2026 ICD-10-CM Diagnosis Code N01.8Rapidly progressive nephritic syndrome with other morphologic changes
ICD-10-CM Codes›N00–N99›N00-N08›N01
- Billable — Valid for Submission
- Not Chronic
N01.8 is a billable ICD-10-CM diagnosis code for rapidly progressive nephritic syndrome with other morphologic changes. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 698 through 700. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Nephritis; nephrosis; renal sclerosis.
Code Identity
Code Classification
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- Rapidly progressive nephritic syndrome with proliferative glomerulonephritis NOS
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Nephritis, nephritic(albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)
- rapidly progressive
- with
- specified morphological changes NEC
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Patient EducationClinical
Kidney Diseases
You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters.
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Convert N01.8 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About N01.8Overview
Is N01.8 (Rapidly progressive nephritic syndrome) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report rapidly progressive nephritic syndrome with other morphologic changes on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does N01.8 group to?
When rapidly progressive nephritic syndrome with other morphologic changes is the principal diagnosis on an inpatient stay, it groups to MS-DRG 698, 699, 700, with relative weights from 0.6899 to 1.6544 depending on complications. Higher weights mean higher Medicare reimbursement.
What is the ICD-9 equivalent of N01.8?
Under the General Equivalence Mappings, rapidly progressive nephritic syndrome with other morphologic changes converts to ICD-9-CM 580.4 (ac rapidly progr nephrit). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.
