2027 ICD-10-CM Diagnosis Code D47.01Cutaneous mastocytosis
ICD-10-CM Codes›C00–D49›D37-D48›D47
- Billable — Valid for Submission
- CC — Complication or Comorbidity
- Not Chronic
D47.01 is a billable ICD-10-CM diagnosis code for cutaneous mastocytosis. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 820 through 825, 840 through 842. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 27 closely related codes. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neoplasms of unspecified nature or uncertain behavior.
D47.01 does not risk-adjust for Medicare Advantage under the CMS-HCC V28 model. It still risk-adjusts in the RxHCC Part D (V08) category 21 for payment year 2027.
Code Identity
Code Classification
Medicare Risk Adjustment (HCC)Billing
D47.01 does not risk-adjust for Medicare Advantage under the CMS-HCC V28 model, but it maps to payment categories in the other CMS models shown below.
Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Bullous cutaneous mastocytosis
- Bullous diffuse cutaneous mastocytosis
- Cutaneous mastocytosis
- Cutaneous mastocytosis, adult form
- Cutaneous mastocytosis, infantile form
- Diffuse erythrodermic mastocytosis
- Familial mastocytosis
- Hennekam Beemer syndrome
- Maculopapular cutaneous mastocytosis
- Mast cell nevus
- Mastocytoma
- Pseudoxanthomatous nodular cutaneous mastocytosis
- Solitary cutaneous mastocytoma
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to D47.01: its own notes plus those printed at D47.0, block D37-D48, and Chapter 2. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Diffuse cutaneous mastocytosis
- Maculopapular cutaneous mastocytosis
- Solitary mastocytoma
- Telangiectasia macularis eruptiva perstans
- Urticaria pigmentosa
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
- neoplasms of unspecified behavior (D49.-)
Notes
General instructions on how these codes are used.
- Functional activity
- All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
- Morphology [Histology]
- Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
- Primary malignant neoplasms overlapping site boundaries
- A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
- Malignant neoplasm of ectopic tissue
- Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name D47.01, its category, or a range that includes it.
Excludes1 5
These codes carry an Excludes1 note naming D47.01: they are not reported together with it, unless the two conditions are unrelated.
- D89.4 Mast cell activation syndrome and related disorders(non-congenital) cutaneous mastocytosis (D47.01)
- L50 Urticariaurticaria pigmentosa (D47.01)
- Q82.2 Congenital cutaneous mastocytosiscutaneous mastocytosis NOS (D47.01)
- Q82.2 Congenital cutaneous mastocytosisdiffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
- Q82.2 Congenital cutaneous mastocytosisurticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
pigmentosa D47.01
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Mastocytosis, Cutaneous
skin lesions due to abnormal infiltration of mast cells. cutaneous mastocytosis is confined to the skin without the involvement of other tissues or organs, and is mostly found in children. the three major variants are: urticaria pigmentosa; diffuse cutaneous mastocytosis; and solitary mastocytoma of skin.
Convert D47.01 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code History & ChangesHistory
Replacement D47.01 replaces the following previously assigned code(s):
- D47.0 - Histiocytic and mast cell tumors of uncertain behavior
- D47.0 - Mast cell neoplasms of uncertain behavior
Questions About D47.01Overview
What is the ICD-10 code for cutaneous mastocytosis?
The ICD-10-CM code for cutaneous mastocytosis is D47.01 (sometimes written as D4701). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is D47.01 (Mast cell neoplasms of uncertain behavior) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report cutaneous mastocytosis on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does D47.01 group to?
When cutaneous mastocytosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 841, 821, 822, 825, 842, 824, 840, 820, 823, with relative weights from 0.9948 to 6.2454 depending on complications. Higher weights mean higher Medicare reimbursement.
Is D47.01 a CC or MCC?
CMS lists D47.01 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 27 closely related codes in its exclusion list.
Can D47.01 be reported with Q82.2?
Not as a rule. The Excludes1 note on D47.01 lists "congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
Does D47.01 risk-adjust for Medicare Advantage payment?
Not for Medicare Advantage: D47.01 maps to no category in the CMS-HCC V28 model. It still risk-adjusts in the RxHCC Part D (V08) category 21 (Lymphomas and Other Hematologic Cancers).
