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  2. ICD-10-CM Codes List
  3. H00–H59
  4. H30-H36
  5. Other retinal disorders (H35)

Other retinal disorders (H35)

The ICD-10 code range H35 covers a comprehensive group of diagnoses for other retinal disorders, including background retinopathy, hypertensive and exudative retinopathies, prematurity-related retinal diseases, retinal dystrophies, macular degeneration, retinal hemorrhage, and various degenerative conditions. These codes are essential for specifying retinal diseases distinct from diabetic retinopathy, allowing precise clinical documentation and billing.

This section includes codes like H35.0 for background retinopathy and vascular changes, H35.03 for hypertensive retinopathy, and H35.3 for degeneration of the macula, with subdivisions accounting for each eye or bilateral involvement. For example, the code H35.00 encompasses various forms of background retinopathy caused by drugs such as hydroxychloroquine or trifluoperazine, while H35.319 addresses nonexudative age-related macular degeneration across different stages. Retinopathy of prematurity (ROP) is covered under H35.1 with detailed staging, aiding clear diagnosis of this common condition in premature infants. The section also includes rare hereditary dystrophies (H35.5), retinal hemorrhages (H35.6), and other specific disorders such as central serous chorioretinopathy (H35.71). Using these codes helps to accurately document retinal conditions which may manifest with symptoms such as vision loss, vascular abnormalities, or retinal degeneration, and supports healthcare providers in tracking treatment progress and complications.

  • Diseases of the eye and adnexa (H00–H59)

    • Disorders of choroid and retina (H30-H36)

        • Other retinal disorders (H35)

