Pemphigoid (L12)
ICD-10 code section L12 covers pemphigoid, a group of rare autoimmune skin disorders characterized by blistering. These codes are used to classify and report various types of pemphigoid, including bullous, cicatricial, and acquired epidermolysis bullosa forms.
This set includes specific codes such as L12.0 for bullous pemphigoid, often known by synonyms like dermatis herpetiformis, drug-induced bullous pemphigoid, or pemphigoid vegetans. L12.1 designates cicatricial pemphigoid, also called benign mucous membrane pemphigoid or ocular cicatricial pemphigoid, reflecting its mucosal involvement and scarring features. For pediatric cases, L12.2 identifies chronic bullous disease of childhood, which includes synonyms such as dermatitis herpetiformis and linear IgA dermatosis. Additionally, acquired epidermolysis bullosa and its drug-induced variants fall under L12.3 with subcodes like L12.30 and L12.31. General or unspecified pemphigoid types are grouped under L12.8 and L12.9. Using these ICD-10 codes ensures precise classification and appropriate documentation of these inflammatory skin conditions.
Diseases of the skin and subcutaneous tissue (L00–L99)
Bullous disorders (L10-L14)
L12 Pemphigoid
- L12.0 Bullous pemphigoid
- L12.1 Cicatricial pemphigoid
- L12.2 Chronic bullous disease of childhood
L12.3 Acquired epidermolysis bullosa
- L12.30 Acquired epidermolysis bullosa, unspecified
- L12.31 Epidermolysis bullosa due to drug
- L12.35 Other acquired epidermolysis bullosa
- L12.8 Other pemphigoid
- L12.9 Pemphigoid, unspecified
Pemphigoid (L12)
Instructional Notations
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Clinical Terms
The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.
Dermatitis Herpetiformis
Rare, chronic, papulo-vesicular disease characterized by an intensely pruritic eruption consisting of various combinations of symmetrical, erythematous, papular, vesicular, or bullous lesions. The disease is strongly associated with the presence of HLA-B8 and HLA-DR3 antigens. A variety of different autoantibodies has been detected in small numbers in patients with dermatitis herpetiformis.
