2027 ICD-10-CM Diagnosis Code Z14.1Cystic fibrosis carrier

ICD-10-CM Codes›Z00–Z99›Z14-Z15›Z14

ICD-10-CM Z14.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Z14.1 is a billable ICD-10-CM diagnosis code for cystic fibrosis carrier. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 951. The code is not accepted as a principal diagnosis by the Medicare Code Editor and exempt from POA reporting. Coders also document this condition as carrier of cystic fibrosis gene mutation. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified status.

Code Identity

ICD-10-CM Code
Z14.1
Billable Status
Yes — Valid for Submission
Code Describes
Cystic fibrosis carrier
Short Description
Cystic fibrosis carrier
Same as the full description in the CMS dataset.
Parent Code
Z14
Genetic carrier

Code Classification

ChapterZ00–Z99Factors influencing health status and contact with health services
SectionZ14-Z15Genetic carrier and genetic susceptibility to disease
CategoryZ14Genetic carrier
This CodeZ14.1Cystic fibrosis carrier

Code EditsBilling

Medicare Code Editor checks that affect claim validity for Z14.1.

Unacceptable principal diagnosis
There are selected codes that describe a circumstance which influences an individual's health status but not a current illness or injury, or codes that are not specific manifestations but may be due to an underlying cause. These codes are considered unacceptable as a principal diagnosis.

Present on Admission (POA)Billing

Z14.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Genetic carrier and genetic susceptibility to disease (Z14-Z15).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Carrier of cystic fibrosis gene mutation

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Z14.1: its own notes plus those printed at Chapter 21. A note printed at a category, block or chapter applies to every code under it.

Notes

General instructions on how these codes are used.

From Chapter 21 (Z00-Z99) Factors influencing health status and contact with health services applies to 1,425 codes
  • Z codes represent reasons for encounters. A corresponding procedure code must accompany a Z code if a procedure is performed. Categories Z00-Z99 are provided for occasions when circumstances other than a disease, injury or external cause classifiable to categories A00-Y89 are recorded as 'diagnoses' or 'problems'. This can arise in two main ways:
  • (a) When a person who may or may not be sick encounters the health services for some specific purpose, such as to receive limited care or service for a current condition, to donate an organ or tissue, to receive prophylactic vaccination (immunization), or to discuss a problem which is in itself not a disease or injury.
  • (b) When some circumstance or problem is present which influences the person's health status but is not in itself a current illness or injury.

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR FAC025
Other specified status
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Cystic Fibrosis

Cystic fibrosis (CF) is an inherited disease of the mucus and sweat glands. It affects mostly your lungs, pancreas, liver, intestines, sinuses, and sex organs. CF causes your mucus to be thick and sticky. The mucus clogs the lungs, causing breathing problems and making it easy for bacteria to grow.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Z14.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
V83.81 Cystic fibrosis gene car
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Z14.1Overview

What is the ICD-10 code for cystic fibrosis carrier?

The ICD-10-CM code for cystic fibrosis carrier is Z14.1 (sometimes written as Z141). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Z14.1 (Genetic carrier) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report cystic fibrosis carrier on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Z14.1 group to?

On inpatient claims, cystic fibrosis carrier maps to MS-DRG 951 (other Factors Influencing Health Status), which carries a relative weight of 0.5574. Higher weights mean higher Medicare reimbursement.

Can Z14.1 be a principal diagnosis?

No. The Medicare Code Editor rejects this code as a principal diagnosis because cystic fibrosis carrier describes a circumstance that influences health status rather than a current illness. Report it as a secondary diagnosis.

Is Z14.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for cystic fibrosis carrier on inpatient claims. The code appears in the Genetic carrier and genetic susceptibility to disease (Z14-Z15) range of the CMS exempt list.