ICD-10-CM Code H35.54

Dystrophies primarily involving the retinal pigment epithelium

Version 2021 Billable Code

Valid for Submission

H35.54 is a billable code used to specify a medical diagnosis of dystrophies primarily involving the retinal pigment epithelium. The code is valid for the fiscal year 2021 for the submission of HIPAA-covered transactions. The ICD-10-CM code H35.54 might also be used to specify conditions or terms like adult vitelliform macular dystrophy, amelogenesis imperfecta co-occurrent with cone rod dystrophy, best vitelliform macular dystrophy, biallelic rpe65 mutation associated retinal dystrophy, fundus pulverulentus, hereditary retinal dystrophy primarily involving retinal pigment epithelium, etc

ICD-10:H35.54
Short Description:Dystrophies primarily w the retinal pigment epithelium
Long Description:Dystrophies primarily involving the retinal pigment epithelium

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code H35.54:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Vitelliform retinal dystrophy

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code H35.54 are found in the index:


Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Adult vitelliform macular dystrophy
  • Amelogenesis imperfecta co-occurrent with cone rod dystrophy
  • Best vitelliform macular dystrophy
  • Biallelic RPE65 mutation associated retinal dystrophy
  • Fundus pulverulentus
  • Hereditary retinal dystrophy primarily involving retinal pigment epithelium
  • Multifocal pattern dystrophy of retinal pigment epithelium simulating fundus flavimaculatus
  • Progressive cone-rod dystrophy
  • Progressive cone-rod dystrophy
  • Reticular dystrophy of retinal pigment epithelium
  • Retinal pigment epithelial dystrophy
  • Spondylometaphyseal dysplasia with cone-rod dystrophy syndrome
  • Vitelliform dystrophy

Diagnostic Related Groups

The ICD-10 code H35.54 is grouped in the following groups for version MS-DRG V38.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2020 through 09/30/2021.

  • 124 - OTHER DISORDERS OF THE EYE WITH MCC
  • 125 - OTHER DISORDERS OF THE EYE WITHOUT MCC

Convert H35.54 to ICD-9

  • 362.76 - Vitelliform dystrophy

Code Classification

  • Diseases of the eye and adnexa (H00–H59)
    • Disorders of choroid and retina (H30-H36)
      • Other retinal disorders (H35)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021

Information for Patients


Retinal Disorders

The retina is a layer of tissue in the back of your eye that senses light and sends images to your brain. In the center of this nerve tissue is the macula. It provides the sharp, central vision needed for reading, driving and seeing fine detail.

Retinal disorders affect this vital tissue. They can affect your vision, and some can be serious enough to cause blindness. Examples are

  • Macular degeneration - a disease that destroys your sharp, central vision
  • Diabetic eye disease
  • Retinal detachment - a medical emergency, when the retina is pulled away from the back of the eye
  • Retinoblastoma - cancer of the retina. It is most common in young children.
  • Macular pucker - scar tissue on the macula
  • Macular hole - a small break in the macula that usually happens to people over 60
  • Floaters - cobwebs or specks in your field of vision

NIH: National Eye Institute

  • Amaurosis fugax (Medical Encyclopedia)
  • Central serous choroidopathy (Medical Encyclopedia)
  • Electroretinography (Medical Encyclopedia)
  • Fluorescein angiography (Medical Encyclopedia)
  • High blood pressure and eye disease (Medical Encyclopedia)
  • Home vision tests (Medical Encyclopedia)
  • Intravitreal injection (Medical Encyclopedia)
  • Retinal artery occlusion (Medical Encyclopedia)
  • Retinal vein occlusion (Medical Encyclopedia)

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