2027 ICD-10-CM Diagnosis Code Q87.0Congenital malformation syndromes predominantly affecting facial appearance

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q87

ICD-10-CM Q87.0
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q87.0 is a billable ICD-10-CM diagnosis code for congenital malformation syndromes predominantly affecting facial appearance. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q87.0
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformation syndromes predominantly affecting facial appearance
Short Description
Congen malform syndromes predom affecting facial appearance
Parent Code
Q87
Other specified congenital malformation syndromes affecting multiple systems

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ87Other specified congenital malformation syndromes affecting multiple systems
This CodeQ87.0Congenital malformation syndromes predominantly affecting facial appearance

Present on Admission (POA)Billing

Q87.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations (Q80-Q89).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • 10p partial monosomy syndrome
  • 16p12.1p12.3 triplication syndrome
  • 4q partial monosomy syndrome
  • 4q25 proximal deletion syndrome
  • Aase Smith type 1 syndrome
  • Abducens nerve palsy
  • Absence of clavicle
  • Acrocallosal syndrome
  • Acrocephalopolysyndactyly
  • Acrocephalopolysyndactyly type II
  • Acrocephalosyndactyly
  • Acrocephalosyndactyly type I
  • Acromegaloid facial appearance syndrome
  • Acromelic frontonasal dysplasia
  • Acro-oto-ocular syndrome
  • Acrorenal mandibular syndrome
  • Aglossia-adactyly syndrome
  • AHDC1-related intellectual disability, obstructive sleep apnea, mild dysmorphism syndrome
  • ALDH18A1-related de Barsy syndrome
  • Ambiguous genitalia
  • Anal atresia
  • Aneurysm osteoarthritis syndrome
  • Aortic arch anomaly, facial dysmorphism, intellectual disability syndrome
  • Aplasia of clavicle
  • Arachnodactyly
  • Arachnodactyly and intellectual disability with facial dysmorphism syndrome
  • Asymmetric crying facies syndrome
  • Asymmetry of mandible
  • Athetoid movement
  • Auriculo-condylar syndrome
  • Baraitser Winter cerebrofrontofacial syndrome
  • Basel Vanagaite Smirin Yosef syndrome
  • Bifid nose
  • Bilateral congenital dislocation of hip
  • Binder syndrome
  • Blepharonasofacial malformation syndrome
  • BNAR syndrome
  • Bowing of upper limb
  • Brachycephaly
  • Brachytelephalangy, facial dysmorphism, Kallmann syndrome
  • Brain malformations, musculoskeletal abnormalities, facial dysmorphism, intellectual disability syndrome
  • Café au lait spots
  • Cardio-acral-facial syndrome
  • Cardio-facio-cutaneous syndrome
  • CCNK-related neurodevelopmental disorder, severe intellectual disability, facial dysmorphism syndrome
  • Central obesity
  • Cerebellar-facial-dental syndrome
  • Cerebrofacioarticular syndrome
  • Cerebro-facio-thoracic dysplasia
  • Cerebrooculonasal syndrome
  • CHAMP1-related intellectual disability, facial dysmorphism, behavioral abnormalities syndrome
  • Char syndrome
  • Charlie M syndrome
  • CHD3-related developmental delay, speech delay, intellectual disability, abnormalities of vision, facial dysmorphism syndrome
  • Clark Baraitser syndrome
  • Cleft lip and palate, craniofacial dysmorphism, congenital heart defect, hearing loss syndrome
  • Cleft mandible
  • CODAS syndrome
  • Cohen Gibson syndrome
  • Combined immunodeficiency with faciooculoskeletal anomalies syndrome
  • Congenital anomaly of aortic arch AND/OR descending aorta
  • Congenital asymmetry of jaw
  • Congenital atrophy of optic nerve
  • Congenital cleft nose
  • Congenital conductive hearing loss
  • Congenital corneal dystrophy
  • Congenital cubitus valgus
  • Congenital diaphragmatic hernia
  • Congenital dislocation of left hip
  • Congenital dislocation of right hip
  • Congenital disorder of facial nerve
  • Congenital dysplasia of nail unit
  • Congenital facial asymmetry
  • Congenital facial nerve palsy
  • Congenital generalized hypertrichosis
  • Congenital hypoplasia of bone of radius and/or ulna
  • Congenital hypoplasia of ulna
  • Congenital hypotrichia
  • Congenital labioscrotal agenesis, cerebellar malformation, corneal dystrophy, facial dysmorphism syndrome
  • Congenital mandibular asymmetry
