2026 ICD-10-CM Diagnosis Code L13.0Dermatitis herpetiformis

ICD-10-CM Codes›L00–L99›L10-L14›L13

ICD-10-CM L13.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

L13.0 is a billable ICD-10-CM diagnosis code for dermatitis herpetiformis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 606 through 607. Coders also document this condition as conjunctivitis associated with autoimmune skin disorder. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified inflammatory condition of skin.

Code Identity

ICD-10-CM Code
L13.0
Billable Status
Yes — Valid for Submission
Code Describes
Dermatitis herpetiformis
Short Description
Dermatitis herpetiformis
Same as the full description in the CMS dataset.
Parent Code
L13
Other bullous disorders

Code Classification

ChapterL00–L99Diseases of the skin and subcutaneous tissue
SectionL10-L14Bullous disorders
CategoryL13Other bullous disorders
This CodeL13.0Dermatitis herpetiformis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Conjunctivitis associated with autoimmune skin disorder
  • Conjunctivitis associated with dermatitis herpetiformis
  • Dermatitis herpetiformis
  • Herpetiform eruption
  • Hydroa herpetiformis
  • Oral mucosal involvement by dermatitis herpetiformis
  • Vesicular eruption

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Duhring's disease
  • Hydroa herpetiformis

Type 1 Excludes

  • juvenile dermatitis herpetiformis L12.2
  • senile dermatitis herpetiformis L12.0

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Brocq-Duhring disease(dermatitis herpetiformis)
    • Dermatitis(eczematous)
      • herpetiformis (bullous) (erythematous) (pustular) (vesicular)
    • Dermatitis(eczematous)
      • multiformis
    • Dermatitis(eczematous)
      • neurotica
    • Dermatitis(eczematous)
      • polymorpha dolorosa
    • Dermatitis(eczematous)
      • pruriginosa
    • Dermatitis(eczematous)
      • trophoneurotica
    • Dermatosis
      • herpetiformis
    • Disease, diseased
      • Brocq-Duhring (dermatitis herpetiformis)
    • Disease, diseased
      • Brocq's
        • meaning
          • dermatitis herpetiformis
    • Disease, diseased
      • Duhring's (dermatitis herpetiformis)
    • Duhring's disease(dermatitis herpetiformis)
    • Pemphigus
      • circinatus

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR SKN002
Other specified inflammatory condition of skin
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Dermatitis Herpetiformis

    rare, chronic, papulo-vesicular disease characterized by an intensely pruritic eruption consisting of various combinations of symmetrical, erythematous, papular, vesicular, or bullous lesions. the disease is strongly associated with the presence of hla-b8 and hla-dr3 antigens. a variety of different autoantibodies has been detected in small numbers in patients with dermatitis herpetiformis.

  • Dermatitis Herpetiformis

    a chronic autoimmune skin disorder characterized by the development of pruritic papulovesicular and bullous lesions in the elbows, knees, buttocks, and back. it is associated with an increased expression of hla-a1, hla-b8, and hla-dr3 antibodies.

Patient EducationClinical

Skin Conditions

Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:

The full article covers:

  • What does your skin do?
  • What problems and conditions can affect your skin?
  • How can I keep my skin healthy?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert L13.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
694.0 Dermatitis herpetiformis
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About L13.0Overview

Is L13.0 (Other bullous disorders) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report dermatitis herpetiformis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does L13.0 group to?

When dermatitis herpetiformis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 606, 607, with relative weights from 0.9064 to 1.5132 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of L13.0?

Under the General Equivalence Mappings, dermatitis herpetiformis converts to ICD-9-CM 694.0 (dermatitis herpetiformis). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.