2026 ICD-10-CM Diagnosis Code H35.53Other dystrophies primarily involving the sensory retina

ICD-10-CM Codes›H00–H59›H30-H36›H35

ICD-10-CM H35.53
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

H35.53 is a billable ICD-10-CM diagnosis code for other dystrophies primarily involving the sensory retina. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 124 through 125. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Retinal and vitreous conditions.

Code Identity

ICD-10-CM Code
H35.53
Billable Status
Yes — Valid for Submission
Code Describes
Other dystrophies primarily involving the sensory retina
Short Description
Other dystrophies primarily involving the sensory retina
Same as the full description in the CMS dataset.
Parent Code
H35.5
Hereditary retinal dystrophy

Code Classification

ChapterH00–H59Diseases of the eye and adnexa
SectionH30-H36Disorders of choroid and retina
CategoryH35Other retinal disorders
This CodeH35.53Other dystrophies primarily involving the sensory retina

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Bilateral degeneration of macula
  • Bilateral fundus flavimaculatus of eyes
  • Cone dystrophy
  • Fundus flavimaculatus
  • Fundus flavimaculatus of left eye
  • Fundus flavimaculatus of right eye
  • Hereditary retinal dystrophy primarily involving sensory retina
  • Hyaline retinal dystrophy
  • Progressive cone dystrophy
  • Progressive rod dystrophy
  • Retinitis pigmentosa-deafness syndrome
  • Retinitis pigmentosa-deafness-ataxia syndrome
  • Rod dystrophy
  • Sensory retinal dystrophy
  • Sorsby pseudoinflammatory fundus dystrophy
  • Usher syndrome type 1
  • Usher syndrome type 1F
  • Usher syndrome type 2

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Stargardt's disease

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Dystrophy, dystrophia
      • retinal (hereditary)
        • involving
          • sensory area

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR EYE005
Retinal and vitreous conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Cone Dystrophy

    a general term which describes a group of rare eye disorders that affect the cone cells of the retina. cone dystrophy can cause a variety of symptoms including decreased visual clarity or acuity when looking straight ahead (central vision), a reduced ability to see colors, and an increased sensitivity to light (photophobia).

  • Usher Syndrome Type 1

    a syndrome characterized by congenital, bilateral, severe sensorineural hearing loss, abnormalities in the vestibular system, and adolescent-onset retinitis pigmentosa.

  • Usher Syndrome Type 2

    a syndrome characterized by congenital, bilateral sensorineural hearing loss that is mild to moderate in the low frequencies and severe to profound in the higher frequencies, no abnormalities in the vestibular system, and retinitis pigmentosa.

  • Usher Syndrome Type 2C|USH2C

    an autosomal recessive sub-type of usher syndrome caused by homozygous or compound heterozygous mutation(s) in the adgrv1 gene, encoding adhesion g protein-coupled receptor v1. it may also result from biallelic digenic mutation(s) in adgrv1 and pdzd7, which encodes pdz domain-containing protein 7.

Patient EducationClinical

Retinal Disorders

The retina is a layer of tissue in the back of your eye that senses light and sends images to your brain. In the center of this nerve tissue is the macula. It provides the sharp, central vision needed for reading, driving and seeing fine detail.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert H35.53 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
362.75 Sensory retina dystrophy
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About H35.53Overview

Is H35.53 (Hereditary retinal dystrophy) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other dystrophies primarily involving the sensory retina on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does H35.53 group to?

When other dystrophies primarily involving the sensory retina is the principal diagnosis on an inpatient stay, it groups to MS-DRG 124, 125, with relative weights from 0.7678 to 1.3231 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of H35.53?

Under the General Equivalence Mappings, other dystrophies primarily involving the sensory retina converts to ICD-9-CM 362.75 (sensory retina dystrophy). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.