2026 ICD-10-CM Diagnosis Code C96.4Sarcoma of dendritic cells (accessory cells)

ICD-10-CM Codes›C00–D49›C81-C96›C96

ICD-10-CM C96.4
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

C96.4 is a billable ICD-10-CM diagnosis code for sarcoma of dendritic cells (accessory cells). It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 820 through 825, 840 through 842. Coders also document this condition as dendritic cell sarcoma. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Sarcoma.

Code Identity

ICD-10-CM Code
C96.4
Billable Status
Yes — Valid for Submission
Code Describes
Sarcoma of dendritic cells (accessory cells)
Short Description
Sarcoma of dendritic cells (accessory cells)
Same as the full description in the CMS dataset.
Parent Code
C96
Other and unspecified malignant neoplasms of lymphoid, hematopoietic and related tissue

Code Classification

ChapterC00–D49Neoplasms
SectionC81-C96Malignant neoplasms of lymphoid, hematopoietic and related tissue
CategoryC96Other and unspecified malignant neoplasms of lymphoid, hematopoietic and related tissue
This CodeC96.4Sarcoma of dendritic cells (accessory cells)

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Dendritic cell sarcoma
  • Follicular dendritic sarcoma of intraabdominal lymph node
  • Follicular dendritic sarcoma of lymph nodes of multiple sites
  • Indeterminate dendritic cell neoplasm
  • Interdigitating dendritic cell sarcoma
  • Langerhans cell sarcoma
  • Primary follicular dendritic cell sarcoma
  • Primary follicular dendritic cell sarcoma of spleen
  • Primary malignant neoplasm of spleen

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Follicular dendritic cell sarcoma
  • Interdigitating dendritic cell sarcoma
  • Langerhans cell sarcoma

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Sarcoma(of)
      • dendritic cells (accessory cells)
    • Sarcoma(of)
      • follicular dendritic cell
    • Sarcoma(of)
      • interdigitating dendritic cell
    • Sarcoma(of)
      • Langerhans cell

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO024
Sarcoma
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Langerhans Cell Sarcoma

    rare malignant neoplasm of dendritic langerhans cells exhibiting atypical cytology, frequent mitoses, and aggressive clinical behavior. they can be distinguished from other histiocytic and dendritic proliferations by immunohistochemical and ultrastructure studies. cytologically benign proliferations of langerhans cells are called langerhans cell histiocytosis.

Patient EducationClinical

Soft Tissue Sarcoma

Your soft tissues connect, support, or surround other tissues. Examples include your muscles, tendons, fat, and blood vessels. Soft tissue sarcoma is a cancer of these soft tissues. There are many kinds, based on the type of tissue they started in. They may cause a lump or swelling in the soft tissue.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert C96.4 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
202.90 Unsp lym unsp xtrndl org
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About C96.4Overview

Is C96.4 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report sarcoma of dendritic cells (accessory cells) on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does C96.4 group to?

When sarcoma of dendritic cells (accessory cells) is the principal diagnosis on an inpatient stay, it groups to MS-DRG 820, 821, 822, 823, 824, 825, 840, 841, 842, with relative weights from 1.0104 to 5.8648 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of C96.4?

Under the General Equivalence Mappings, sarcoma of dendritic cells (accessory cells) converts to ICD-9-CM 202.90 (unsp lym unsp xtrndl org). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.