Pemphigus (L10) ICD-10-CM
The L10 code range covers pemphigus with 11 ICD-10-CM diagnosis codes. 9 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- pemphigus neonatorum L01.03
Codes in the L10 Range 11 codes · 9 billable
- L10 PemphigusNon-billable
- L10.0 Pemphigus vulgaris
- L10.1 Pemphigus vegetans
- L10.2 Pemphigus foliaceous
- L10.3 Brazilian pemphigus [fogo selvagem]
- L10.4 Pemphigus erythematosus
- L10.5 Drug-induced pemphigus
- L10.8 Other pemphigusNon-billable
- L10.81 Paraneoplastic pemphigus
- L10.89 Other pemphigus
- L10.9 Pemphigus, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the L10 range.
Desmoglein 1
A desmosomal cadherin that is an autoantigen in the acquired skin disorder PEMPHIGUS FOLIACEUS.
Pemphigus
Group of chronic blistering diseases characterized histologically by ACANTHOLYSIS and blister formation within the EPIDERMIS.
Pemphigus, Benign Familial
An autosomal dominantly inherited skin disorder characterized by recurrent eruptions of vesicles and BULLAE mainly on the neck, axillae, and groin. Mutations in the ATP2C1 gene (encoding the secretory pathway Ca2++/Mn2++ ATPase 1 (SPCA1)) cause this disease. It is clinically and histologically similar to DARIER DISEASE - both have abnormal, unstable DESMOSOMES between KERATINOCYTES and defective CALCIUM-TRANSPORTING ATPASES. It is unrelated to PEMPHIGUS VULGARIS though it closely resembles that disease.
About the L10 Code Range
ICD-10 codes beginning with L10 cover the diagnosis of pemphigus, a rare group of autoimmune skin disorders characterized by blistering. These codes help specify the exact type of pemphigus present for accurate medical documentation and treatment planning.
These codes range from the general L10 for pemphigus to detailed subtypes like L10.0 for pemphigus vulgaris, commonly referred to as "oral pemphigus vulgaris" or "pemphigus vulgaris of gingival mucous membrane." Other variations include L10.1 for pemphigus vegetans, also called "Neumann type," and L10.2 for pemphigus foliaceous (sometimes spelled "pemphigus foliaceus"). The classification includes less common forms such as L10.3 Brazilian pemphigus, known as "fogo selvagem," and L10.4 pemphigus erythematosus. Drug-related cases are coded under L10.5. For instances related to cancer, L10.81 represents paraneoplastic pemphigus. Finally, codes L10.8, L10.89, and L10.9 cover other specified and unspecified pemphigus types, helping coders pinpoint diagnoses like IgA pemphigus or prebullous pemphigus. Using these ICD-10 codes for pemphigus ensures clear identification of the exact subtype, facilitating targeted treatment and appropriate medical billing.
Questions About This Page
How many billable codes are in the L10 range?
Of the 11 codes in this range, 9 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the L10 range classify?
The range classifies pemphigus. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
