ICD-10 Diagnosis Code H35.50

Unspecified hereditary retinal dystrophy

Diagnosis Code H35.50

ICD-10: H35.50
Short Description: Unspecified hereditary retinal dystrophy
Long Description: Unspecified hereditary retinal dystrophy
This is the 2019 version of the ICD-10-CM diagnosis code H35.50

Valid for Submission
The code H35.50 is valid for submission for HIPAA-covered transactions.

Code Classification
  • Diseases of the eye and adnexa (H00–H59)
    • Disorders of choroid and retina (H30-H36)
      • Other retinal disorders (H35)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code H35.50 is grouped in the following Diagnostic Related Group(s) (MS-DRG V35.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.
  • 362.70 - Hered retin dystrphy NOS

  • Aland Islands eye disease
  • Autosomal dominant late-onset retinal degeneration
  • Autosomal recessive bestrophinopathy
  • Benign concentric annular macular dystrophy
  • Bothnia retinal dystrophy
  • Central obesity
  • Cerebral calcification
  • Cleft lip retinopathy syndrome
  • Cone dystrophy
  • Cone dystrophy with supernormal rod response
  • Congenital cerebellar hypoplasia co-occurrent with tapetoretinal degeneration
  • Congenital hypoplasia of penis
  • Congenital hypotrichia
  • Ectodermal dysplasia with ectrodactyly and macular dystrophy syndrome
  • Encephalopathy, intracerebral calcification, retinal degeneration syndrome
  • Familial diabetes insipidus
  • Familial pseudoinflammatory macular degeneration
  • Hereditary retinal dystrophies in lipidoses
  • Hereditary retinal dystrophy
  • Hypotrichosis with juvenile macular degeneration syndrome
  • Leber's amaurosis
  • Leber's amaurosis
  • MORM syndrome
  • Nanophthalmia
  • North Carolina macular dystrophy
  • Oligocone trichromacy
  • Optic atrophy associated with retinal dystrophy
  • Retinal degeneration, nanophthalmos, glaucoma syndrome
  • Retinal dystrophy
  • Retinal dystrophy in cerebroretinal lipidosis
  • Retinitis punctata albescens
  • Retinohepatoendocrinologic syndrome
  • Rod dystrophy
  • Severe early childhood onset retinal dystrophy
  • Spastic tetraparesis
  • Stargardt's disease
  • Tetraparesis
  • X-linked intellectual disability, limb spasticity, retinal dystrophy, diabetes insipidus syndrome

Information for Patients

Retinal Disorders

The retina is a layer of tissue in the back of your eye that senses light and sends images to your brain. In the center of this nerve tissue is the macula. It provides the sharp, central vision needed for reading, driving and seeing fine detail.

Retinal disorders affect this vital tissue. They can affect your vision, and some can be serious enough to cause blindness. Examples are

  • Macular degeneration - a disease that destroys your sharp, central vision
  • Diabetic eye disease
  • Retinal detachment - a medical emergency, when the retina is pulled away from the back of the eye
  • Retinoblastoma - cancer of the retina. It is most common in young children.
  • Macular pucker - scar tissue on the macula
  • Macular hole - a small break in the macula that usually happens to people over 60
  • Floaters - cobwebs or specks in your field of vision

NIH: National Eye Institute

  • Amaurosis fugax (Medical Encyclopedia)
  • Central serous choroidopathy (Medical Encyclopedia)
  • Electroretinography (Medical Encyclopedia)
  • Fluorescein angiography (Medical Encyclopedia)
  • High blood pressure and eye disease (Medical Encyclopedia)
  • Home vision tests (Medical Encyclopedia)
  • Intravitreal injection (Medical Encyclopedia)
  • Retinal artery occlusion (Medical Encyclopedia)
  • Retinal vein occlusion (Medical Encyclopedia)

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