        • H35 Other retinal disorders
        • H35.0 Background retinopathy and retinal vascular changes
        • H35.00 Unspecified background retinopathy
        • H35.01 Changes in retinal vascular appearance
        • H35.011 Changes in retinal vascular appearance, right eye
        • H35.012 Changes in retinal vascular appearance, left eye
        • H35.013 Changes in retinal vascular appearance, bilateral
        • H35.019 Changes in retinal vascular appearance, unspecified eye
        • H35.02 Exudative retinopathy
        • H35.021 Exudative retinopathy, right eye
        • H35.022 Exudative retinopathy, left eye
        • H35.023 Exudative retinopathy, bilateral
        • H35.029 Exudative retinopathy, unspecified eye
        • H35.03 Hypertensive retinopathy
        • H35.031 Hypertensive retinopathy, right eye
        • H35.032 Hypertensive retinopathy, left eye
        • H35.033 Hypertensive retinopathy, bilateral
        • H35.039 Hypertensive retinopathy, unspecified eye
        • H35.04 Retinal micro-aneurysms, unspecified
        • H35.041 Retinal micro-aneurysms, unspecified, right eye
        • H35.042 Retinal micro-aneurysms, unspecified, left eye
        • H35.043 Retinal micro-aneurysms, unspecified, bilateral
        • H35.049 Retinal micro-aneurysms, unspecified, unspecified eye
        • H35.05 Retinal neovascularization, unspecified
        • H35.051 Retinal neovascularization, unspecified, right eye
        • H35.052 Retinal neovascularization, unspecified, left eye
        • H35.053 Retinal neovascularization, unspecified, bilateral
        • H35.059 Retinal neovascularization, unspecified, unspecified eye
        • H35.06 Retinal vasculitis
        • H35.061 Retinal vasculitis, right eye
        • H35.062 Retinal vasculitis, left eye
        • H35.063 Retinal vasculitis, bilateral
        • H35.069 Retinal vasculitis, unspecified eye
        • H35.07 Retinal telangiectasis
        • H35.071 Retinal telangiectasis, right eye
        • H35.072 Retinal telangiectasis, left eye
        • H35.073 Retinal telangiectasis, bilateral
        • H35.079 Retinal telangiectasis, unspecified eye
        • H35.09 Other intraretinal microvascular abnormalities
        • H35.1 Retinopathy of prematurity
        • H35.10 Retinopathy of prematurity, unspecified
        • H35.101 Retinopathy of prematurity, unspecified, right eye
        • H35.102 Retinopathy of prematurity, unspecified, left eye
        • H35.103 Retinopathy of prematurity, unspecified, bilateral
        • H35.109 Retinopathy of prematurity, unspecified, unspecified eye
        • H35.11 Retinopathy of prematurity, stage 0
        • H35.111 Retinopathy of prematurity, stage 0, right eye
        • H35.112 Retinopathy of prematurity, stage 0, left eye
        • H35.113 Retinopathy of prematurity, stage 0, bilateral
        • H35.119 Retinopathy of prematurity, stage 0, unspecified eye
        • H35.12 Retinopathy of prematurity, stage 1
        • H35.121 Retinopathy of prematurity, stage 1, right eye
        • H35.122 Retinopathy of prematurity, stage 1, left eye
        • H35.123 Retinopathy of prematurity, stage 1, bilateral
        • H35.129 Retinopathy of prematurity, stage 1, unspecified eye
        • H35.13 Retinopathy of prematurity, stage 2
        • H35.131 Retinopathy of prematurity, stage 2, right eye
        • H35.132 Retinopathy of prematurity, stage 2, left eye
        • H35.133 Retinopathy of prematurity, stage 2, bilateral
        • H35.139 Retinopathy of prematurity, stage 2, unspecified eye
        • H35.14 Retinopathy of prematurity, stage 3
        • H35.141 Retinopathy of prematurity, stage 3, right eye
        • H35.142 Retinopathy of prematurity, stage 3, left eye
        • H35.143 Retinopathy of prematurity, stage 3, bilateral
        • H35.149 Retinopathy of prematurity, stage 3, unspecified eye
        • H35.15 Retinopathy of prematurity, stage 4
        • H35.151 Retinopathy of prematurity, stage 4, right eye
        • H35.152 Retinopathy of prematurity, stage 4, left eye
        • H35.153 Retinopathy of prematurity, stage 4, bilateral
        • H35.159 Retinopathy of prematurity, stage 4, unspecified eye
        • H35.16 Retinopathy of prematurity, stage 5
        • H35.161 Retinopathy of prematurity, stage 5, right eye
        • H35.162 Retinopathy of prematurity, stage 5, left eye
        • H35.163 Retinopathy of prematurity, stage 5, bilateral
        • H35.169 Retinopathy of prematurity, stage 5, unspecified eye
        • H35.17 Retrolental fibroplasia
        • H35.171 Retrolental fibroplasia, right eye
        • H35.172 Retrolental fibroplasia, left eye
        • H35.173 Retrolental fibroplasia, bilateral
        • H35.179 Retrolental fibroplasia, unspecified eye
        • H35.2 Other non-diabetic proliferative retinopathy
        • H35.20 Other non-diabetic proliferative retinopathy, unspecified eye
        • H35.21 Other non-diabetic proliferative retinopathy, right eye
        • H35.22 Other non-diabetic proliferative retinopathy, left eye
