Other congenital malformations of respiratory system (Q34)

The ICD-10 code Q34 covers various congenital malformations of the respiratory system that do not fall into more common specific categories. These codes are essential for documenting rare or unspecified birth defects affecting respiratory structures.

This section includes codes for specific anomalies such as Q34.0 for pleural anomalies (also known as congenital anomaly of pleural folds or hydrothorax), and Q34.1 for congenital cysts in the mediastinum. The Q34.8 category captures other specified congenital defects like congenital pulmonary alveolar capillary dysplasia or congenital atresia of the pharynx, addressing uncommon or complex respiratory abnormalities. Finally, Q34.9 is used when a congenital malformation of the respiratory system is recognized but not otherwise specified, including abnormalities of the nose, nasopharynx, or bronchopulmonary foregut. These codes assist healthcare providers and coders in accurately identifying and reporting rare respiratory congenital defects through the ICD-10 coding system, such as the ICD-10 code for congenital cyst of mediastinum or ICD-10 code for anomaly of pleura.

Instructional Notations

Type 2 Excludes

A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.

  • congenital central alveolar hypoventilation syndrome G47.35

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Hydrothorax

A collection of watery fluid in the pleural cavity. (Dorland, 27th ed)