2026 ICD-10-CM Diagnosis Code G36.0Neuromyelitis optica [Devic]

ICD-10-CM CodesG00–G99G35-G37G36

ICD-10-CM G36.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G36.0 is a billable ICD-10-CM diagnosis code for neuromyelitis optica [Devic]. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as demyelination of spinal cord. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (neither hereditary nor degenerative).

Code Identity

ICD-10-CM Code
G36.0
Billable Status
Yes — Valid for Submission
Code Describes
Neuromyelitis optica [Devic]
Short Description
Neuromyelitis optica [Devic]
Same as the full description in the CMS dataset.
Parent Code
Other acute disseminated demyelination

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG35-G37Demyelinating diseases of the central nervous system
CategoryG36Other acute disseminated demyelination
This CodeG36.0Neuromyelitis optica [Devic]

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Demyelination of spinal cord
  • Neuromyelitis optica

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Demyelination in optic neuritis

Type 1 Excludes

  • optic neuritis NOS H46

Index to Diseases and InjuriesGuidance

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Demyelination, demyelinization
      • in optic neuritis
    • Devic's disease
    • Disease, diseased
      • Devic's
    • Myelitis(acute) (ascending) (childhood) (chronic) (descending) (diffuse) (disseminated) (idiopathic) (pressure) (progressive) (spinal cord) (subacute)
      • optic neuritis in
    • Neuritis(rheumatoid)
      • optic (nerve) (hereditary) (sympathetic)
        • with demyelination
    • Neuritis(rheumatoid)
      • optic (nerve) (hereditary) (sympathetic)
        • in myelitis
    • Neuroencephalomyelopathy, optic
    • Neuromyelitis
      • optica
    • Ophthalmoneuromyelitis

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS020
Other nervous system disorders (neither hereditary nor degenerative)
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Neuromyelitis Optica

    a syndrome characterized by acute optic neuritis; myelitis, transverse; demyelinating and/or necrotizing lesions in the optic nerves and spinal cord; and presence of specific autoantibodies to aquaporin 4.

Patient EducationClinical

Autoimmune Diseases

Your immune system protects you from disease and infection by attacking germs that get into your body, such as viruses and bacteria. Your immune system can tell that the germs aren't part of you, so it destroys them. If you have an autoimmune disease, your immune system attacks the healthy cells of your organs and tissues by mistake.

The full article covers:

  • What are autoimmune diseases?
  • What causes autoimmune diseases?
  • Who is at risk for autoimmune diseases?
  • What are the symptoms of autoimmune diseases?
  • How are autoimmune diseases diagnosed?
  • What are the treatments for autoimmune diseases?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert G36.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
341.0 Neuromyelitis optica
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G36.0Overview

Is G36.0 (Other acute disseminated demyelination) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report neuromyelitis optica [Devic] on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of G36.0?

Under the General Equivalence Mappings, neuromyelitis optica [Devic] converts to ICD-9-CM 341.0 (neuromyelitis optica). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.