ICD-10-CM Code H35.52

Pigmentary retinal dystrophy

Version 2020 Billable Code

Valid for Submission

H35.52 is a billable code used to specify a medical diagnosis of pigmentary retinal dystrophy. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code H35.52 might also be used to specify conditions or terms like atrophic macular change, autosomal dominant retinitis pigmentosa, autosomal dominant retinitis pigmentosa, autosomal recessive leukoencephalopathy, ischemic stroke, retinitis pigmentosa syndrome, autosomal recessive posterior column ataxia and retinitis pigmentosa, autosomal recessive retinitis pigmentosa, etc

Short Description:Pigmentary retinal dystrophy
Long Description:Pigmentary retinal dystrophy

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code H35.52:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Albipunctate retinal dystrophy
  • Retinitis pigmentosa
  • Tapetoretinal dystrophy

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code H35.52 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Atrophic macular change
  • Autosomal dominant retinitis pigmentosa
  • Autosomal dominant retinitis pigmentosa
  • Autosomal recessive leukoencephalopathy, ischemic stroke, retinitis pigmentosa syndrome
  • Autosomal recessive posterior column ataxia and retinitis pigmentosa
  • Autosomal recessive retinitis pigmentosa
  • Butterfly-shaped pigmentary macular dystrophy
  • Cholestasis
  • Cholestasis with pigmentary retinopathy and cleft palate syndrome
  • Drusen of optic disc
  • Early onset cerebellar ataxia with retinitis pigmentosa and optic atrophy
  • Hereditary motor and sensory neuropathy with retinitis pigmentosa
  • Hypogonadotropic hypogonadism retinitis pigmentosa syndrome
  • Immotile cilia syndrome
  • Macular pigment deposit
  • Microphthalmia, retinitis pigmentosa, foveoschisis, optic disc drusen syndrome
  • Muscular atrophy, ataxia, retinitis pigmentosa, and diabetes mellitus
  • Neurogenic muscle weakness, ataxia and retinitis pigmentosa
  • Oculotrichodysplasia
  • Osteochondrodysplatic nanism, deafness, retinitis pigmentosa syndrome
  • Pattern dystrophy of macula
  • Polyneuropathy, hearing loss, ataxia, retinitis pigmentosa, cataract syndrome
  • Primary ciliary dyskinesia and retinitis pigmentosa syndrome
  • Retinal pigment deposits
  • Retinal pigment epithelial dystrophy
  • Retinitis pigmentosa
  • Retinitis pigmentosa of bilateral eyes
  • Retinitis pigmentosa of left eye
  • Retinitis pigmentosa of right eye
  • Retinitis pigmentosa, intellectual disability, deafness, hypogenitalism syndrome
  • RHYNS syndrome
  • Saldino-Mainzer dysplasia
  • Spastic tetraplegia
  • Spastic tetraplegia, retinitis pigmentosa, intellectual disability syndrome
  • Tapetoretinal dystrophy
  • Uncombable hair, retinal pigmentary dystrophy, dental anomaly and brachydactyly syndrome
  • X-linked retinitis pigmentosa
  • X-linked retinitis pigmentosa heterozygote

Diagnostic Related Groups

The ICD-10 code H35.52 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.


Convert H35.52 to ICD-9

  • 362.74 - Pigment retina dystrophy

Code Classification

  • Diseases of the eye and adnexa (H00–H59)
    • Disorders of choroid and retina (H30-H36)
      • Other retinal disorders (H35)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Retinal Disorders

The retina is a layer of tissue in the back of your eye that senses light and sends images to your brain. In the center of this nerve tissue is the macula. It provides the sharp, central vision needed for reading, driving and seeing fine detail.

