Congenital malformations of lung (Q33) ICD-10-CM

About the Q33 Code Range

ICD-10 codes Q33 to Q33.9 cover specific congenital malformations of the lung, identifying various structural lung abnormalities present from birth. These codes help characterize and distinguish between different types of lung conditions such as cystic lesions, malformations, absence, and unusual tissue presence affecting the respiratory system.

The ICD-10 code for congenital cystic lung (Q33.0) includes conditions like congenital cystic adenomatoid malformation, often referred to as lung cyst or congenital pulmonary airway malformation of various types. Q33.1 identifies accessory lobes of the lung, such as the azygos lobe, which represent extra segments of lung tissue. Q33.2 describes sequestration of lung tissue, either intralobar or extralobar, where lung parts receive abnormal blood supply. Q33.3 denotes agenesis of lung, meaning complete or partial absence of one or more lung lobes. Other codes like Q33.4 for congenital bronchiectasis, Q33.5 for ectopic lung tissue (e.g., bone or cartilage inside the lung), and Q33.6 for congenital hypoplasia or dysplasia define varied structural underdevelopment or malformations. Q33.8 includes other congenital lung malformations, such as unusual lobation or lymphatic abnormalities, while Q33.9 covers unspecified congenital lung malformations. These codes aid healthcare professionals in accurately documenting and differentiating lung defects detected early in development or after birth.