2026 ICD-10-CM Diagnosis Code Q77.7Spondyloepiphyseal dysplasia
ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q77
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q77.7 is a billable ICD-10-CM diagnosis code for spondyloepiphyseal dysplasia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q77.7 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Abnormally short fourth metatarsal
- Brachymetatarsia
- Brachymetatarsia of fourth metatarsal
- Chronic deafness
- Congenital conductive hearing loss
- Congenital hypoplasia of bone of radius and/or ulna
- Congenital hypoplasia of ulna
- Congenital hypotrichia
- Cono-spondylar dysplasia
- Czech dysplasia metatarsal type
- Degenerative polyarthritis
- Disproportionate short stature
- Dyggve-Melchior-Clausen syndrome
- Eiken syndrome
- EVEN-plus syndrome
- Immuno-osseous dysplasia
- Leber's amaurosis
- Mild spondyloepiphyseal dysplasia due to COL2A1 mutation with early onset osteoarthritis
- Mild spondyloepiphyseal dysplasia with premature onset arthrosis
- MIR140-related spondyloepiphyseal dysplasia
- Multiple epiphyseal dysplasia Al-Gazali type
- Multiple epiphyseal dysplasia Beighton type
- Oligodontia
- Opsismodysplasia
- Progressive spondyloepimetaphyseal dysplasia, short stature, short fourth metatarsals, intellectual disability syndrome
- Pseudoachondroplastic spondyloepiphyseal dysplasia syndrome
- Roifman syndrome
- Scoliosis in skeletal dysplasia
- Sponastrime dysplasia
- Spondyloepimetaphyseal disorder
- Spondyloepimetaphyseal dysplasia aggrecan type
- Spondyloepimetaphyseal dysplasia anauxetic type
- Spondyloepimetaphyseal dysplasia Genevieve type
- Spondyloepimetaphyseal dysplasia Handigodu type
- Spondyloepimetaphyseal dysplasia Irapa type
- Spondyloepimetaphyseal dysplasia Isidor type
- Spondyloepimetaphyseal dysplasia matrilin-3 type
- Spondyloepimetaphyseal dysplasia Missouri type
- Spondyloepimetaphyseal dysplasia PAPSS2 type
- Spondyloepimetaphyseal dysplasia Shohat type
- Spondyloepimetaphyseal dysplasia with joint laxity Beighton type
- Spondyloepimetaphyseal dysplasia with joint laxity, EXOC6B type
- Spondyloepimetaphyseal dysplasia with multiple dislocations
- Spondyloepimetaphyseal dysplasia, abnormal dentition syndrome
- Spondyloepimetaphyseal dysplasia, hypotrichosis syndrome
- Spondyloepimetaphyseal dysplasia, short limb, abnormal calcification syndrome
- Spondyloepiphyseal dysplasia Cantu type
- Spondyloepiphyseal dysplasia congenita
- Spondyloepiphyseal dysplasia Kimberley type
- Spondyloepiphyseal dysplasia MacDermot type
- Spondyloepiphyseal dysplasia Maroteaux type
- Spondyloepiphyseal dysplasia Reardon type
- Spondyloepiphyseal dysplasia Stanescu type
- Spondyloepiphyseal dysplasia tarda
- Spondyloepiphyseal dysplasia tarda Kohn type
- Spondyloepiphyseal dysplasia with congenital joint dislocations
- Spondyloepiphyseal dysplasia with joint laxity
- Spondyloepiphyseal dysplasia, craniosynostosis, cleft palate, cataract and intellectual disability syndrome
- Spondyloepiphyseal dysplasia, sensorineural hearing loss, intellectual disability, Leber congenital amaurosis syndrome
- Spondylo-megaepiphyseal-metaphyseal dysplasia
- Spondylometaphyseal dysplasia Golden type
- Spondyloperipheral dysplasia
- Spondyloperipheral dysplasia with short ulna syndrome
- X-linked intellectual disability, cerebellar hypoplasia, spondyloepiphyseal dysplasia syndrome
- X-linked spondyloepimetaphyseal dysplasia
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- Dysplasia - See Also: Anomaly;
- spondyloepiphyseal - Q77.7
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Dysplasia
- spondyloepiphyseal
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Spondyloperipheral Dysplasia
an autosomal dominant condition caused by mutation(s) in the col2a1 gene, encoding collagen alpha-1(ii) chain. it is characterized by short stature, pugilistic facies, midface hypoplasia, spondyloepiphyseal dysplasia, kyphosis, short ulna, and absent styloid process. mutation(s) in the same gene are responsible for kniest dysplasia.AXIN2-Associated Polyposis|ODCRCS|Oligodontia-Colorectal Cancer Syndrome
a rare autosomal dominant syndrome caused by constitutional (germline) loss-of-function variants in axin2 gene. it is characterized by the presence of multiple colorectal adenomatous polyps and an increased risk of colorectal carcinoma. oligodontia and ectodermal dysplasia may or may not be present.EDA wt Allele|ECTD1|ED1|ED1-A1|ED1-A2|EDA|EDA-A1|EDA-A2|EDA1|EDA2|Ectodermal Dysplasia 1, Anhidrotic Gene|Ectodysplasin A wt Allele|Ectodysplasin Gene|HED|HED1|ODT1|Oligodontia 1 Gene|STHAGX1|TNLG7C|XHED|XLHED
human eda wild-type allele is located in the vicinity of xq13.1 and is approximately 423 kb in length. this allele, which encodes ectodysplasin-a protein, is involved in the morphogenesis of ectodermally derived tissues. mutation of the gene is associated with x-linked hypohidrotic ectodermal dysplasia type 1 and x-linked, selective tooth agenesis type 1.Oligodontia
the congenital absence of six or more permanent teeth with the exclusion of third molars.
Patient EducationClinical
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
The full article covers:
- What are birth defects?
- What causes birth defects?
- Who is at risk of having a baby with birth defects?
- How are birth defects diagnosed?
- What are the treatments for birth defects?
- Can birth defects be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q77.7 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q77.7Overview
Is Q77.7 a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report spondyloepiphyseal dysplasia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does Q77.7 group to?
When spondyloepiphyseal dysplasia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q77.7 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for spondyloepiphyseal dysplasia on inpatient claims.
What is the ICD-9 equivalent of Q77.7?
Under the General Equivalence Mappings, spondyloepiphyseal dysplasia converts to ICD-9-CM 756.4 (chondrodystrophy). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.