Retinal disorders affect this vital tissue. They can affect your vision, and some can be serious enough to cause blindness. Examples are

  • Macular degeneration - a disease that destroys your sharp, central vision
  • Diabetic eye disease
  • Retinal detachment - a medical emergency, when the retina is pulled away from the back of the eye
  • Retinoblastoma - cancer of the retina. It is most common in young children.
  • Macular pucker - scar tissue on the macula
  • Macular hole - a small break in the macula that usually happens to people over 60
  • Floaters - cobwebs or specks in your field of vision

NIH: National Eye Institute

[Learn More]

Cone-rod dystrophy Cone-rod dystrophy is a group of related eye disorders that causes vision loss, which becomes more severe over time. These disorders affect the retina, which is the layer of light-sensitive tissue at the back of the eye. In people with cone-rod dystrophy, vision loss occurs as the light-sensing cells of the retina gradually deteriorate.The first signs and symptoms of cone-rod dystrophy, which often occur in childhood, are usually decreased sharpness of vision (visual acuity) and increased sensitivity to light (photophobia). These features are typically followed by impaired color vision (dyschromatopsia), blind spots (scotomas) in the center of the visual field, and partial side (peripheral) vision loss. Over time, affected individuals develop night blindness and a worsening of their peripheral vision, which can limit independent mobility. Decreasing visual acuity makes reading increasingly difficult and most affected individuals are legally blind by mid-adulthood. As the condition progresses, individuals may develop involuntary eye movements (nystagmus).There are more than 30 types of cone-rod dystrophy, which are distinguished by their genetic cause and their pattern of inheritance: autosomal recessive, autosomal dominant, and X-linked. Additionally, cone-rod dystrophy can occur alone without any other signs and symptoms or it can occur as part of a syndrome that affects multiple parts of the body.
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Fundus albipunctatus Fundus albipunctatus is an eye disorder characterized by an impaired ability to see in low light (night blindness) and the presence of whitish-yellow flecks in the retina, which is the specialized light-sensitive tissue in the inner lining of the back of the eye (the fundus). The flecks are detected during an eye examination.Individuals with fundus albipunctatus experience night blindness from an early age. In particular, they have delayed dark adaptation, which means they have trouble adapting from bright light to dark conditions, such as when driving into a dark tunnel on a sunny day. It often takes hours for adaptation to occur. Their vision in bright light is usually normal.The flecks are especially abundant near the outer edge (the periphery) of the retina. Their density varies among affected individuals; some people have numerous flecks that overlap, while others have fewer. For unknown reasons, the flecks get smaller or fade with age in some affected individuals, although night vision does not improve.While fundus albipunctatus typically does not worsen (progress) over time, some individuals with the condition develop other eye conditions, such as breakdown of the central region of the retina known as the macula (macular dystrophy) with loss of specialized light receptor cells called cones, which can affect vision in bright light.
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Retinitis pigmentosa Retinitis pigmentosa is a group of related eye disorders that cause progressive vision loss. These disorders affect the retina, which is the layer of light-sensitive tissue at the back of the eye. In people with retinitis pigmentosa, vision loss occurs as the light-sensing cells of the retina gradually deteriorate.The first sign of retinitis pigmentosa is usually a loss of night vision, which becomes apparent in childhood. Problems with night vision can make it difficult to navigate in low light. Later, the disease causes blind spots to develop in the side (peripheral) vision. Over time, these blind spots merge to produce tunnel vision. The disease progresses over years or decades to affect central vision, which is needed for detailed tasks such as reading, driving, and recognizing faces. In adulthood, many people with retinitis pigmentosa become legally blind.The signs and symptoms of retinitis pigmentosa are most often limited to vision loss. When the disorder occurs by itself, it is described as nonsyndromic. Researchers have identified several major types of nonsyndromic retinitis pigmentosa, which are usually distinguished by their pattern of inheritance: autosomal dominant, autosomal recessive, or X-linked.Less commonly, retinitis pigmentosa occurs as part of syndromes that affect other organs and tissues in the body. These forms of the disease are described as syndromic. The most common form of syndromic retinitis pigmentosa is Usher syndrome, which is characterized by the combination of vision loss and hearing loss beginning early in life. Retinitis pigmentosa is also a feature of several other genetic syndromes, including Bardet-Biedl syndrome; Refsum disease; and neuropathy, ataxia, and retinitis pigmentosa (NARP).
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