2026 ICD-10-CM Diagnosis Code J84.848Other interstitial lung diseases of childhood

ICD-10-CM Codes›J00–J99›J80-J84›J84

ICD-10-CM J84.848
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

J84.848 is a billable ICD-10-CM diagnosis code for other interstitial lung diseases of childhood. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 196 through 198. Coders also document this condition as congenital nephrotic syndrome, interstitial lung disease, epidermolysis bullosa syndrome. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified lower respiratory disease.

Code Identity

ICD-10-CM Code
J84.848
Billable Status
Yes — Valid for Submission
Code Describes
Other interstitial lung diseases of childhood
Short Description
Other interstitial lung diseases of childhood
Same as the full description in the CMS dataset.
Parent Code
J84.84
Other interstitial lung diseases of childhood

Code Classification

ChapterJ00–J99Diseases of the respiratory system
SectionJ80-J84Other respiratory diseases principally affecting the interstitium
CategoryJ84Other interstitial pulmonary diseases
This CodeJ84.848Other interstitial lung diseases of childhood

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Congenital nephrotic syndrome, interstitial lung disease, epidermolysis bullosa syndrome
  • Interstitial lung disease
  • Interstitial lung disease due to granulomatous disease
  • Interstitial lung disease due to metabolic disease
  • Interstitial lung disease due to systemic disease
  • Interstitial lung disease of childhood
  • Interstitial lung disease with systemic vasculitis
  • Interstitial pneumonia
  • Vasculitis due to systemic disease

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disease, diseased
      • lung
        • interstitial
          • of childhood, specified NEC

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR RSP016
Other specified and unspecified lower respiratory disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Desquamative Interstitial Pneumonia|DIP|RBILD|Respiratory Bronchiolitis Interstitial Lung Disease

    a rare idiopathic interstitial pneumonia characterized by accumulation of macrophages in alveolar spaces and interstitial inflammation. it usually occurs in smokers. some patients develop progressive interstitial lung fibrosis.

  • Interstitial Lung Disease

    a category of lung diseases characterized by varying degrees of inflammation and fibrosis of the interstitial lung tissue. causes include occupational lung exposures and drugs. in a minority of cases there is no clear cause and such cases are termed idiopathic interstitial pneumonia.

  • Pulmonary Surfactant Metabolism Dysfunction-3|Interstitial Lung Disease Due To ABCA3 Deficiency|SMDP3|Surfactant Apoprotein ABCA3 Deficiency|Surfactant Metabolism Dysfunction-3|Surfactant Protein ABCA3 Deficiency|Surfactant Protein ABCA3 Deficiency

    an autosomal recessive condition caused by mutation(s) in the abca3 gene, encoding atp-binding cassette sub-family a member 3. it is characterized by severe respiratory insufficiency or failure in neonates or infants.

Patient EducationClinical

Interstitial Lung Diseases

Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. The inflammation and scarring make it hard to get enough oxygen. The scarring is called pulmonary fibrosis.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert J84.848 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
516.69 Oth intrst lung dis chld
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About J84.848Overview

Is J84.848 (Other interstitial lung diseases of childhood) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other interstitial lung diseases of childhood on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does J84.848 group to?

When other interstitial lung diseases of childhood is the principal diagnosis on an inpatient stay, it groups to MS-DRG 196, 197, 198, with relative weights from 0.7162 to 1.8872 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of J84.848?

Under the General Equivalence Mappings, other interstitial lung diseases of childhood converts to ICD-9-CM 516.69 (oth intrst lung dis chld). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.