2027 ICD-10-CM Diagnosis Code G13.1Other systemic atrophy primarily affecting central nervous system in neoplastic disease

ICD-10-CM Codes›G00–G99›G10-G14›G13

ICD-10-CM G13.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

G13.1 is a billable ICD-10-CM diagnosis code for other systemic atrophy primarily affecting central nervous system in neoplastic disease. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 73 through 74. The code is a manifestation code that cannot be reported as the principal diagnosis. Coders also document this condition as paraneoplastic cerebellar degeneration. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Conditions due to neoplasm or the treatment of neoplasm and Other nervous system disorders (neither hereditary nor degenerative).

G13.1 no longer risk-adjusts for Medicare Advantage: it mapped to HCC 75 under the retired CMS-HCC V24 model through payment year 2025 but maps to no category in the live V28 model. It still risk-adjusts in the PACE (CMS-HCC V22) category 75, ESRD (V21) category 75, ESRD (V24) category 75, and RxHCC Part D (V08) category 158 for payment year 2027.

Code Identity

ICD-10-CM Code
G13.1
Billable Status
Yes — Valid for Submission
Code Describes
Other systemic atrophy primarily affecting central nervous system in neoplastic disease
Short Description
Oth systemic atrophy aff cnsl in neoplastic disease
Parent Code
Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG10-G14Systemic atrophies primarily affecting the central nervous system
CategoryG13Systemic atrophies primarily affecting central nervous system in diseases classified elsewhere
This CodeG13.1Other systemic atrophy primarily affecting central nervous system in neoplastic disease

Code EditsBilling

Medicare Code Editor checks that affect claim validity for G13.1.

Manifestation codes describe the manifestation of an underlying disease, not the disease itself, and therefore should not be used as a principal diagnosis.

Medicare Risk Adjustment (HCC)Billing

G13.1 no longer risk-adjusts for Medicare Advantage: it maps to no payment category in the live CMS-HCC V28 model, although it still risk-adjusts in the other CMS models shown below.

CMS-HCC V28 (Medicare Advantage Payment Model)
Not mapped
Dropped in V28 see all codes that no longer risk-adjust
Prior Model (CMS-HCC V24)
HCC 75
V24 retired last contributed to a Medicare Advantage risk score in payment year 2025
Other CMS Models
PACE (CMS-HCC V22): HCC 75 · ESRD (V21): HCC 75 · ESRD (V24): HCC 75
ESRD V21 weights: 0.059 dialysis, 0.284–0.323 functioning graft · ESRD V24 weights: 0.074 dialysis, 0.344–0.599 functioning graft
Part D (RxHCC)
RxHCC 158 — Inflammatory and Toxic Neuropathy
also risk-adjusts in the Part D prescription drug model (V08)

Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Paraneoplastic cerebellar degeneration
  • Secondary cerebellar degeneration

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to G13.1: its own notes plus those printed at Chapter 6. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Paraneoplastic limbic encephalopathy

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 6 (G00-G99) Diseases of the nervous system applies to 700 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Code First

The underlying condition named in the note is sequenced before this code.

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO074
Conditions due to neoplasm or the treatment of neoplasm
Default principal diagnosis: inpatient No · outpatient No
CCSR NVS020
Other nervous system disorders (neither hereditary nor degenerative)
Default principal diagnosis: inpatient No · outpatient No

Patient EducationClinical

Brain Diseases

Your brain is the control center of your body. It controls your thoughts, memory, speech, and movement. It regulates the function of many organs. It's part of your nervous system, which also includes your spinal cord and peripheral nerves. The nervous system sends signals between your brain and the rest of the body.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert G13.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
357.3 Neuropathy in malig dis
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About G13.1Overview

Is G13.1 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other systemic atrophy primarily affecting central nervous system in neoplastic disease on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does G13.1 group to?

On inpatient claims, other systemic atrophy primarily affecting central nervous system in neoplastic disease maps to MS-DRG 74, 73, with relative weights from 1.0172 to 1.5773 depending on complications. Higher weights mean higher Medicare reimbursement.

Can G13.1 be a principal diagnosis?

No. This is a manifestation code: other systemic atrophy primarily affecting central nervous system in neoplastic disease describes the manifestation of an underlying disease rather than the disease itself, so the underlying condition is sequenced first.

What is coded first with G13.1?

The Code First note reads: underlying neoplasm (C00-D49). When one of these applies, it is sequenced before G13.1.

What is the ICD-9 equivalent of G13.1?

Under the General Equivalence Mappings, other systemic atrophy primarily affecting central nervous system in neoplastic disease converts to ICD-9-CM 357.3 (neuropathy in malig dis). The mapping is approximate, so confirm the match fits the documentation.

Does G13.1 risk-adjust for Medicare Advantage payment?

Not for Medicare Advantage. G13.1 mapped to HCC 75 in the retired CMS-HCC V24 model, which last determined payment in 2025, but it maps to no category in the live V28 model; see all codes that no longer risk-adjust. It still risk-adjusts in the PACE (CMS-HCC V22) category 75 (Myasthenia Gravis/Myoneural Disorders and Guillain-Barre Syndrome/Inflammatory and Toxic Neuropathy), ESRD (V21) category 75 (Polyneuropathy), ESRD (V24) category 75 (Myasthenia Gravis/Myoneural Disorders and Guillain-Barre Syndrome/Inflammatory and Toxic Neuropathy), and RxHCC Part D (V08) category 158 (Inflammatory and Toxic Neuropathy).