2027 ICD-10-CM Diagnosis Code Q77.4Achondroplasia

ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q77

ICD-10-CM Q77.4
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q77.4 is a billable ICD-10-CM diagnosis code for achondroplasia. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. Coders also document this condition as acanthosis nigricans. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q77.4
Billable Status
Yes — Valid for Submission
Code Describes
Achondroplasia
Short Description
Achondroplasia
Same as the full description in the CMS dataset.
Parent Code
Osteochondrodysplasia with defects of growth of tubular bones and spine

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategoryQ77Osteochondrodysplasia with defects of growth of tubular bones and spine
This CodeQ77.4Achondroplasia

Present on Admission (POA)Billing

Q77.4 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations and deformations of the musculoskeletal system (Q65-Q79).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acanthosis nigricans
  • Achondrogenesis
  • Achondroplasia
  • Hypochondroplasia
  • Lethal chondrodysplasia with fragmented bone
  • Severe achondroplasia, developmental delay, acanthosis nigricans syndrome
  • Severe combined immunodeficiency with low T- and B-cell numbers
  • Short-limb skeletal dysplasia with severe combined immunodeficiency

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q77.4: its own notes plus those printed at Q77 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Hypochondroplasia
  • Osteosclerosis congenita

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Q77 Osteochondrodysplasia with defects of growth of tubular bones and spine applies to 10 codes

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Q77 Osteochondrodysplasia with defects of growth of tubular bones and spine applies to 10 codes
  • congenital myotonic chondrodystrophy (G71.13)
From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q77.4, its category, or a range that includes it.

Excludes1 3

These codes carry an Excludes1 note naming Q77.4: they are not reported together with it, unless the two conditions are unrelated.

  • E34.3 Short stature due to endocrine disorder
    achondroplastic short stature (Q77.4)
  • E34.3 Short stature due to endocrine disorder
    hypochondroplastic short stature (Q77.4)
  • M85.8 Other specified disorders of bone density and structure
    osteosclerosis congenita (Q77.4)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Achondroplasia

    an autosomal dominant disorder that is the most frequent form of short-limb dwarfism. affected individuals exhibit short stature caused by rhizomelic shortening of the limbs, characteristic facies with frontal bossing and mid-face hypoplasia, exaggerated lumbar lordosis, limitation of elbow extension, genu varum, and trident hand. (online mendelian inheritance in man, http://www.ncbi.nlm.nih.gov/omim, mim#100800, april 20, 2001)

Patient EducationClinical

Dwarfism

People with dwarfism have short stature. This means that their height is under 4' 10" as an adult. They are usually of normal intelligence. Dwarfism most often does happen in families where both parents are of average height.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q77.4 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
756.4 Chondrodystrophy
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q77.4Overview

What is the ICD-10 code for achondroplasia?

The ICD-10-CM code for achondroplasia is Q77.4 (sometimes written as Q774). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q77.4 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report achondroplasia on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q77.4 group to?

When achondroplasia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q77.4 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for achondroplasia on inpatient claims. The code appears in the Congenital malformations and deformations of the musculoskeletal system (Q65-Q79) range of the CMS exempt list.

What is the ICD-9 equivalent of Q77.4?

Under the General Equivalence Mappings, achondroplasia converts to ICD-9-CM 756.4 (chondrodystrophy). The mapping is approximate, so confirm the match fits the documentation.