2027 ICD-10-CM Diagnosis Code Q50.01Congenital absence of ovary, unilateral

ICD-10-CM Codes›Q00-Q99›Q50-Q56›Q50

ICD-10-CM Q50.01
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q50.01 is a billable ICD-10-CM diagnosis code for congenital absence of ovary, unilateral. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 742 through 743, 760 through 761. The code is exempt from POA reporting. Coders also document this condition as agenesis of ovary. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q50.01
Billable Status
Yes — Valid for Submission
Code Describes
Congenital absence of ovary, unilateral
Short Description
Congenital absence of ovary, unilateral
Same as the full description in the CMS dataset.
Parent Code
Q50.0
Congenital absence of ovary

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ50-Q56Congenital malformations of genital organs
CategoryQ50Congenital malformations of ovaries, fallopian tubes and broad ligaments
This CodeQ50.01Congenital absence of ovary, unilateral

Present on Admission (POA)Billing

Q50.01 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of genital organs (Q50-Q56).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Agenesis of ovary
  • Aplasia of ovary
  • Congenital absence of left ovary
  • Congenital absence of ovary
  • Congenital absence of right ovary
  • Congenital anomaly of left ovary
  • Congenital anomaly of right ovary

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q50.01: its own notes plus those printed at Q50.0, block Q50-Q56, and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Q50.0 Congenital absence of ovary applies to 2 codes
  • Turner's syndrome (Q96.-)
From Block Q50-Q56 Congenital malformations of genital organs applies to 91 codes
  • androgen insensitivity syndrome (E34.5-)
  • syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q50.01 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
752.0 Anomalies of ovaries
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q50.01Overview

What is the ICD-10 code for congenital absence of ovary, unilateral?

The ICD-10-CM code for congenital absence of ovary, unilateral is Q50.01 (sometimes written as Q5001). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q50.01 (Congenital absence of ovary) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital absence of ovary, unilateral on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q50.01 group to?

When congenital absence of ovary, unilateral is the principal diagnosis on an inpatient stay, it groups to MS-DRG 742, 743, 760, 761, with relative weights from 0.7039 to 1.8448 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q50.01 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital absence of ovary, unilateral on inpatient claims. The code appears in the Congenital malformations of genital organs (Q50-Q56) range of the CMS exempt list.

Can Q50.01 be reported with a code from Q96?

Not as a rule. The Excludes1 note at Q50.0, which applies to Q50.01, lists "Turner's syndrome (Q96.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).