Bullous disorders (L10-L14)
ICD-10 codes L10-L14 cover a group of rare autoimmune and inflammatory skin diseases characterized by blistering, known as bullous disorders. These codes are used to document specific types of pemphigus, pemphigoid, and other blistering skin conditions that require precise classification for treatment and diagnosis.
The L10 series focuses on pemphigus variants, including pemphigus vulgaris (also known as oral pemphigus vulgaris or pemphigus of gingival mucous membrane), pemphigus vegetans, and pemphigus foliaceous. It also includes drug-induced pemphigus and rare forms like paraneoplastic pemphigus. The L11 codes group other acantholytic disorders such as acquired keratosis follicularis and transient acantholytic dermatosis. L12 codes represent pemphigoid disorders, including bullous pemphigoid; sometimes called dermatitis herpetiformis or drug-induced bullous pemphigoid; and cicatricial pemphigoid, which affects mucous membranes. The L13 series describes other bullous disorders like dermatitis herpetiformis and subcorneal pustular dermatitis. Finally, L14 captures bullous disorders linked to diseases classified elsewhere. These codes help healthcare professionals accurately identify the exact type of blistering condition, guiding appropriate management and care.
Diseases of the skin and subcutaneous tissue (L00–L99)
Bullous disorders (L10-L14)
L10 Pemphigus
- L10.0 Pemphigus vulgaris
- L10.1 Pemphigus vegetans
- L10.2 Pemphigus foliaceous
- L10.3 Brazilian pemphigus [fogo selvagem]
- L10.4 Pemphigus erythematosus
- L10.5 Drug-induced pemphigus
L10.8 Other pemphigus
- L10.81 Paraneoplastic pemphigus
- L10.89 Other pemphigus
- L10.9 Pemphigus, unspecified
Pemphigus (L10)
L12 Pemphigoid
- L12.0 Bullous pemphigoid
- L12.1 Cicatricial pemphigoid
- L12.2 Chronic bullous disease of childhood
L12.3 Acquired epidermolysis bullosa
- L12.30 Acquired epidermolysis bullosa, unspecified
- L12.31 Epidermolysis bullosa due to drug
- L12.35 Other acquired epidermolysis bullosa
- L12.8 Other pemphigoid
- L12.9 Pemphigoid, unspecified
Pemphigoid (L12)
- L14 Bullous disorders in diseases classified elsewhere
Bullous disorders in diseases classified elsewhere (L14)
Instructional Notations
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
