2026 ICD-10-CM Diagnosis Code J84.843Alveolar capillary dysplasia with vein misalignment

ICD-10-CM Codes›J00–J99›J80-J84›J84

ICD-10-CM J84.843
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

J84.843 is a billable ICD-10-CM diagnosis code for alveolar capillary dysplasia with vein misalignment. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 196 through 198. Coders also document this condition as alveolar capillary dysplasia with pulmonary venous misalignment. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified lower respiratory disease.

Code Identity

ICD-10-CM Code
J84.843
Billable Status
Yes — Valid for Submission
Code Describes
Alveolar capillary dysplasia with vein misalignment
Short Description
Alveolar capillary dysplasia with vein misalignment
Same as the full description in the CMS dataset.
Parent Code
J84.84
Other interstitial lung diseases of childhood

Code Classification

ChapterJ00–J99Diseases of the respiratory system
SectionJ80-J84Other respiratory diseases principally affecting the interstitium
CategoryJ84Other interstitial pulmonary diseases
This CodeJ84.843Alveolar capillary dysplasia with vein misalignment

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Alveolar capillary dysplasia with pulmonary venous misalignment

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Dysplasia
      • alveolar capillary, with vein misalignment

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR RSP016
Other specified and unspecified lower respiratory disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Interstitial Lung Diseases

Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. The inflammation and scarring make it hard to get enough oxygen. The scarring is called pulmonary fibrosis.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert J84.843 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
516.64 Alv cap dysp w vn misaln
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About J84.843Overview

Is J84.843 (Other interstitial lung diseases of childhood) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report alveolar capillary dysplasia with vein misalignment on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does J84.843 group to?

When alveolar capillary dysplasia with vein misalignment is the principal diagnosis on an inpatient stay, it groups to MS-DRG 196, 197, 198, with relative weights from 0.7162 to 1.8872 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of J84.843?

Under the General Equivalence Mappings, alveolar capillary dysplasia with vein misalignment converts to ICD-9-CM 516.64 (alv cap dysp w vn misaln). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.