 for Neurofibromatosis (nonmalignant)

  • Use Q85.00 for Neurofibromatosis, unspecified

  • Use Q85.01 for Neurofibromatosis, type 1

  • Use Q85.02 for Neurofibromatosis, type 2

  • Use Q85.03 for Schwannomatosis

  • Use Q85.09 for Other neurofibromatosis

  • Use Q85.1 for Tuberous sclerosis

  • Q85.8 for Other phakomatoses, not elsewhere classified

  • Use Q85.81 for PTEN hamartoma tumor syndrome

  • Use Q85.82 for Other Cowden syndrome

  • Use Q85.83 for Von Hippel-Lindau syndrome

  • Use Q85.89 for Other phakomatoses, not elsewhere classified

  • Use Q85.9 for Phakomatosis, unspecified

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Type 1 Excludes

  • ataxia telangiectasia Louis-Bar G11.3
  • familial dysautonomia Riley-Day G90.1

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q85Overview

Is Q85 (Phakomatoses, not elsewhere classified) a billable code?

No. This is a category header that groups the codes for phakomatoses, not elsewhere classified, and headers cannot be submitted on claims. Claims for phakomatoses, not elsewhere classified need a more specific code from this category, such as Q85.00, Q85.01, and Q85.02.