2027 ICD-10-CM Diagnosis Code Q87.3Congenital malformation syndromes involving early overgrowth

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q87

ICD-10-CM Q87.3
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q87.3 is a billable ICD-10-CM diagnosis code for congenital malformation syndromes involving early overgrowth. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 40 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q87.3
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformation syndromes involving early overgrowth
Short Description
Congenital malformation syndromes involving early overgrowth
Same as the full description in the CMS dataset.
Parent Code
Q87
Other specified congenital malformation syndromes affecting multiple systems

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ87Other specified congenital malformation syndromes affecting multiple systems
This CodeQ87.3Congenital malformation syndromes involving early overgrowth

Present on Admission (POA)Billing

Q87.3 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations (Q80-Q89).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • 15q overgrowth syndrome
  • Autosomal translocation
  • Beckwith-Wiedemann syndrome
  • CHD8 overgrowth syndrome
  • CLAPO syndrome
  • Cohen Gibson syndrome
  • Congenital macroglossia
  • Congenital omphalocele
  • Congenital overgrowth of foot
  • Congenital umbilical hernia
  • Diffuse capillary malformation with overgrowth
  • DNMT3A-related overgrowth syndrome
  • Gigantism
  • Global developmental delay, lung cysts, overgrowth, Wilms tumor syndrome
  • Hemihyperplasia with multiple lipomatosis syndrome
  • Imagawa Matsumoto syndrome
  • Klippel Trenaunay syndrome
  • Kosaki overgrowth syndrome
  • Lipomatosis of subcutaneous tissue
  • Luscan Lumish syndrome
  • Macrodactyly of toe
  • Macroencephaly
  • Macrosomia, microphthalmia, cleft palate syndrome
  • Malan overgrowth syndrome
  • Marshall-Smith syndrome
  • Megalencephaly, severe kyphoscoliosis, overgrowth syndrome
  • Multiple malformation syndrome with early overgrowth
  • Nephroblastoma
  • Overgrowth syndrome with 2q37 translocation
  • Overgrowth, macrocephaly, facial dysmorphism syndrome
  • Overgrowth, metaphyseal undermodeling, spondylar dysplasia syndrome
  • Parkes Weber syndrome
  • Partial duplication of long arm of chromosome 15
  • Partial trisomy of chromosome 15
  • Perlman syndrome
  • PIK3CA related overgrowth syndrome
  • Port-wine stain of skin
  • Segmental progressive overgrowth syndrome with fibroadipose hyperplasia
  • Simpson-Golabi-Behmel syndrome
  • Tall stature, intellectual disability, renal anomalies syndrome
  • Tall stature, scoliosis, macrodactyly of great toe syndrome
  • Weaver syndrome

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q87.3: its own notes plus those printed at Q87 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Beckwith-Wiedemann syndrome
  • Sotos syndrome
  • Weaver syndrome

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Use Additional Code

Add a second code, after this one, to fully describe the condition.

From Q87 Other specified congenital malformation syndromes affecting multiple systems applies to 21 codes
  • code(s) to identify all associated manifestations

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q87.3, its category, or a range that includes it.

Excludes1 3

These codes carry an Excludes1 note naming Q87.3: they are not reported together with it, unless the two conditions are unrelated.

  • Q67 Congenital musculoskeletal deformities of head, face, spine and chest
    congenital malformation syndromes classified to Q87.- names Q87.-, which includes this code
  • Q75 Other congenital malformations of skull and face bones
    congenital malformation syndromes classified to Q87.- names Q87.-, which includes this code
  • Q89.7 Multiple congenital malformations, not elsewhere classified
    congenital malformation syndromes affecting multiple systems (Q87.-) names Q87.-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Beckwith-Wiedemann Syndrome

    a syndrome of multiple defects characterized primarily by umbilical hernia (hernia, umbilical); macroglossia; and gigantism; and secondarily by visceromegaly; hypoglycemia; and ear abnormalities.

  • Sotos Syndrome

    congenital or postnatal overgrowth syndrome most often in height and occipitofrontal circumference with variable delayed motor and cognitive development. other associated features include advanced bone age, seizures, neonatal jaundice; hypotonia; and scoliosis. it is also associated with increased risk of developing neoplasms in adulthood. mutations in the nsd1 protein and its haploinsufficiency are associated with the syndrome.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q87.3 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.89 Specfied cong anomal NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q87.3Overview

What is the ICD-10 code for congenital malformation syndromes involving early overgrowth?

The ICD-10-CM code for congenital malformation syndromes involving early overgrowth is Q87.3 (sometimes written as Q873). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q87.3 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation syndromes involving early overgrowth on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q87.3 group to?

When congenital malformation syndromes involving early overgrowth is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q87.3 a CC or MCC?

CMS lists Q87.3 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 40 closely related codes in its exclusion list.

Is Q87.3 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation syndromes involving early overgrowth on inpatient claims. The code appears in the Other congenital malformations (Q80-Q89) range of the CMS exempt list.