Other cerebrovascular diseases (I67)
The ICD-10 code section I67 covers "Other cerebrovascular diseases," including various uncommon or complex conditions affecting brain blood vessels beyond typical strokes. These codes help specify diagnoses like cerebral artery dissections, nonruptured aneurysms, and rare vascular syndromes.
Specifically, I67.0 identifies nonruptured dissections of cerebral arteries, known also as dissecting aneurysms of various brain arteries. I67.1 denotes nonruptured cerebral aneurysms, including conditions like intracranial aneurysm and Berry aneurysm. I67.2 involves cerebral atherosclerosis, a cause of chronic brain blood flow problems. Other codes address progressive white-matter disease (I67.3), hypertensive encephalopathy (I67.4), and Moyamoya disease (I67.5), a rare stenosis of the carotid arteries. Venous thromboses are coded under I67.6, while cerebral arteritis falls under I67.7. Additional codes cover acute and chronic cerebral ischemia, reversible vasoconstriction syndromes, hereditary cerebrovascular disorders, and radiation-induced brain necrosis. This section uniquely helps medical coders precisely classify and document these less common cerebrovascular conditions in medical records and billing.
Diseases of the circulatory system (I00–I99)
Cerebrovascular diseases (I60-I69)
I67 Other cerebrovascular diseases
- I67.0 Dissection of cerebral arteries, nonruptured
- I67.1 Cerebral aneurysm, nonruptured
- I67.2 Cerebral atherosclerosis
- I67.3 Progressive vascular leukoencephalopathy
- I67.4 Hypertensive encephalopathy
- I67.5 Moyamoya disease
- I67.6 Nonpyogenic thrombosis of intracranial venous system
- I67.7 Cerebral arteritis, not elsewhere classified
I67.8 Other specified cerebrovascular diseases
- I67.81 Acute cerebrovascular insufficiency
- I67.82 Cerebral ischemia
- I67.83 Posterior reversible encephalopathy syndrome
I67.84 Cerebral vasospasm and vasoconstriction
- I67.841 Reversible cerebrovascular vasoconstriction syndrome
- I67.848 Other cerebrovascular vasospasm and vasoconstriction
I67.85 Hereditary cerebrovascular diseases
- I67.850 Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy
- I67.858 Other hereditary cerebrovascular disease
- I67.89 Other cerebrovascular disease
- I67.9 Cerebrovascular disease, unspecified
Other cerebrovascular diseases (I67)
Instructional Notations
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- Occlusion and stenosis of cerebral artery causing cerebral infarction I63.3 I63.5
- Occlusion and stenosis of precerebral artery causing cerebral infarction I63.2
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
- sequelae of the listed conditions I69.8
Clinical Terms
The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.
Giant Cell Arteritis
A systemic autoimmune disorder that typically affects medium and large ARTERIES, usually leading to occlusive granulomatous vasculitis with transmural infiltrate containing multinucleated GIANT CELLS. The TEMPORAL ARTERY is commonly involved. This disorder appears primarily in people over the age of 50. Symptoms include FEVER; FATIGUE; HEADACHE; visual impairment; pain in the jaw and tongue; and aggravation of pain by cold temperatures. (From Adams et al., Principles of Neurology, 6th ed)
Hypertensive Encephalopathy
Brain dysfunction or damage resulting from sustained MALIGNANT HYPERTENSION. When BLOOD PRESSURE exceeds the limits of cerebral autoregulation, cerebral blood flow is impaired (BRAIN ISCHEMIA). Clinical manifestations include HEADACHE; NAUSEA; VOMITING; SEIZURES; altered mental status (in some cases progressing to COMA); PAPILLEDEMA; and RETINAL HEMORRHAGE.
Intracranial Aneurysm
Abnormal outpouching in the wall of intracranial blood vessels. Most common are the saccular (berry) aneurysms located at branch points in CIRCLE OF WILLIS at the base of the brain. Vessel rupture results in SUBARACHNOID HEMORRHAGE or INTRACRANIAL HEMORRHAGES. Giant aneurysms (>2.5 cm in diameter) may compress adjacent structures, including the OCULOMOTOR NERVE. (From Adams et al., Principles of Neurology, 6th ed, p841)
Moyamoya Disease
A noninflammatory, progressive occlusion of the intracranial CAROTID ARTERIES and the formation of netlike collateral arteries arising from the CIRCLE OF WILLIS. Cerebral angiogram shows the puff-of-smoke (moyamoya) collaterals at the base of the brain. It is characterized by endothelial HYPERPLASIA and FIBROSIS with thickening of arterial walls. This disease primarily affects children but can also occur in adults.
