2026 ICD-10-CM Diagnosis Code Z14.1Cystic fibrosis carrier

ICD-10-CM Codes›Z00–Z99›Z14-Z15›Z14

ICD-10-CM Z14.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Z14.1 is a billable ICD-10-CM diagnosis code for cystic fibrosis carrier. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). The code is not accepted as a principal diagnosis by the Medicare Code Editor and exempt from POA reporting. Coders also document this condition as carrier of cystic fibrosis gene mutation. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified status.

Code Identity

ICD-10-CM Code
Z14.1
Billable Status
Yes — Valid for Submission
Code Describes
Cystic fibrosis carrier
Short Description
Cystic fibrosis carrier
Same as the full description in the CMS dataset.
Parent Code
Z14
Genetic carrier

Code Classification

ChapterZ00–Z99Factors influencing health status and contact with health services
SectionZ14-Z15Genetic carrier and genetic susceptibility to disease
CategoryZ14Genetic carrier
This CodeZ14.1Cystic fibrosis carrier

Code EditsBilling

Medicare Code Editor checks that affect claim validity for Z14.1.

Unacceptable principal diagnosis
There are selected codes that describe a circumstance which influences an individual's health status but not a current illness or injury, or codes that are not specific manifestations but may be due to an underlying cause. These codes are considered unacceptable as a principal diagnosis.

Present on Admission (POA)Billing

Z14.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Carrier of cystic fibrosis gene mutation

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Carrier(suspected) of
      • genetic
        • cystic fibrosis
    • Genetic
      • carrier (status)
        • cystic fibrosis

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR FAC025
Other specified status
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Cystic Fibrosis

Cystic fibrosis (CF) is an inherited disease of the mucus and sweat glands. It affects mostly your lungs, pancreas, liver, intestines, sinuses, and sex organs. CF causes your mucus to be thick and sticky. The mucus clogs the lungs, causing breathing problems and making it easy for bacteria to grow.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Z14.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
V83.81 Cystic fibrosis gene car
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Z14.1Overview

Is Z14.1 (Genetic carrier) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report cystic fibrosis carrier on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Can Z14.1 be a principal diagnosis?

No. The Medicare Code Editor rejects this code as a principal diagnosis because cystic fibrosis carrier describes a circumstance that influences health status rather than a current illness. Report it as a secondary diagnosis.

Is Z14.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for cystic fibrosis carrier on inpatient claims.

What is the ICD-9 equivalent of Z14.1?

Under the General Equivalence Mappings, cystic fibrosis carrier converts to ICD-9-CM V83.81 (cystic fibrosis gene car). The mapping is a direct match.