        • H35.23 Other non-diabetic proliferative retinopathy, bilateral
        • H35.3 Degeneration of macula and posterior pole
        • H35.30 Unspecified macular degeneration
        • H35.31 Nonexudative age-related macular degeneration
        • H35.311 Nonexudative age-related macular degeneration, right eye
        • H35.3110 Nonexudative age-related macular degeneration, right eye, stage unspecified
        • H35.3111 Nonexudative age-related macular degeneration, right eye, early dry stage
        • H35.3112 Nonexudative age-related macular degeneration, right eye, intermediate dry stage
        • H35.3113 Nonexudative age-related macular degeneration, right eye, advanced atrophic without subfoveal involvement
        • H35.3114 Nonexudative age-related macular degeneration, right eye, advanced atrophic with subfoveal involvement
        • H35.312 Nonexudative age-related macular degeneration, left eye
        • H35.3120 Nonexudative age-related macular degeneration, left eye, stage unspecified
        • H35.3121 Nonexudative age-related macular degeneration, left eye, early dry stage
        • H35.3122 Nonexudative age-related macular degeneration, left eye, intermediate dry stage
        • H35.3123 Nonexudative age-related macular degeneration, left eye, advanced atrophic without subfoveal involvement
        • H35.3124 Nonexudative age-related macular degeneration, left eye, advanced atrophic with subfoveal involvement
        • H35.313 Nonexudative age-related macular degeneration, bilateral
        • H35.3130 Nonexudative age-related macular degeneration, bilateral, stage unspecified
        • H35.3131 Nonexudative age-related macular degeneration, bilateral, early dry stage
        • H35.3132 Nonexudative age-related macular degeneration, bilateral, intermediate dry stage
        • H35.3133 Nonexudative age-related macular degeneration, bilateral, advanced atrophic without subfoveal involvement
        • H35.3134 Nonexudative age-related macular degeneration, bilateral, advanced atrophic with subfoveal involvement
        • H35.319 Nonexudative age-related macular degeneration, unspecified eye
        • H35.3190 Nonexudative age-related macular degeneration, unspecified eye, stage unspecified
        • H35.3191 Nonexudative age-related macular degeneration, unspecified eye, early dry stage
        • H35.3192 Nonexudative age-related macular degeneration, unspecified eye, intermediate dry stage
        • H35.3193 Nonexudative age-related macular degeneration, unspecified eye, advanced atrophic without subfoveal involvement
        • H35.3194 Nonexudative age-related macular degeneration, unspecified eye, advanced atrophic with subfoveal involvement
        • H35.32 Exudative age-related macular degeneration
        • H35.321 Exudative age-related macular degeneration, right eye
        • H35.3210 Exudative age-related macular degeneration, right eye, stage unspecified
        • H35.3211 Exudative age-related macular degeneration, right eye, with active choroidal neovascularization
        • H35.3212 Exudative age-related macular degeneration, right eye, with inactive choroidal neovascularization
        • H35.3213 Exudative age-related macular degeneration, right eye, with inactive scar
        • H35.322 Exudative age-related macular degeneration, left eye
        • H35.3220 Exudative age-related macular degeneration, left eye, stage unspecified
        • H35.3221 Exudative age-related macular degeneration, left eye, with active choroidal neovascularization
        • H35.3222 Exudative age-related macular degeneration, left eye, with inactive choroidal neovascularization
        • H35.3223 Exudative age-related macular degeneration, left eye, with inactive scar
        • H35.323 Exudative age-related macular degeneration, bilateral
        • H35.3230 Exudative age-related macular degeneration, bilateral, stage unspecified
        • H35.3231 Exudative age-related macular degeneration, bilateral, with active choroidal neovascularization
        • H35.3232 Exudative age-related macular degeneration, bilateral, with inactive choroidal neovascularization
        • H35.3233 Exudative age-related macular degeneration, bilateral, with inactive scar
        • H35.329 Exudative age-related macular degeneration, unspecified eye
        • H35.3290 Exudative age-related macular degeneration, unspecified eye, stage unspecified
        • H35.3291 Exudative age-related macular degeneration, unspecified eye, with active choroidal neovascularization
        • H35.3292 Exudative age-related macular degeneration, unspecified eye, with inactive choroidal neovascularization
        • H35.3293 Exudative age-related macular degeneration, unspecified eye, with inactive scar
        • H35.33 Angioid streaks of macula
        • H35.34 Macular cyst, hole, or pseudohole
        • H35.341 Macular cyst, hole, or pseudohole, right eye
        • H35.342 Macular cyst, hole, or pseudohole, left eye
        • H35.343 Macular cyst, hole, or pseudohole, bilateral
        • H35.349 Macular cyst, hole, or pseudohole, unspecified eye
