2027 ICD-10-CM Diagnosis Code D35.6Benign neoplasm of aortic body and other paraganglia

ICD-10-CM Codes›C00–D49›D10-D36›D35

ICD-10-CM D35.6
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

D35.6 is a billable ICD-10-CM diagnosis code for benign neoplasm of aortic body and other paraganglia. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 54 through 55. Coders also document this condition as benign neoplasm of aortic body. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Benign neoplasms.

Code Identity

ICD-10-CM Code
D35.6
Billable Status
Yes — Valid for Submission
Code Describes
Benign neoplasm of aortic body and other paraganglia
Short Description
Benign neoplasm of aortic body and other paraganglia
Same as the full description in the CMS dataset.
Parent Code
Benign neoplasm of other and unspecified endocrine glands

Code Classification

ChapterC00–D49Neoplasms
SectionD10-D36Benign neoplasms, except benign neuroendocrine tumors
CategoryD35Benign neoplasm of other and unspecified endocrine glands
This CodeD35.6Benign neoplasm of aortic body and other paraganglia

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Benign neoplasm of aortic body
  • Benign neoplasm of glomus jugulare
  • Benign neoplasm of para-aortic body
  • Benign neoplasm of paraganglion
  • Neoplasm of aortic body
  • Neoplasm of glomus jugulare
  • Neoplasm of para-aortic body

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to D35.6: its own notes plus those printed at D35 and Chapter 2. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Benign tumor of glomus jugulare

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From D35 Benign neoplasm of other and unspecified endocrine glands applies to 11 codes
  • benign neoplasm of endocrine pancreas (D13.7)
  • benign neoplasm of ovary (D27.-)
  • benign neoplasm of testis (D29.2.-)
  • benign neoplasm of thymus (D15.0)

Use Additional Code

Add a second code, after this one, to fully describe the condition.

From D35 Benign neoplasm of other and unspecified endocrine glands applies to 11 codes
  • code to identify any functional activity

Notes

General instructions on how these codes are used.

From Chapter 2 (C00-D49) Neoplasms applies to 1,730 codes
  • Functional activity
  • All neoplasms are classified in this chapter, whether they are functionally active or not. An additional code from Chapter 4 may be used, to identify functional activity associated with any neoplasm.
  • Morphology [Histology]
  • Chapter 2 classifies neoplasms primarily by site (topography), with broad groupings for behavior, malignant, in situ, benign, etc. The Table of Neoplasms should be used to identify the correct topography code. In a few cases, such as for malignant melanoma and certain neuroendocrine tumors, the morphology (histologic type) is included in the category and codes.
  • Primary malignant neoplasms overlapping site boundaries
  • A primary malignant neoplasm that overlaps two or more contiguous (next to each other) sites should be classified to the subcategory/code .8 ('overlapping lesion'), unless the combination is specifically indexed elsewhere. For multiple neoplasms of the same site that are not contiguous, such as tumors in different quadrants of the same breast, codes for each site should be assigned.
  • Malignant neoplasm of ectopic tissue
  • Malignant neoplasms of ectopic tissue are to be coded to the site mentioned, e.g., ectopic pancreatic malignant neoplasms are coded to pancreas, unspecified (C25.9).

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name D35.6, its category, or a range that includes it.

Excludes2 1

These codes carry an Excludes2 note naming D35.6: its condition is not part of those codes, and both may be reported when the patient has both.

  • D18 Hemangioma and lymphangioma, any site
    benign neoplasm of glomus jugulare (D35.6)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO073
Benign neoplasms
Default principal diagnosis: inpatient Yes · outpatient Yes

Table of NeoplasmsClinical

Anatomical sites in the Table of Neoplasms that reference this code family.

SiteMalig.
Primary
Malig.
Secondary
Ca
in situ
BenignUncertainUnspec.
aortic bodyC75.5C79.89–D35.6D44.7D49.7
glomus › jugularisC75.5C79.89–D35.6D44.7D49.7
organ of ZuckerkandlC75.5C79.89–D35.6D44.7D49.7
para-aortic bodyC75.5C79.89–D35.6D44.7D49.7
paraganglion NECC75.5C79.89–D35.6D44.7D49.7
Zuckerkandl organC75.5C79.89–D35.6D44.7D49.7

Patient EducationClinical

Benign Tumors

Tumors are abnormal growths in your body. They can be either benign or malignant. Benign tumors aren't cancer. Malignant ones are. Benign tumors grow only in one place. They cannot spread or invade other parts of your body. Even so, they can be dangerous if they press on vital organs, such as your brain.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert D35.6 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
227.6 Ben neo paraganglia NEC
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About D35.6Overview

What is the ICD-10 code for benign neoplasm of aortic body and other paraganglia?

The ICD-10-CM code for benign neoplasm of aortic body and other paraganglia is D35.6 (sometimes written as D356). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is D35.6 (Benign neoplasm of other and unspecified endocrine glands) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report benign neoplasm of aortic body and other paraganglia on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does D35.6 group to?

When benign neoplasm of aortic body and other paraganglia is the principal diagnosis on an inpatient stay, it groups to MS-DRG 55, 54, with relative weights from 1.0291 to 1.5197 depending on complications. Higher weights mean higher Medicare reimbursement.

Can D35.6 be reported with D13.7?

Not as a rule. The Excludes1 note at D35, which applies to D35.6, lists "benign neoplasm of endocrine pancreas (D13.7)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).

Does D35.6 need an additional code?

When the condition applies, yes. The Use Additional Code note at D35, which applies to D35.6, reads: code to identify any functional activity. The additional code is reported after D35.6.