2026 ICD-10-CM Diagnosis Code N00Acute nephritic syndrome

ICD-10-CM Codes›N00–N99›N00-N08›N00

ICD-10-CM N00
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

N00 is a non-billable ICD-10-CM category code for acute nephritic syndrome, so it cannot be submitted on claims. Use a more specific code from this category instead, such as N00.0, N00.1, N00.2, and N00.3.

Code Identity

ICD-10-CM Code
N00
Billable Status
No — Non-Billable Category
Code Describes
Acute nephritic syndrome
Short Description
Acute nephritic syndrome
Same as the full description in the CMS dataset.
Chapter
N00-N08
Glomerular diseases

Code Classification

ChapterN00–N99Diseases of the genitourinary system
SectionN00-N08Glomerular diseases
CategoryN00Acute nephritic syndrome
This CodeN00Acute nephritic syndrome

Specific Coding for Acute nephritic syndromeOverview

Non-specific codes like N00 require more characters. Use one of these billable codes instead:

  • Use N00.0 for Acute nephritic syndrome with minor glomerular abnormality

  • Use N00.1 for Acute nephritic syndrome with focal and segmental glomerular lesions

  • Use N00.2 for Acute nephritic syndrome with diffuse membranous glomerulonephritis

  • Use N00.3 for Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis

  • Use N00.4 for Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis

  • Use N00.5 for Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis

  • Use N00.6 for Acute nephritic syndrome with dense deposit disease

  • Use N00.7 for Acute nephritic syndrome with diffuse crescentic glomerulonephritis

  • Use N00.8 for Acute nephritic syndrome with other morphologic changes

  • Use N00.9 for Acute nephritic syndrome with unspecified morphologic changes

  • Use N00.A for Acute nephritic syndrome with C3 glomerulonephritis

  • N00.B for Acute nephritic syndrome with immune complex membranoproliferative glomerulonephritis

  • Use N00.B1 for Acute nephritic syndrome with idiopathic immune membranoproliferative glomerulonephritis (IC-MPGN)

  • Use N00.B2 for Acute nephritic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Includes

  • acute glomerular disease
  • acute glomerulonephritis
  • acute nephritis

Type 1 Excludes

  • acute tubulo-interstitial nephritis N10
  • nephritic syndrome NOS N05

Patient EducationClinical

Kidney Diseases

You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About N00Overview

Is N00 (Acute nephritic syndrome) a billable code?

No. This is a category header that groups the codes for acute nephritic syndrome, and headers cannot be submitted on claims. Claims for acute nephritic syndrome need a more specific code from this category, such as N00.0, N00.1, and N00.2.