2027 ICD-10-CM Diagnosis Code Q33.6Congenital hypoplasia and dysplasia of lung
ICD-10-CM Codes›Q00-Q99›Q30-Q34›Q33
- Billable — Valid for Submission
- MCC — Major Complication or Comorbidity
- POA Exempt
- Chronic Condition
Q33.6 is a billable ICD-10-CM diagnosis code for congenital hypoplasia and dysplasia of lung. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 205 through 206. As a secondary diagnosis, it counts as a major complication or comorbidity (MCC) and places an inpatient stay in the highest severity level of its MS-DRG family. It does not count, however, when the principal diagnosis is one of 13 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Respiratory congenital malformations.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q33.6 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the respiratory system (Q30-Q34).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Bilateral primary congenital hypoplasia of lung
- Bilateral secondary hypoplasia of lung
- Congenital dysplasia of left lobe of lung co-occurrent with congenital vascular malformation
- Congenital dysplasia of right lobe of lung co-occurrent with congenital vascular malformation
- Congenital hypoplasia of left side of chest
- Congenital hypoplasia of lung
- Congenital hypoplasia of right side of chest
- Congenital pulmonary acinar dysplasia
- Congenital pulmonary hypoplasia due to lung space occupying lesion
- Congenital pulmonary hypoplasia due to prolonged premature rupture of membranes
- Dysplasia of lung
- Game Friedman Paradice syndrome
- PAGOD syndrome
- Primary pulmonary hypoplasia
- Secondary pulmonary hypoplasia
- Thymic, renal, anal, lung dysplasia syndrome
- Vascular ring with malrotation and dextroversion of heart and hypoplasia of right lung and left arterial duct
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q33.6: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
- pulmonary hypoplasia associated with short gestation (P28.0)
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
imperfect, congenital See Also: Anomaly, by site;
lungs Q33.6
Dysplasia See Also: Anomaly;
Undeveloped, undevelopment See Also: Hypoplasia;
lung Q33.6
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
The full article covers:
- What are birth defects?
- What causes birth defects?
- Who is at risk of having a baby with birth defects?
- How are birth defects diagnosed?
- What are the treatments for birth defects?
- Can birth defects be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q33.6 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q33.6Overview
What is the ICD-10 code for congenital hypoplasia and dysplasia of lung?
The ICD-10-CM code for congenital hypoplasia and dysplasia of lung is Q33.6 (sometimes written as Q336). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q33.6 (Congenital malformations of lung) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report congenital hypoplasia and dysplasia of lung on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q33.6 group to?
When congenital hypoplasia and dysplasia of lung is the principal diagnosis on an inpatient stay, it groups to MS-DRG 206, 205, with relative weights from 0.9255 to 1.8244 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q33.6 a CC or MCC?
CMS lists Q33.6 as an MCC (major complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it places the inpatient stay in the highest-weighted DRG of its severity family. It does not count when the principal diagnosis is one of the 13 closely related codes in its exclusion list.
Is Q33.6 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital hypoplasia and dysplasia of lung on inpatient claims. The code appears in the Congenital malformations of the respiratory system (Q30-Q34) range of the CMS exempt list.