  • Congenital nonprogressive myopathy with Moebius and Robin sequences
  • Congenital omphalocele
  • Congenital sixth nerve palsy
  • Congenital stenosis of carotid artery
  • Congenital umbilical hernia
  • Connective tissue disorder due to lysyl hydroxylase-3 deficiency
  • Contracture with ectodermal dysplasia and orofacial cleft syndrome
  • Cortical blindness
  • Crane Heise syndrome
  • Craniodigital syndrome and intellectual disability syndrome
  • Craniofacial dysplasia osteopenia syndrome
  • Craniofacial dyssynostosis syndrome
  • Craniofacial microsomia
  • Craniofaciofrontodigital syndrome
  • Craniofrontonasal dysplasia
  • Craniomicromelic syndrome
  • Cryptophthalmos syndrome
  • Cutis laxa, autosomal recessive
  • Cyclops
  • Cyclops hypognathus
  • Cyprus facial neuromusculoskeletal syndrome
  • Dandy-Walker syndrome
  • de Barsey syndrome
  • Deafness and intellectual disability Martin Probst type syndrome
  • Deletion of part of chromosome 10
  • Deletion of part of chromosome 4
  • Deletion of part of chromosome 5
  • Deletion of part of long arm of chromosome 5
  • Developmental delay, facial dysmorphism syndrome due to MED13L deficiency
  • Developmental malformation of branchial arch
  • Dextrotransposition of aorta
  • Diencephalic mesencephalic junction dysplasia
  • Dislocation of hip and facial dysmorphism syndrome
  • Dobrow syndrome
  • Duane's syndrome
  • DYRK1A-related intellectual disability syndrome
  • Dysplasia with defective mineralization
  • Ear, face and neck congenital anomalies
  • Early-onset epileptic encephalopathy, cortical blindness, intellectual disability, facial dysmorphism syndrome
  • Early-onset seizures, distal limb anomalies, facial dysmorphism, global developmental delay syndrome
  • Edinburgh malformation syndrome
  • Emery Nelson syndrome
  • Epiphyseal dysplasia, hearing loss, dysmorphism syndrome
  • Expressive dysphasia
  • Facial dysmorphism, anorexia, cachexia, eye and skin anomalies syndrome
  • Facial dysmorphism, cleft palate, loose skin syndrome
  • Facial dysmorphism, conductive hearing loss, heart defect syndrome
  • Facial dysmorphism, developmental delay, behavioral abnormalities syndrome due to 10p11.21p12.31 microdeletion
  • Facial dysmorphism, hypertrichosis, epilepsy, intellectual disability/developmental delay, gingival overgrowth syndrome
  • Facial dysmorphism, immunodeficiency, livedo, short stature syndrome
  • Facial dysmorphism, lens dislocation, anterior segment abnormalities, spontaneous filtering bleb syndrome
  • Facial dysmorphism, macrocephaly, myopia, Dandy-Walker malformation syndrome
  • Facio-auriculo-vertebral spectrum
  • Familial aplasia of the vermis
  • Familial omphalocele syndrome with facial dysmorphism
  • Fetal growth restriction
  • Filippi syndrome
  • Fine Lubinsky syndrome
  • First and second branchial arch syndrome
  • First arch syndrome
  • Flat face, microstomia, ear anomaly syndrome
  • Frank-Ter Haar syndrome
  • Freeman-Sheldon syndrome
  • Frontonasal dysplasia sequence
  • Frontonasal dysplasia, severe microphthalmia, severe facial clefting syndrome
  • Fryns macrocephaly
  • Fryns Smeets Thiry syndrome
  • Fryns syndrome
  • Gabriele-de Vries syndrome
  • Genetic syndromic childhood obesity
  • Global developmental delay, intellectual disability, facial dysmorphism, pseudo Pelger-Huët anomaly syndrome
  • Goldberg Shprintzen megacolon syndrome
  • Goldenhar syndrome
  • Gollop syndrome
  • Gorlin-Chaudhry-Moss syndrome
  • Greig cephalopolysyndactyly syndrome
  • Greig cephalopolysyndactyly, contiguous gene syndrome
  • Grob's syndrome
  • Hadziselimovic syndrome
  • Hall Riggs syndrome
  • Hallermann-Streiff syndrome
  • Hanhart's syndrome
  • Harrod syndrome
  • Hip pathological dislocation
  • Holzgreve syndrome
  • Hyperreflexia
  • Hypertelorism
  • Hypogonadotropic hypogonadism, severe microcephaly, sensorineural hearing loss, dysmorphism syndrome
  • Illum syndrome
  • Imagawa Matsumoto syndrome
  • Immuno-osseous dysplasia
  • Intellectual disability Buenos Aires type
  • Intellectual disability Wolff type
  • Intellectual disability, brachydactyly, Pierre Robin syndrome
  • Intellectual disability, cardiac anomalies, short stature, joint laxity syndrome
  • Intellectual disability, coarse face, macrocephaly, cerebellar hypotrophy syndrome
