2026 ICD-10-CM Diagnosis Code I67.858Other hereditary cerebrovascular disease

ICD-10-CM Codes›I00–I99›I60-I69›I67

ICD-10-CM I67.858
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

I67.858 is a billable ICD-10-CM diagnosis code for other hereditary cerebrovascular disease. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as fibrosis, neurodegeneration, cerebral angiomatosis syndrome. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other and ill-defined cerebrovascular disease.

Code Identity

ICD-10-CM Code
I67.858
Billable Status
Yes — Valid for Submission
Code Describes
Other hereditary cerebrovascular disease
Short Description
Other hereditary cerebrovascular disease
Same as the full description in the CMS dataset.
Parent Code
I67.85
Hereditary cerebrovascular diseases

Code Classification

ChapterI00–I99Diseases of the circulatory system
SectionI60-I69Cerebrovascular diseases
CategoryI67Other cerebrovascular diseases
This CodeI67.858Other hereditary cerebrovascular disease

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Fibrosis, neurodegeneration, cerebral angiomatosis syndrome
  • HTRA1-related autosomal dominant cerebral small vessel disease
  • PF-ILD-progressive fibrosing interstitial lung disease
  • Small vessel cerebrovascular disease

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disease, diseased
      • cerebrovascular
        • hereditary NEC

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR CIR024
Other and ill-defined cerebrovascular disease
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Brain Diseases

Your brain is the control center of your body. It controls your thoughts, memory, speech, and movement. It regulates the function of many organs. It's part of your nervous system, which also includes your spinal cord and peripheral nerves. The nervous system sends signals between your brain and the rest of the body.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement I67.858 replaces the following previously assigned code(s):

  • I67.89 - Other cerebrovascular disease
FY 2019AddedAdded to the ICD-10-CM code setEffective October 1, 2018.
FY 2020–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About I67.858Overview

Is I67.858 (Hereditary cerebrovascular diseases) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other hereditary cerebrovascular disease on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.