2026 ICD-10-CM Diagnosis Code Q61.4Renal dysplasia

ICD-10-CM Codes›Q00-Q99›Q60-Q64›Q61

ICD-10-CM Q61.4
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q61.4 is a billable ICD-10-CM diagnosis code for renal dysplasia. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 698 through 700. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q61.4
Billable Status
Yes — Valid for Submission
Code Describes
Renal dysplasia
Short Description
Renal dysplasia
Same as the full description in the CMS dataset.
Parent Code
Q61
Cystic kidney disease

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ60-Q64Congenital malformations of the urinary system
CategoryQ61Cystic kidney disease
This CodeQ61.4Renal dysplasia

Present on Admission (POA)Billing

Q61.4 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Bilateral multicystic renal dysplasia
  • Bilateral renal dysplasia
  • Bilateral secondary renal dysplasia
  • BRESEK syndrome
  • Cystic dysplasia of kidney
  • Dysplasia of left kidney
  • Dysplasia of right kidney
  • Fibrosis of pancreas
  • Hydranencephaly
  • Left kidney absent
  • Left renal agenesis
  • Left renal agenesis co-occurrent with right renal dysplasia
  • MARCH syndrome
  • Multicystic renal dysplasia
  • Multiple renal cysts
  • Nephronophthisis
  • Primary renal dysplasia
  • Renal agenesis
  • Renal dysplasia
  • Renal dysplasia and retinal aplasia
  • Renal dysplasia due to fetal exposure to angiotensin converting enzyme inhibitor
  • Renal hepatic pancreatic dysplasia
  • Retinal pigment epithelial dystrophy
  • Right kidney absent
  • Right renal agenesis
  • Right renal agenesis co-occurrent with left renal dysplasia
  • Saldino-Mainzer dysplasia
  • Secondary renal dysplasia
  • Thymic, renal, anal, lung dysplasia syndrome
  • Torticollis, keloids, cryptorchidism, renal dysplasia syndrome
  • Ulbright Hodes syndrome
  • Unilateral multicystic renal dysplasia

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Multicystic dysplastic kidney
  • Multicystic kidney (development)
  • Multicystic kidney disease
  • Multicystic renal dysplasia

Type 1 Excludes

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disease, diseased
      • kidney (functional) (pelvis)
        • multicystic
    • Dysplasia
      • kidney
    • Dysplasia
      • kidney
        • multicystic
    • Dysplasia
      • renal
    • Dysplasia
      • renal
        • multicystic
    • Multicystic kidney(development)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Hydranencephaly

    a congenital condition where the greater portions of the cerebral hemispheres and corpus striatum are replaced by csf and glial tissue. the meninges and the skull are well formed, which is consistent with earlier normal embryogenesis of the telencephalon. bilateral occlusions of the internal carotid arteries in utero is a potential mechanism. clinical features include intact brainstem reflexes without evidence of higher cortical activity. (menkes, textbook of child neurology, 5th ed, p307)

  • Multinucleated Neurons, Anhydramnios, Renal Dysplasia, Cerebellar Hypoplasia and Hydranencephaly|MARCH

    a lethal autosomal recessive condition caused by mutation(s) in the cep55 gene, encoding centrosomal protein of 55 kda. it is characterized by renal dysplasia, anhydramnios, hydrancephaly, cerebellar hypoplasia, and multinucleated neurons in remaining brain tissue.

  • Bilateral Renal Agenesis

    a congenital abnormality characterized by the absence of both kidneys.

  • Renal Agenesis

    a congenital abnormality characterized by the absence of one or both kidneys.

  • Unilateral Renal Agenesis|Congenital Single Kidney|Congenital Solitary Kidney|Congenital Solitary Kidney

    a congenital abnormality characterized by the presence of only one kidney.

  • Bilateral Renal Dysplasia

    a finding of congenital malformations in both kidneys characterized by the presence of cysts of various sizes, primitive ducts, islands of metaplastic cartilage and undifferentiated mesenchyme, and the absence of cortico-medullary demarcation.

  • Nephrocystin-1|Juvenile Nephronophthisis 1 Protein|NPHP1

    nephrocystin-1 (732 aa, ~83 kda) is encoded by the human nphp1 gene. this protein is involved in the modulation of signaling.

  • Nephronophthisis

    progressive tubulointerstitial injury, inherited in an autosomal recessive pattern, caused by mutations in genes involved in ciliary function, which may result in an end stage renal failure.

  • Nephronophthisis 1|Familial Juvenile Nephronophthisis|Juvenile Nephronophthisis|NPH1

    progressive tubulointerstitial nephritis inherited in an autosomal recessive manner. it is caused by mutations in the nphp1 gene. patients present with anemia, polyuria, and polydipsia during childhood. the progressive bilateral kidney damage results in renal failure.

  • NPHP1 Gene|NPHP1|NPHP1|Nephronophthisis 1 (Juvenile) Gene

    this gene is involved in the mediation of signal transduction.

  • NPHP1 wt Allele|FLJ97602|JBTS4|NPH1|Nephronophthisis 1 (Juvenile) wt Allele|SLSN1

    human nphp1 wild-type allele is located in the vicinity of 2q13 and is approximately 83 kb in length. this allele, which encodes nephrocystin-1 protein, plays a role in the progression of adhesion-dependent signaling pathways. mutations in the gene are associated with familial juvenile nephronophthisis type 1, senior-loken syndrome type 1, and joubert syndrome type 4.

  • Hydranencephaly

    a rare congenital brain disorder in which the cerebral hemispheres are absent and replaced by sacs that contain cerebrospinal fluid. signs and symptoms include irritability, increased muscle tone, seizures, and hydrocephalus. the prognosis is poor.

  • Multinucleated Neurons, Anhydramnios, Renal Dysplasia, Cerebellar Hypoplasia And Hydranencephaly|MARCH

    a lethal autosomal recessive condition caused by mutation(s) in the cep55 gene, encoding centrosomal protein of 55 kda. it is characterized by renal dysplasia, anhydramnios, hydrancephaly, cerebellar hypoplasia, and multinucleated neurons in remaining brain tissue.

Patient EducationClinical

Kidney Cysts

A cyst is a fluid-filled sac. You may get simple kidney cysts as you age; they are usually harmless. There are also some diseases which cause kidney cysts. One type is polycystic kidney disease (PKD). It runs in families. In PKD, many cysts grow in the kidneys. This can enlarge the kidneys and make them work poorly.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q61.4 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
753.15 Renal dysplasia
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q61.4Overview

Is Q61.4 (Cystic kidney disease) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report renal dysplasia on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q61.4 group to?

When renal dysplasia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 698, 699, 700, with relative weights from 0.6899 to 1.6544 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q61.4 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for renal dysplasia on inpatient claims.

What is the ICD-9 equivalent of Q61.4?

Under the General Equivalence Mappings, renal dysplasia converts to ICD-9-CM 753.15 (renal dysplasia). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.