  • Intellectual disability, craniofacial dysmorphism, cryptorchidism syndrome
  • Intellectual disability, craniofacial dysmorphism, hypogonadism, diabetes mellitus syndrome
  • Intellectual disability, expressive aphasia, facial dysmorphism syndrome
  • Intellectual disability, facial dysmorphism syndrome due to SETD5 haploinsufficiency
  • Intellectual disability, facial dysmorphism, hand anomalies syndrome
  • Intellectual disability, nasal speech, craniofacial dysmorphism syndrome
  • Intellectual disability, obesity, brain malformation, facial dysmorphism syndrome
  • Intellectual disability, seizures, abnormal gait, facial dysmorphism syndrome
  • Intellectual disability, severe speech delay, mild dysmorphism syndrome
  • Intellectual disability, speech delay, dysmorphic features, T cell abnormalities syndrome
  • Internal carotid artery stenosis
  • Intrauterine growth retardation, micrognathia, short stature, facial dysmorphism, rhizomelic shortening syndrome
  • Isolated hereditary congenital facial paralysis
  • Isotretinoin-like syndrome
  • Jawad syndrome
  • Joint contractures, developmental delay, Pierre Robin syndrome
  • Joubert syndrome
  • Joubert syndrome with orofaciodigital defect
  • Juberg Marsidi syndrome
  • Kagami Ogata syndrome
  • Kapur Toriello syndrome
  • Keipert syndrome
  • Keppen Lubinsky syndrome
  • King Denborough syndrome
  • Klippel-Feil anomaly, myopathy, facial dysmorphism syndrome
  • Klippel-Feil sequence
  • Koolen De Vries syndrome
  • Lamb Shaffer syndrome
  • Lanugo
  • Larsen-like syndrome B3GAT3 type
  • Lentiglobus
  • Lethal faciocardiomelic dysplasia
  • Lethal polymalformative syndrome Boissel type
  • Livedo reticularis
  • Lymphedema of lower extremity
  • Lymphedema, atrial septal defect, facial changes syndrome
  • Lysine demethylase 3B-related intellectual disability, facial dysmorphism, short stature syndrome
  • Marfanoid habitus, facial dysmorphism, skeletal abnormality, heart defect syndrome
  • Marfanoid physique
  • McDonough syndrome
  • Megalocornea
  • Mehes syndrome
  • Melnick-Fraser syndrome
  • Menke Hennekam syndrome
  • Metopic ridging, ptosis, facial dysmorphism syndrome
  • Microcephaly, facial dysmorphism, ocular anomalies, multiple congenital anomalies syndrome
  • Microcephaly, short stature, intellectual disability, facial dysmorphism syndrome
  • Microphthalmos due to Fryns syndrome
  • Microstomia
  • Microtia
  • Mietens syndrome
  • Miller syndrome
  • Moebius syndrome
  • Moebius syndrome, axonal neuropathy, hypogonadotropic hypogonadism syndrome
  • Mohr syndrome
  • Mowat-Wilson syndrome
  • Moyamoya angiopathy, short stature, facial dysmorphism, hypergonadotropic hypogonadism syndrome
  • Moyamoya disease
  • Mucopolysaccharidosis-like plus disease
  • Multicentric osteolysis nodulosis arthropathy spectrum
  • Multiple malformation syndrome with facial defects as major feature
  • Multiple malformation syndrome with facial-limb defects as major feature
  • Multiple malformation syndrome, moderate short stature, facial
  • Multiple malformation syndrome, small stature, without skeletal dysplasia
  • Nager syndrome
  • Night blindness
  • Night blindness, skeletal anomalies, dysmorphism syndrome
  • Nijmegen breakage syndrome-like disorder
  • Non-specific syndromic intellectual disability
  • Occipital encephalocele
  • Oculoauriculofrontonasal syndrome
  • Oculo-auriculo-vertebral spectrum
  • Oculocerebrodental syndrome
  • Oculocerebrofacial syndrome Kaufman type
  • Oculomaxillofacial dysostosis
  • Oculo-palato-digital syndrome
  • Ogden syndrome
  • Ophthalmological abnormalities, facial dysmorphism, intellectual disability syndrome
  • Ophthalmomandibulomelic dysplasia
  • Opocephalus
  • Oral-facial-digital syndrome
  • Oro-facial digital syndrome type 1
  • Oro-facial digital syndrome type 10
  • Oro-facial digital syndrome type 11
  • Oro-facial digital syndrome type 12
  • Oro-facial digital syndrome type 13
  • Oro-facial digital syndrome type 14
  • Oro-facial digital syndrome type 5
  • Oro-facial digital syndrome type 8
  • Orofacial-digital syndrome III
  • Orofacial-digital syndrome IV
  • Oromandibular-limb hypogenesis spectrum
  • Otocephalic syndrome
  • Otofaciocervical syndrome
  • Otopalatodigital syndrome spectrum disorder
