2027 ICD-10-CM Diagnosis Code Q84.1Congenital morphological disturbances of hair, not elsewhere classified
ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q84
- Billable — Valid for Submission
- POA Exempt
- Not Chronic
Q84.1 is a billable ICD-10-CM diagnosis code for congenital morphological disturbances of hair, not elsewhere classified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 606 through 607. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q84.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations (Q80-Q89).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Autosomal dominant familial wooly hair
- Autosomal recessive familial wooly hair
- Bayonet hair
- Beaded hair
- Björnstad syndrome
- Black locks, oculocutaneous albinism, AND deafness of the sensorineural type
- Congenital dysplasia of nail unit
- Congenital ringed hair
- Congenital wooly hair
- Curly hair, ankyloblepharon, nail dysplasia syndrome
- Ectodermal dysplasia, syndactyly and pili torti
- Pili annulati
- Pili torti
- Pili torti onychodysplasia syndrome
- Pili torti with developmental delay and neurological abnormality syndrome
- Skin fragility, wooly hair, palmoplantar keratoderma syndrome
- Trichostasis spinulosa
- Uncombable hair, retinal pigmentary dystrophy, dental anomaly and brachydactyly syndrome
- Wooly hair and palmoplantar keratoderma with dilated cardiomyopathy syndrome
- Wooly hair with palmoplantar keratoderma syndrome
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q84.1: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Beaded hair
- Monilethrix
- Pili annulati
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
- Menkes' kinky hair syndrome (E83.09)
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q84.1, its category, or a range that includes it.
Excludes1 4
These codes carry an Excludes1 note naming Q84.1: they are not reported together with it, unless the two conditions are unrelated.
- L67 Hair color and hair shaft abnormalitiesmonilethrix (Q84.1)
- L67 Hair color and hair shaft abnormalitiespili annulati (Q84.1)
- Block L60-L75 Disorders of skin appendagescongenital malformations of integument (Q84.-) names Q84.-, which includes this code
- P83 Other conditions of integument specific to newborn
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Beaded hair (congenital) Q84.1
Monilethrix (congenital) Q84.1
Ringed hair (congenital) Q84.1
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Monilethrix
rare autosomal dominant disorder of the hair shaft. the clinical features of the disease include hypotrichosis, dry, and/or brittle hair, with varying degrees of alopecia. mutations in the hair-specific keratin genes krthb1, krthb3, or krthb6 are associated with monilethrix. autosomal recessive monilethrix with limited hypotrichosis are also known. mutations in dsg4, liph, and p2ry5 protein genes are associated with the recessive form of monilethrix.
Patient EducationClinical
Hair Problems
The average person has 5 million hairs. Hair grows all over your body except on your lips, palms, and the soles of your feet. It takes about a month for healthy hair to grow half an inch. Most hairs grow for up to six years and then fall out. New hairs grow in their place.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q84.1 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q84.1Overview
Is Q84.1 (Other congenital malformations of integument) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report congenital morphological disturbances of hair, not elsewhere classified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q84.1 group to?
When congenital morphological disturbances of hair, not elsewhere classified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 607, 606, with relative weights from 0.8772 to 1.5721 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q84.1 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital morphological disturbances of hair, not elsewhere classified on inpatient claims. The code appears in the Other congenital malformations (Q80-Q89) range of the CMS exempt list.
Can Q84.1 be reported with E83.09?
Not as a rule. The Excludes1 note on Q84.1 lists "Menkes' kinky hair syndrome (E83.09)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
What is the ICD-9 equivalent of Q84.1?
Under the General Equivalence Mappings, congenital morphological disturbances of hair, not elsewhere classified converts to ICD-9-CM 757.4 (hair anomalies NEC). The mapping is approximate, so confirm the match fits the documentation.
