Pemphigus (L10) ICD-10-CM
The L10 code range covers pemphigus with 11 ICD-10-CM diagnosis codes. 9 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- pemphigus neonatorum L01.03
Codes in the L10 Range 11 codes · 9 billable
- L10 PemphigusNon-billable
- L10.0 Pemphigus vulgaris
- L10.1 Pemphigus vegetans
- L10.2 Pemphigus foliaceous
- L10.3 Brazilian pemphigus [fogo selvagem]
- L10.4 Pemphigus erythematosus
- L10.5 Drug-induced pemphigus
- L10.8 Other pemphigusNon-billable
- L10.81 Paraneoplastic pemphigus
- L10.89 Other pemphigus
- L10.9 Pemphigus, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the L10 range.
Pemphigus
Group of chronic blistering diseases characterized histologically by ACANTHOLYSIS and blister formation within the EPIDERMIS.
Pemphigus Vulgaris
An autoimmune blistering disorder. It is characterized by the presence of painful blisters and erosions in the skin and mucous membranes.
About the L10 Code Range
Pemphigus is a group of long-lasting blistering diseases in which blisters form within the skin’s outer layer.
The subdivisions distinguish named forms: L10.0 vulgaris, L10.1 vegetans, L10.2 foliaceous, and L10.4 erythematosus. Separate codes identify L10.3 Brazilian pemphigus and L10.5 drug-induced pemphigus. Under L10.8, other pemphigus splits into L10.81 paraneoplastic pemphigus and L10.89 other pemphigus. L10.9 is pemphigus without a specified form.
Questions About This Page
How many billable codes are in the L10 range?
Of the 11 codes in this range, 9 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the L10 range classify?
The range classifies pemphigus. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.