  • Oto-palato-digital syndrome, type I
  • Oto-palato-digital syndrome, type II
  • Palatal anomalies, widely spaced teeth, facial dysmorphism, developmental delay syndrome
  • Pallister W syndrome
  • Pathological dislocation of bilateral hips
  • Pathological dislocation of left hip
  • Pathological dislocation of right hip
  • PDE4D haploinsufficiency syndrome
  • Pelviscapular dysplasia
  • Peripheral axonal neuropathy
  • Perlman syndrome
  • Pierpont syndrome
  • Pierre Robin sequence faciodigital anomaly syndrome
  • Pilotto syndrome
  • Plagiocephaly
  • Poliosis
  • Postaxial polydactyly, anterior pituitary anomalies, facial dysmorphism syndrome
  • Potter's facies
  • Prieto Badia Mulas syndrome
  • Progressive macrocephaly
  • Proximal deletion of long arm of chromosome 4
  • Pseudoaminopterin syndrome
  • Pseudopapilledema
  • PYCR2-related microcephaly, progressive leukoencephalopathy
  • Pyrroline-5-carboxylate reductase 1 related de Barsy syndrome
  • Ramos Arroyo syndrome
  • Renal agenesis
  • Rhizomelia
  • RIDDLE syndrome
  • Right aortic arch
  • Robin sequence
  • Robin sequence and oligodactyly syndrome
  • Roifman syndrome
  • Rozin Hertz Goodman syndrome
  • Ruvalcaba syndrome
  • Sanjad Sakati syndrome
  • SATB2-associated syndrome
  • SCARF syndrome
  • Schilbach Rott syndrome
  • Seaver Cassidy syndrome
  • Severe intellectual disability, hypotonia, strabismus, coarse face, planovalgus syndrome
  • Severe intellectual disability, poor language, strabismus, grimacing face, long fingers syndrome
  • Severe intellectual disability, short stature, behavioral abnormalities, facial dysmorphism syndrome
  • Severe X-linked intellectual disability Gustavson type
  • Short stature, onychodysplasia, facial dysmorphism, hypotrichosis syndrome
  • Short stature, Pierre Robin sequence, cleft mandible, hand anomalies, clubfoot syndrome
  • Short stature, unique facies, enamel hypoplasia, progressive joint stiffness, high-pitched voice syndrome
  • Short ulna, dysmorphism, hypotonia, intellectual disability syndrome
  • Sixth cranial nerve finding
  • Sonoda syndrome
  • Speech delay
  • Spherophakia
  • Spondylometaphyseal dysplasia, bowed forearms, facial dysmorphism syndrome
  • STAG1-related intellectual disability, facial dysmorphism, gastroesophageal reflux syndrome
  • STAR syndrome
  • Steel syndrome
  • Steinfeld syndrome
  • Stenosis of intracranial carotid artery
  • Syndromic multisystem autoimmune disease due to ITCH deficiency
  • Syndromic X-linked intellectual disability type 11
  • TARP syndrome
  • Teebi Shaltout syndrome
  • Telecanthus
  • Temple syndrome
  • Temtamy syndrome
  • Thakker Donnai syndrome
  • Thin ribs, tubular bones, dysmorphism syndrome
  • THOC6-related developmental delay-microcephaly-facial dysmorphism syndrome
  • TMEM94-associated congenital heart defect, facial dysmorphism, developmental delay syndrome
  • Tongue absent
  • Toriello Carey syndrome
  • Townes syndrome
  • Van den Ende-Gupta syndrome
  • Velofacioskeletal syndrome
  • Ventricular extrasystoles with syncope, perodactyly and Robin sequence syndrome
  • WAC-related facial dysmorphism, developmental delay, behavioral abnormalities syndrome
  • Weill-Marchesani syndrome
  • White forelock with malformations syndrome
  • Wildervanck syndrome
  • Wilson Turner syndrome
  • Witteveen Kolk syndrome
  • X-linked female restricted facial dysmorphism, short stature, choanal atresia, intellectual disability
  • X-linked intellectual disability and epilepsy with progressive joint contracture and facial dysmorphism syndrome
  • X-linked intellectual disability and hypotonia with facial dysmorphism and aggressive behavior syndrome
  • X-linked intellectual disability hypotonic face syndrome
  • X-linked intellectual disability Nascimento type
  • X-linked intellectual disability Seemanova type
  • X-linked intellectual disability Siderius type
  • X-linked intellectual disability Stevenson type
  • X-linked intellectual disability Stoll type
  • X-linked intellectual disability with cubitus valgus and dysmorphism syndrome
  • X-linked intellectual disability with plagiocephaly syndrome
  • X-linked intellectual disability, global development delay, facial dysmorphism, sacral caudal remnant syndrome
  • X-linked sensorineural hearing loss
  • Zechi Ceide syndrome

