2026 ICD-10-CM Diagnosis Code Q77.2Short rib syndrome

ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q77

ICD-10-CM Q77.2
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q77.2 is a billable ICD-10-CM diagnosis code for short rib syndrome. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q77.2
Billable Status
Yes — Valid for Submission
Code Describes
Short rib syndrome
Short Description
Short rib syndrome
Same as the full description in the CMS dataset.
Parent Code
Q77
Osteochondrodysplasia with defects of growth of tubular bones and spine

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategoryQ77Osteochondrodysplasia with defects of growth of tubular bones and spine
This CodeQ77.2Short rib syndrome

Present on Admission (POA)Billing

Q77.2 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Cloverleaf skull syndrome
  • Cloverleaf skull, asphyxiating thoracic dysplasia syndrome
  • Complex craniosynostosis
  • Congenital hypoplasia of bone of pelvis
  • Familial aplasia of the vermis
  • Jeune thoracic dystrophy
  • Joubert syndrome
  • Joubert syndrome with Jeune asphyxiating thoracic dystrophy
  • Micromelia
  • Parieto-occipital craniosynostosis
  • Sagittal craniosynostosis
  • Short rib
  • Short rib dysplasia
  • Short rib polydactyly syndrome
  • Short rib polydactyly syndrome Saldino Noonan type
  • Short rib polydactyly syndrome type 5
  • Short rib-polydactyly syndrome, Majewski type
  • Thin ribs, tubular bones, dysmorphism syndrome
  • Thoracomelic dysplasia
  • Type III short rib polydactyly syndrome
  • Type IV short rib polydactyly syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Asphyxiating thoracic dysplasia Jeune

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Dysplasia
      • asphyxiating thoracic (congenital)
    • Dystrophy, dystrophia
      • thoracic, asphyxiating
    • Jeune's disease
    • Short, shortening, shortness
      • rib syndrome
    • Syndrome
      • short
        • rib

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Joubert Syndrome

    a rare genetic syndrome characterized by the hypoplasia or absence of the cerebellar vermis. signs and symptoms include rapid breathing (hyperpnea), sleep apnea, abnormal eye movements, mental retardation, and ataxia.

  • Joubert Syndrome 17|JBTS17

    an autosomal recessive subtype of joubert syndrome caused by mutation(s) in the cplane1 gene, encoding ciliogenesis and planar polarity effector 1.

  • Joubert Syndrome 3|JBTS3

    an autosomal recessive subtype of joubert syndrome caused by mutation(s) in the ahi1 gene, encoding jouberin.

  • Joubert Syndrome 4

    a rare genetic syndrome caused by mutations in the nphp1 gene. it is characterized by the hypoplasia or absence of the cerebellar vermis. signs and symptoms include rapid breathing (hyperpnea), sleep apnea, abnormal eye movements, mental retardation, and ataxia.

  • Joubert Syndrome 7|JBTS7

    an autosomal recessive sub-type of joubert syndrome caused by mutation(s) in the rpgrip1l gene, encoding a protein thought to function in programmed cell death. it is characterized by cerebellar and oculomotor apraxia, hypotonia and psychomotor delay, neonatal respiratory abnormalities, renal abnormalities, and retinal dystrophy.

  • Joubert Syndrome 9|JBTS9

    an autosomal recessive subtype of joubert syndrome caused by mutation(s) in the cc2d2a gene, encoding coiled-coil and c2 domain-containing protein 2a.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q77.2 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
756.3 Rib & sternum anomal NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q77.2Overview

Is Q77.2 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report short rib syndrome on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q77.2 group to?

When short rib syndrome is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q77.2 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for short rib syndrome on inpatient claims.

What is the ICD-9 equivalent of Q77.2?

Under the General Equivalence Mappings, short rib syndrome converts to ICD-9-CM 756.3 (rib & sternum anomal NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.