2027 ICD-10-CM Diagnosis Code N01.8Rapidly progressive nephritic syndrome with other morphologic changes
ICD-10-CM Codes›N00–N99›N00-N08›N01
- Billable — Valid for Submission
- MCC — Major Complication or Comorbidity
- Not Chronic
N01.8 is a billable ICD-10-CM diagnosis code for rapidly progressive nephritic syndrome with other morphologic changes. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 698 through 700, 791, 793. As a secondary diagnosis, it counts as a major complication or comorbidity (MCC) and places an inpatient stay in the highest severity level of its MS-DRG family. It does not count, however, when the principal diagnosis is one of 286 closely related codes. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Nephritis; nephrosis; renal sclerosis.
N01.8 does not risk-adjust for Medicare Advantage under the CMS-HCC V28 model. It still risk-adjusts in the ESRD (V21) category 141 for payment year 2027.
Code Identity
Code Classification
Medicare Risk Adjustment (HCC)Billing
N01.8 does not risk-adjust for Medicare Advantage under the CMS-HCC V28 model, but it maps to payment categories in the other CMS models shown below.
Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to N01.8: its own notes plus those printed at N01, block N00-N08, and Chapter 14. A note printed at a category, block or chapter applies to every code under it.
Includes
Further defines, or gives examples of, the content of the category.
- rapidly progressive glomerular disease
- rapidly progressive glomerulonephritis
- rapidly progressive nephritis
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Rapidly progressive nephritic syndrome with proliferative glomerulonephritis NOS
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
- hypertensive chronic kidney disease (I12.-)
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Code Also
A second code may be needed to fully describe the condition; the note gives no sequencing direction.
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Kidney Diseases
You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert N01.8 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About N01.8Overview
What is the ICD-10 code for rapidly progressive nephritic syndrome with other morphologic changes?
The ICD-10-CM code for rapidly progressive nephritic syndrome with other morphologic changes is N01.8 (sometimes written as N018). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is N01.8 (Rapidly progressive nephritic syndrome) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report rapidly progressive nephritic syndrome with other morphologic changes on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does N01.8 group to?
When rapidly progressive nephritic syndrome with other morphologic changes is the principal diagnosis on an inpatient stay, it groups to MS-DRG 793, 791, 699, 698, 700, with relative weights from 0.6740 to 4.2192 depending on complications. Higher weights mean higher Medicare reimbursement.
Is N01.8 a CC or MCC?
CMS lists N01.8 as an MCC (major complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it places the inpatient stay in the highest-weighted DRG of its severity family. It does not count when the principal diagnosis is one of the 286 closely related codes in its exclusion list.
Can N01.8 be reported with a code from N05?
Not as a rule. The Excludes1 note at N01, which applies to N01.8, lists "nephritic syndrome NOS (N05.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
Does N01.8 risk-adjust for Medicare Advantage payment?
Not for Medicare Advantage: N01.8 maps to no category in the CMS-HCC V28 model. It still risk-adjusts in the ESRD (V21) category 141 (Nephritis).