        • H35.35 Cystoid macular degeneration
        • H35.351 Cystoid macular degeneration, right eye
        • H35.352 Cystoid macular degeneration, left eye
        • H35.353 Cystoid macular degeneration, bilateral
        • H35.359 Cystoid macular degeneration, unspecified eye
        • H35.36 Drusen (degenerative) of macula
        • H35.361 Drusen (degenerative) of macula, right eye
        • H35.362 Drusen (degenerative) of macula, left eye
        • H35.363 Drusen (degenerative) of macula, bilateral
        • H35.369 Drusen (degenerative) of macula, unspecified eye
        • H35.37 Puckering of macula
        • H35.371 Puckering of macula, right eye
        • H35.372 Puckering of macula, left eye
        • H35.373 Puckering of macula, bilateral
        • H35.379 Puckering of macula, unspecified eye
        • H35.38 Toxic maculopathy
        • H35.381 Toxic maculopathy, right eye
        • H35.382 Toxic maculopathy, left eye
        • H35.383 Toxic maculopathy, bilateral
        • H35.389 Toxic maculopathy, unspecified eye
        • H35.4 Peripheral retinal degeneration
        • H35.40 Unspecified peripheral retinal degeneration
        • H35.41 Lattice degeneration of retina
        • H35.411 Lattice degeneration of retina, right eye
        • H35.412 Lattice degeneration of retina, left eye
        • H35.413 Lattice degeneration of retina, bilateral
        • H35.419 Lattice degeneration of retina, unspecified eye
        • H35.42 Microcystoid degeneration of retina
        • H35.421 Microcystoid degeneration of retina, right eye
        • H35.422 Microcystoid degeneration of retina, left eye
        • H35.423 Microcystoid degeneration of retina, bilateral
        • H35.429 Microcystoid degeneration of retina, unspecified eye
        • H35.43 Paving stone degeneration of retina
        • H35.431 Paving stone degeneration of retina, right eye
        • H35.432 Paving stone degeneration of retina, left eye
        • H35.433 Paving stone degeneration of retina, bilateral
        • H35.439 Paving stone degeneration of retina, unspecified eye
        • H35.44 Age-related reticular degeneration of retina
        • H35.441 Age-related reticular degeneration of retina, right eye
        • H35.442 Age-related reticular degeneration of retina, left eye
        • H35.443 Age-related reticular degeneration of retina, bilateral
        • H35.449 Age-related reticular degeneration of retina, unspecified eye
        • H35.45 Secondary pigmentary degeneration
        • H35.451 Secondary pigmentary degeneration, right eye
        • H35.452 Secondary pigmentary degeneration, left eye
        • H35.453 Secondary pigmentary degeneration, bilateral
        • H35.459 Secondary pigmentary degeneration, unspecified eye
        • H35.46 Secondary vitreoretinal degeneration
        • H35.461 Secondary vitreoretinal degeneration, right eye
        • H35.462 Secondary vitreoretinal degeneration, left eye
        • H35.463 Secondary vitreoretinal degeneration, bilateral
        • H35.469 Secondary vitreoretinal degeneration, unspecified eye
        • H35.5 Hereditary retinal dystrophy
        • H35.50 Unspecified hereditary retinal dystrophy
        • H35.51 Vitreoretinal dystrophy
        • H35.52 Pigmentary retinal dystrophy
        • H35.53 Other dystrophies primarily involving the sensory retina
        • H35.54 Dystrophies primarily involving the retinal pigment epithelium
        • H35.6 Retinal hemorrhage
        • H35.60 Retinal hemorrhage, unspecified eye
        • H35.61 Retinal hemorrhage, right eye
        • H35.62 Retinal hemorrhage, left eye
        • H35.63 Retinal hemorrhage, bilateral
        • H35.7 Separation of retinal layers
        • H35.70 Unspecified separation of retinal layers
        • H35.71 Central serous chorioretinopathy
        • H35.711 Central serous chorioretinopathy, right eye
        • H35.712 Central serous chorioretinopathy, left eye
        • H35.713 Central serous chorioretinopathy, bilateral
        • H35.719 Central serous chorioretinopathy, unspecified eye
        • H35.72 Serous detachment of retinal pigment epithelium
        • H35.721 Serous detachment of retinal pigment epithelium, right eye
        • H35.722 Serous detachment of retinal pigment epithelium, left eye
        • H35.723 Serous detachment of retinal pigment epithelium, bilateral
        • H35.729 Serous detachment of retinal pigment epithelium, unspecified eye
        • H35.73 Hemorrhagic detachment of retinal pigment epithelium
        • H35.731 Hemorrhagic detachment of retinal pigment epithelium, right eye
        • H35.732 Hemorrhagic detachment of retinal pigment epithelium, left eye
        • H35.733 Hemorrhagic detachment of retinal pigment epithelium, bilateral
        • H35.739 Hemorrhagic detachment of retinal pigment epithelium, unspecified eye
        • H35.8 Other specified retinal disorders
        • H35.81 Retinal edema
        • H35.82 Retinal ischemia
        • H35.89 Other specified retinal disorders
        • H35.9 Unspecified retinal disorder

