2026 ICD-10-CM Diagnosis Code J84.842Pulmonary interstitial glycogenosis

ICD-10-CM Codes›J00–J99›J80-J84›J84

ICD-10-CM J84.842
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

J84.842 is a billable ICD-10-CM diagnosis code for pulmonary interstitial glycogenosis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 196 through 198. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified lower respiratory disease.

Code Identity

ICD-10-CM Code
J84.842
Billable Status
Yes — Valid for Submission
Code Describes
Pulmonary interstitial glycogenosis
Short Description
Pulmonary interstitial glycogenosis
Same as the full description in the CMS dataset.
Parent Code
J84.84
Other interstitial lung diseases of childhood

Code Classification

ChapterJ00–J99Diseases of the respiratory system
SectionJ80-J84Other respiratory diseases principally affecting the interstitium
CategoryJ84Other interstitial pulmonary diseases
This CodeJ84.842Pulmonary interstitial glycogenosis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Pulmonary interstitial glycogenosis

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Glycogenosis(diffuse) (generalized)
      • pulmonary interstitial

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR RSP016
Other specified and unspecified lower respiratory disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Interstitial Lung Diseases

Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. The inflammation and scarring make it hard to get enough oxygen. The scarring is called pulmonary fibrosis.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert J84.842 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
516.62 Pulm interstitl glycogen
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About J84.842Overview

Is J84.842 (Other interstitial lung diseases of childhood) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report pulmonary interstitial glycogenosis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does J84.842 group to?

When pulmonary interstitial glycogenosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 196, 197, 198, with relative weights from 0.7162 to 1.8872 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of J84.842?

Under the General Equivalence Mappings, pulmonary interstitial glycogenosis converts to ICD-9-CM 516.62 (pulm interstitl glycogen). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.