2026 ICD-10-CM Diagnosis Code N01Rapidly progressive nephritic syndrome

ICD-10-CM Codes›N00–N99›N00-N08›N01

ICD-10-CM N01
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

N01 is a non-billable ICD-10-CM category code for rapidly progressive nephritic syndrome, so it cannot be submitted on claims. Use a more specific code from this category instead, such as N01.0, N01.1, N01.2, and N01.3.

Code Identity

ICD-10-CM Code
N01
Billable Status
No — Non-Billable Category
Code Describes
Rapidly progressive nephritic syndrome
Chapter
N00-N08
Glomerular diseases

Code Classification

ChapterN00–N99Diseases of the genitourinary system
SectionN00-N08Glomerular diseases
CategoryN01Rapidly progressive nephritic syndrome
This CodeN01Rapidly progressive nephritic syndrome

Specific Coding for Rapidly progressive nephritic syndromeOverview

Non-specific codes like N01 require more characters. Use one of these billable codes instead:

  • Use N01.0 for Rapidly progressive nephritic syndrome with minor glomerular abnormality

  • Use N01.1 for Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions

  • Use N01.2 for Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis

  • Use N01.3 for Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis

  • Use N01.4 for Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis

  • Use N01.5 for Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis

  • Use N01.6 for Rapidly progressive nephritic syndrome with dense deposit disease

  • Use N01.7 for Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis

  • Use N01.8 for Rapidly progressive nephritic syndrome with other morphologic changes

  • Use N01.9 for Rapidly progressive nephritic syndrome with unspecified morphologic changes

  • Use N01.A for Rapidly progressive nephritic syndrome with C3 glomerulonephritis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Includes

  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis

Type 1 Excludes

  • nephritic syndrome NOS N05

Patient EducationClinical

Kidney Diseases

You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About N01Overview

Is N01 (Rapidly progressive nephritic syndrome) a billable code?

No. This is a category header that groups the codes for rapidly progressive nephritic syndrome, and headers cannot be submitted on claims. Claims for rapidly progressive nephritic syndrome need a more specific code from this category, such as N01.0, N01.1, and N01.2.