2027 ICD-10-CM Diagnosis Code Q61.4Renal dysplasia
ICD-10-CM Codes›Q00-Q99›Q60-Q64›Q61
- Billable — Valid for Submission
- CC — Complication or Comorbidity
- POA Exempt
- Chronic Condition
Q61.4 is a billable ICD-10-CM diagnosis code for renal dysplasia. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 698 through 700. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 2 closely related codes. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q61.4 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the urinary system (Q60-Q64).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Bilateral multicystic renal dysplasia
- Bilateral renal dysplasia
- Bilateral secondary renal dysplasia
- BRESEK syndrome
- Cystic dysplasia of kidney
- Dysplasia of left kidney
- Dysplasia of right kidney
- Fibrosis of pancreas
- Hydranencephaly
- Left kidney absent
- Left renal agenesis
- Left renal agenesis co-occurrent with right renal dysplasia
- MARCH syndrome
- Multicystic renal dysplasia
- Multiple renal cysts
- Nephronophthisis
- Primary renal dysplasia
- Renal agenesis
- Renal dysplasia
- Renal dysplasia and retinal aplasia
- Renal dysplasia due to fetal exposure to angiotensin converting enzyme inhibitor
- Renal hepatic pancreatic dysplasia
- Retinal pigment epithelial dystrophy
- Right kidney absent
- Right renal agenesis
- Right renal agenesis co-occurrent with left renal dysplasia
- Saldino-Mainzer dysplasia
- Secondary renal dysplasia
- Thymic, renal, anal, lung dysplasia syndrome
- Torticollis, keloids, cryptorchidism, renal dysplasia syndrome
- Ulbright Hodes syndrome
- Unilateral multicystic renal dysplasia
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q61.4: its own notes plus those printed at Q61 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Multicystic dysplastic kidney
- Multicystic kidney (development)
- Multicystic kidney disease
- Multicystic renal dysplasia
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q61.4, its category, or a range that includes it.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Disease, diseased See Also: Syndrome;
Dysplasia See Also: Anomaly;
kidney Q61.4
multicystic Q61.4
renal Q61.4
multicystic Q61.4
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Multicystic Dysplastic Kidney
a nongenetic defect due to malformation of the kidney which appears as a bunch of grapes with multiple renal cysts but lacking the normal renal bean shape, and the collection drainage system. this condition can be detected in-utero with ultrasonography.
Patient EducationClinical
Kidney Cysts
A cyst is a fluid-filled sac. You may get simple kidney cysts as you age; they are usually harmless. There are also some diseases which cause kidney cysts. One type is polycystic kidney disease (PKD). It runs in families. In PKD, many cysts grow in the kidneys. This can enlarge the kidneys and make them work poorly.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q61.4 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q61.4Overview
What is the ICD-10 code for renal dysplasia?
The ICD-10-CM code for renal dysplasia is Q61.4 (sometimes written as Q614). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q61.4 (Cystic kidney disease) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report renal dysplasia on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q61.4 group to?
When renal dysplasia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 699, 698, 700, with relative weights from 0.6740 to 1.6400 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q61.4 a CC or MCC?
CMS lists Q61.4 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 2 closely related codes in its exclusion list.
Is Q61.4 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for renal dysplasia on inpatient claims. The code appears in the Congenital malformations of the urinary system (Q60-Q64) range of the CMS exempt list.