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q87.0: its own notes plus those printed at Q87 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Acrocephalopolysyndactyly
  • Acrocephalosyndactyly [Apert]
  • Cryptophthalmos syndrome
  • Cyclopia
  • Goldenhar syndrome
  • Moebius syndrome
  • Oro-facial-digital syndrome
  • Robin syndrome
  • Whistling face

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Use Additional Code

Add a second code, after this one, to fully describe the condition.

From Q87 Other specified congenital malformation syndromes affecting multiple systems applies to 21 codes
  • code(s) to identify all associated manifestations

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q87.0, its category, or a range that includes it.

Excludes1 9

These codes carry an Excludes1 note naming Q87.0: they are not reported together with it, unless the two conditions are unrelated.

  • M26.0 Major anomalies of jaw size
    Robin's syndrome (Q87.0)
  • Q04 Other congenital malformations of brain
    cyclopia (Q87.0)
  • Q10 Congenital malformations of eyelid, lacrimal apparatus and orbit
    cryptophthalmos syndrome (Q87.0)
  • Q11.2 Microphthalmos
    cryptophthalmos syndrome (Q87.0)
  • Q18 Other congenital malformations of face and neck
    cyclopia (Q87.0)
  • Q18 Other congenital malformations of face and neck
    malformation syndromes affecting facial appearance (Q87.0)
  • Q67 Congenital musculoskeletal deformities of head, face, spine and chest
    congenital malformation syndromes classified to Q87.- names Q87.-, which includes this code
  • Q75 Other congenital malformations of skull and face bones
    congenital malformation syndromes classified to Q87.- names Q87.-, which includes this code
  • Q89.7 Multiple congenital malformations, not elsewhere classified
    congenital malformation syndromes affecting multiple systems (Q87.-) names Q87.-, which includes this code

Excludes2 1

These codes carry an Excludes2 note naming Q87.0: its condition is not part of those codes, and both may be reported when the patient has both.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Fraser Syndrome

    rare autosomal recessive congenital malformation syndrome characterized by cryptophthalmos, syndactyly and urogenital abnormalities. other anomalies of bone, ear, lung, and nose are common. mutations on fras1 and frem2 are associated with the syndrome.

  • Goldenhar Syndrome

    mandibulofacial dysostosis with congenital eyelid dermoids.

  • Weill-Marchesani Syndrome

    rare congenital disorder of connective tissue characterized by brachydactyly, joint stiffness, childhood onset of ocular abnormalities (e.g., microspherophakia, ectopia lentis; glaucoma), and proportionate short stature. cardiovascular anomalies are occasionally seen.

Patient EducationClinical

Craniofacial Abnormalities

Craniofacial is a medical term that relates to the bones of the skull and face. Craniofacial abnormalities are birth defects of the face or head. Some, like cleft lip and palate, are among the most common of all birth defects. Others are very rare. Most of them affect how a person's face or head looks.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q87.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
755.55 Acrocephalosyndactyly
Approximate The match is approximate rather than exact.
ICD-9-CM
756.0 Anomal skull/face bones
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q87.0Overview

Is Q87.0 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation syndromes predominantly affecting facial appearance on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q87.0 group to?

When congenital malformation syndromes predominantly affecting facial appearance is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q87.0 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation syndromes predominantly affecting facial appearance on inpatient claims. The code appears in the Other congenital malformations (Q80-Q89) range of the CMS exempt list.

Does Q87.0 need an additional code?

When the condition applies, yes. The Use Additional Code note at Q87, which applies to Q87.0, reads: code(s) to identify all associated manifestations. The additional code is reported after Q87.0.

What is the ICD-9 equivalent of Q87.0?

Under the General Equivalence Mappings, congenital malformation syndromes predominantly affecting facial appearance converts to ICD-9-CM 755.55 (acrocephalosyndactyly) and 756.0 (anomal skull/face bones). The mapping is approximate, so confirm the match fits the documentation.