2026 ICD-10-CM Diagnosis Code D47.Z2Castleman disease

ICD-10-CM Codes›C00–D49›D37-D48›D47

ICD-10-CM D47.Z2
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

D47.Z2 is a billable ICD-10-CM diagnosis code for castleman disease. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 820 through 825, 840 through 842. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neoplasms of unspecified nature or uncertain behavior.

Code Identity

ICD-10-CM Code
D47.Z2
Billable Status
Yes — Valid for Submission
Code Describes
Castleman disease
Short Description
Castleman disease
Same as the full description in the CMS dataset.
Parent Code
D47.Z
Other specified neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue

Code Classification

ChapterC00–D49Neoplasms
SectionD37-D48Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes
CategoryD47Other neoplasms of uncertain behavior of lymphoid, hematopoietic and related tissue
This CodeD47.Z2Castleman disease

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Castleman disease
  • Castleman disease co-occurrent with infection caused by Human herpesvirus 8
  • Castleman disease with immunoglobulin M monoclonal gammopathy of uncertain significance
  • Disease caused by Human herpesvirus 8
  • Hyperplastic lymph node
  • IgM monoclonal gammopathy of uncertain significance
  • Large B-cell lymphoma arising in HHV8-associated multicentric Castleman disease
  • Localized Castleman disease
  • Monoclonal gammopathy of uncertain significance
  • Multicentric Castleman disease

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Code Also

  • , if applicable, human herpesvirus 8 infection B10.89

Type 2 Excludes

  • Kaposi's sarcoma C46

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disease, diseased
      • Castleman (unicentric) (multicentric)
    • Disease, diseased
      • Castleman (unicentric) (multicentric)
        • HHV-8-associated

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO072
Neoplasms of unspecified nature or uncertain behavior
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Castleman Disease

    large benign, hyperplastic lymph nodes. the more common hyaline vascular subtype is characterized by small hyaline vascular follicles and interfollicular capillary proliferations. plasma cells are often present and represent another subtype with the plasma cells containing igm and immunoglobulin a.

Patient EducationClinical

Lymphatic Diseases

The lymphatic system is a network of tissues and organs. It is made up of:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert D47.Z2 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
238.79 Lymph/hematpoitc tis NEC
Approximate The match is approximate rather than exact.

Code History & ChangesHistory

Replacement D47.Z2 replaces the following previously assigned code(s):

  • D47.9 - Neoplm of uncrt behav of lymphoid,hematpoetc & rel tiss,unsp
FY 2018AddedAdded to the ICD-10-CM code setEffective October 1, 2017.
FY 2019–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About D47.Z2Overview

Is D47.Z2 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report castleman disease on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does D47.Z2 group to?

When castleman disease is the principal diagnosis on an inpatient stay, it groups to MS-DRG 820, 821, 822, 823, 824, 825, 840, 841, 842, with relative weights from 1.0104 to 5.8648 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of D47.Z2?

Under the General Equivalence Mappings, castleman disease converts to ICD-9-CM 238.79 (lymph/hematpoitc tis NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.