Instructional Notations

Type 2 Excludes

A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Central Serous Chorioretinopathy

A visual impairment characterized by the accumulation of fluid under the retina through a defect in the retinal pigment epithelium.

Choroid

The thin, highly vascular membrane covering most of the posterior of the eye between the RETINA and SCLERA.

Cone Dystrophy

A general term which describes a group of rare eye disorders that affect the cone cells of the RETINA. Cone dystrophy can cause a variety of symptoms including decreased visual clarity or acuity when looking straight ahead (central vision), a reduced ability to see colors, and an increased sensitivity to light (PHOTOPHOBIA).

Endarteritis

Inflammation of the inner endothelial lining (TUNICA INTIMA) of an artery.

Epiretinal Membrane

A membrane on the vitreal surface of the retina resulting from the proliferation of one or more of three retinal elements: (1) fibrous astrocytes; (2) fibrocytes; and (3) RETINAL PIGMENT EPITHELIUM. Localized epiretinal membranes may occur at the posterior pole of the eye without clinical signs or may cause marked loss of vision as a result of covering, distorting, or detaching the FOVEA CENTRALIS. Epiretinal membranes may cause vascular leakage and secondary retinal edema. In younger individuals some membranes appear to be developmental in origin and occur in otherwise normal eyes. The majority occur in association with RETINAL HOLES, ocular concussions, retinal inflammation, or after ocular surgery. (Newell, Ophthalmology: Principles and Concepts, 7th ed, p291)

Geographic Atrophy

A form of MACULAR DEGENERATION also known as dry macular degeneration marked by occurrence of a well-defined progressive lesion or atrophy in the central part of the RETINA called the MACULA LUTEA. It is distinguishable from WET MACULAR DEGENERATION in that the latter involves neovascular exudates.

Hypertensive Retinopathy

Degenerative changes to the RETINA due to HYPERTENSION.

Macular Degeneration

Degenerative changes in the RETINA usually of older adults which results in a loss of vision in the center of the visual field (the MACULA LUTEA) because of damage to the retina. It occurs in dry and wet forms.

Polypoidal Choroidal Vasculopathy

A CHOROID neovascularization characterized by serosanguineous retinal pigment epithelial detachment and leakage of serous exudate sometimes associated with aneurysmal polypoidal lesions.

Retinal Drusen

Colloid or hyaline bodies lying beneath the retinal pigment epithelium. They may occur either secondary to changes in the choroid that affect the pigment epithelium or as an autosomal dominant disorder of the retinal pigment epithelium.

Retinal Hemorrhage

Bleeding from the vessels of the retina.

Retinal Neovascularization

Formation of new blood vessels originating from the retinal veins and extending along the inner (vitreal) surface of the retina.

Retinal Telangiectasis

A group of rare, idiopathic, congenital retinal vascular anomalies affecting the retinal capillaries. It is characterized by dilation and tortuosity of retinal vessels and formation of multiple aneurysms, with different degrees of leakage and exudates emanating from the blood vessels.

Retinal Vasculitis

Inflammation of the retinal vasculature with various causes including infectious disease; LUPUS ERYTHEMATOSUS, SYSTEMIC; MULTIPLE SCLEROSIS; BEHCET SYNDROME; and CHORIORETINITIS.

Retinitis Pigmentosa

Hereditary, progressive degeneration of the retina due to death of ROD PHOTORECEPTORS initially and subsequent death of CONE PHOTORECEPTORS. It is characterized by deposition of pigment in the retina.

Retinopathy of Prematurity

A bilateral retinopathy occurring in premature infants treated with excessively high concentrations of oxygen, characterized by vascular dilatation, proliferation, and tortuosity, edema, and retinal detachment, with ultimate conversion of the retina into a fibrous mass that can be seen as a dense retrolental membrane. Usually growth of the eye is arrested and may result in microophthalmia, and blindness may occur. (Dorland, 27th ed)

Stargardt Disease

A juvenile-onset macular dystrophy characterized by progressive loss of VISUAL ACUITY with normal acuity in peripheral VISUAL FIELDS. Other associated clinical features may include LIPOFUSCIN fundus autofluorescence, atrophy of the RETINAL PIGMENT EPITHELIUM, loss of color vision, PHOTOPHOBIA and PARACENTRAL SCOTOMA. Germline mutations in the ABCA4 gene have been identified in recessive and dominant diseases.

Subretinal Fluid

An exudate between the RETINA and CHOROID from various sources including the vitreous cavity, SUBARACHNOID SPACE, or abnormal vessels.

Tunica Intima

The innermost layer of an artery or vein, made up of one layer of endothelial cells and supported by an internal elastic lamina.

Usher Syndromes

Autosomal recessive hereditary disorders characterized by congenital SENSORINEURAL HEARING LOSS and RETINITIS PIGMENTOSA. Genetically and symptomatically heterogeneous, clinical classes include type I, type II, and type III. Their severity, age of onset of retinitis pigmentosa and the degree of vestibular dysfunction are variable.

Vitelliform Macular Dystrophy

Autosomal dominant hereditary maculopathy with childhood-onset accumulation of LIPOFUSION in RETINAL PIGMENT EPITHELIUM. Affected individuals develop progressive central acuity loss, and distorted vision (METAMORPHOPSIA). It is associated with mutations in bestrophin, a chloride channel.

Wet Macular Degeneration

A form of RETINAL DEGENERATION in which abnormal CHOROIDAL NEOVASCULARIZATION occurs under the RETINA and MACULA LUTEA, causing bleeding and leaking of fluid. This leads to bulging and or lifting of the macula and the distortion or destruction of central vision.