2027 ICD-10-CM Diagnosis Code H35.52Pigmentary retinal dystrophy
ICD-10-CM Codes›H00–H59›H30-H36›H35
- Billable — Valid for Submission
- Chronic Condition
H35.52 is a billable ICD-10-CM diagnosis code for pigmentary retinal dystrophy. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 124 through 125. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Retinal and vitreous conditions.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Autosomal dominant retinitis pigmentosa
- Autosomal recessive leukoencephalopathy, ischemic stroke, retinitis pigmentosa syndrome
- Autosomal recessive posterior column ataxia and retinitis pigmentosa
- Autosomal recessive retinitis pigmentosa
- Brachydactyly, short stature, retinitis pigmentosa syndrome
- Butterfly-shaped pigmentary macular dystrophy
- Cholestasis with pigmentary retinopathy and cleft palate syndrome
- Drusen of optic disc
- Early onset cerebellar ataxia with retinitis pigmentosa and optic atrophy
- Hereditary motor and sensory neuropathy with retinitis pigmentosa
- Hereditary retinal dystrophy primarily involving retinal pigment epithelium
- Hypogonadotropic hypogonadism retinitis pigmentosa syndrome
- Infantile and/or juvenile cataract
- Juvenile cataract
- Macular pigment deposit
- Microphthalmia, retinitis pigmentosa, foveoschisis, optic disc drusen syndrome
- Mitochondrial myopathy, cerebellar ataxia, pigmentary retinopathy syndrome
- Mitochondrially encoded ATP synthase membrane subunit 6-related mitochondrial disease
- Muscular atrophy, ataxia, retinitis pigmentosa, and diabetes mellitus
- NARP syndrome
- Neurological muscle weakness
- Oculotrichodysplasia
- Pattern dystrophy of macula
- Polyneuropathy, hearing loss, ataxia, retinitis pigmentosa, cataract syndrome
- Primary ciliary dyskinesia and retinitis pigmentosa syndrome
- Progressive weakness of muscle
- Pseudoxanthoma elasticum-like skin manifestations with retinitis pigmentosa
- Retinal dystrophy due to systemic disorder
- Retinal pigment deposits
- Retinal pigment epithelial dystrophy
- Retinitis pigmentosa
- Retinitis pigmentosa due to systemic disease
- Retinitis pigmentosa of bilateral eyes
- Retinitis pigmentosa of left eye
- Retinitis pigmentosa of right eye
- Retinitis pigmentosa, hearing loss, premature aging, short stature, facial dysmorphism syndrome
- Retinitis pigmentosa, intellectual disability, deafness, hypogenitalism syndrome
- Retinitis pigmentosa, juvenile cataract, short stature, intellectual disability syndrome
- Retinitis pigmentosa-deafness syndrome
- Retinitis pigmentosa-deafness syndrome type 3
- RHYNS syndrome
- Saldino-Mainzer dysplasia
- Spastic tetraplegia
- Spastic tetraplegia, retinitis pigmentosa, intellectual disability syndrome
- Structural abnormality of fovea centralis
- Uncombable hair, retinal pigmentary dystrophy, dental anomaly and brachydactyly syndrome
- X-linked retinitis pigmentosa
- X-linked retinitis pigmentosa heterozygote
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to H35.52: its own notes plus those printed at H35.5, H35, and Chapter 7. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Albipunctate retinal dystrophy
- Retinitis pigmentosa
- Tapetoretinal dystrophy
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- diabetes mellitus related eye conditions (E09.3-, E10.3-, E11.3-, E13.3-)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury (trauma) of eye and orbit (S05.-)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
- syphilis related eye disorders (A50.01, A50.3-, A51.43, A52.71)
Notes
General instructions on how these codes are used.
- Use an external cause code following the code for the eye condition, if applicable, to identify the cause of the eye condition
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name H35.52, its category, or a range that includes it.
Excludes1 2
These codes carry an Excludes1 note naming H35.52: they are not reported together with it, unless the two conditions are unrelated.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Retinitis See Also: Inflammation, chorioretinal;
pigmentosa H35.52
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Hereditary Retinal Dystrophy
an inherited form of retinal dystrophy.
Patient EducationClinical
Retinal Disorders
Retinal disorders are conditions that affect the retina, the thin light-sensitive tissue at the back of your eye. The retina senses light and sends signals to your brain so you can see.
The full article covers:
- What are retinal disorders?
- What causes retinal disorders?
- What are common retinal disorders?
- What are the symptoms of retinal disorders?
- How are retinal disorders diagnosed?
- How are retinal disorders treated?
- Can retinal disorders be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert H35.52 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About H35.52Overview
What is the ICD-10 code for pigmentary retinal dystrophy?
The ICD-10-CM code for pigmentary retinal dystrophy is H35.52 (sometimes written as H3552). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is H35.52 (Hereditary retinal dystrophy) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report pigmentary retinal dystrophy on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does H35.52 group to?
When pigmentary retinal dystrophy is the principal diagnosis on an inpatient stay, it groups to MS-DRG 125, 124, with relative weights from 0.7699 to 1.2470 depending on complications. Higher weights mean higher Medicare reimbursement.
Can H35.52 be reported with a code from H31.1?
Not as a rule. The Excludes1 note at H35.5, which applies to H35.52, lists "dystrophies primarily involving Bruch's membrane (H31.1-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
What is the ICD-9 equivalent of H35.52?
Under the General Equivalence Mappings, pigmentary retinal dystrophy converts to ICD-9-CM 362.74 (pigment retina dystrophy). The mapping is a direct match.
