2027 ICD-10-CM Diagnosis Code L11.9Acantholytic disorder, unspecified

ICD-10-CM Codes›L00–L99›L10-L14›L11

ICD-10-CM L11.9
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

L11.9 is a billable ICD-10-CM diagnosis code for acantholytic disorder, unspecified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 606 through 607. Coders also document this condition as acantholytic dermatosis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified inflammatory condition of skin.

Code Identity

ICD-10-CM Code
L11.9
Billable Status
Yes — Valid for Submission
Code Describes
Acantholytic disorder, unspecified
Short Description
Acantholytic disorder, unspecified
Same as the full description in the CMS dataset.
Parent Code
L11
Other acantholytic disorders

Code Classification

ChapterL00–L99Diseases of the skin and subcutaneous tissue
SectionL10-L14Bullous disorders
CategoryL11Other acantholytic disorders
This CodeL11.9Acantholytic disorder, unspecified

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acantholytic dermatosis
  • Familial acantholysis

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to L11.9: its own notes plus those printed at block L10-L14 and Chapter 12. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Block L10-L14 Bullous disorders applies to 26 codes
  • benign familial pemphigus [Hailey-Hailey] (Q82.8)
  • staphylococcal scalded skin syndrome (L00)
  • toxic epidermal necrolysis [Lyell] (L51.2)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 12 (L00-L99) Diseases of the skin and subcutaneous tissue applies to 1,001 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • lipomelanotic reticulosis (I89.8)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
  • systemic connective tissue disorders (M30-M36)
  • viral warts (B07.-)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR SKN002
Other specified inflammatory condition of skin
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Acantholysis

    separation of the prickle cells of the stratum spinosum of the epidermis, resulting in atrophy of the prickle cell layer. it is seen in diseases such as pemphigus vulgaris (see pemphigus) and darier disease.

Patient EducationClinical

Skin Conditions

Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:

The full article covers:

  • What does your skin do?
  • What problems and conditions can affect your skin?
  • How can I keep my skin healthy?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert L11.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
701.8 Skin hypertro/atroph NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About L11.9Overview

What is the ICD-10 code for acantholytic disorder, unspecified?

The ICD-10-CM code for acantholytic disorder, unspecified is L11.9 (sometimes written as L119). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is L11.9 (Other acantholytic disorders) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report acantholytic disorder, unspecified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does L11.9 group to?

When acantholytic disorder, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 607, 606, with relative weights from 0.8772 to 1.5721 depending on complications. Higher weights mean higher Medicare reimbursement.

Can L11.9 be reported with Q82.8?

Not as a rule. The Excludes1 note at block L10-L14, which applies to L11.9, lists "benign familial pemphigus [Hailey-Hailey] (Q82.8)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).

What is the ICD-9 equivalent of L11.9?

Under the General Equivalence Mappings, acantholytic disorder, unspecified converts to ICD-9-CM 701.8 (skin hypertro/atroph NEC). The mapping is approximate, so confirm the match fits the documentation.