Other bullous disorders (L13)
ICD-10 code L13 covers a group of rare skin conditions known as other bullous disorders, which cause blistering of the skin and mucous membranes. These codes help identify specific forms of blistering diseases beyond the more common bullous disorders.
The section includes codes like L13.0 for dermatitis herpetiformis; also called herpetiform eruption or hydroa herpetiformis; a condition causing itchy, blistering skin often linked to celiac disease. Code L13.1 refers to subcorneal pustular dermatitis, known as subcorneal pustular dermatosis, characterized by sterile pustules beneath the outer skin layer, sometimes associated with monoclonal gammopathy. The L13.8 code classifies various other specified autoimmune blistering diseases, including linear IgA disease and drug-induced bullous dermatoses, which can present with skin and mucosal blistering, conjunctivitis, and ulcerations. For cases where the bullous disorder isn’t clearly defined, L13.9 denotes an unspecified bullous disorder, covering a broad range of blistering eruptions and related symptoms like bullous eruptions from insect bites or neonatal blistering conditions. These codes are essential for accurate diagnosis and treatment of uncommon blistering skin diseases in clinical practice.
Clinical Terms
The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.
Dermatitis Herpetiformis
Rare, chronic, papulo-vesicular disease characterized by an intensely pruritic eruption consisting of various combinations of symmetrical, erythematous, papular, vesicular, or bullous lesions. The disease is strongly associated with the presence of HLA-B8 and HLA-DR3 antigens. A variety of different autoantibodies has been detected in small numbers in patients with dermatitis herpetiformis.
