Congenital malformations of lung (Q33) ICD-10-CM
The Q33 code range covers congenital malformations of lung with 10 ICD-10-CM diagnosis codes. 9 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Codes in the Q33 Range 10 codes · 9 billable
- Q33 Congenital malformations of lungNon-billable
- Q33.0 Congenital cystic lung
- Q33.1 Accessory lobe of lung
- Q33.2 Sequestration of lung
- Q33.3 Agenesis of lung
- Q33.4 Congenital bronchiectasis
- Q33.5 Ectopic tissue in lung
- Q33.6 Congenital hypoplasia and dysplasia of lung
- Q33.8 Other congenital malformations of lung
- Q33.9 Congenital malformation of lung, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the Q33 range.
Supernumerary Lung Lobe
Lung tissue that is separated by an accessory fissure.
About the Q33 Code Range
These are differences in lung structure present at birth. They belong to a broader group of congenital respiratory system malformations.
The subdivisions distinguish specific findings, including a cystic lung (Q33.0), an accessory lung lobe (Q33.1), and an absent lung (Q33.3). Other specified lung malformations have a separate subdivision (Q33.8) from unspecified lung malformations (Q33.9).
Questions About This Page
How many billable codes are in the Q33 range?
Of the 10 codes in this range, 9 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the Q33 range classify?
The range classifies congenital malformations of lung. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
