2026 ICD-10-CM Diagnosis Code C47.9Malignant neoplasm of peripheral nerves and autonomic nervous system, unspecified

ICD-10-CM Codes›C00–D49›C45-C49›C47

ICD-10-CM C47.9
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

C47.9 is a billable ICD-10-CM diagnosis code for malignant neoplasm of peripheral nerves and autonomic nervous system, unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 542 through 544. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Nervous system cancers - all other types.

Code Identity

ICD-10-CM Code
C47.9
Billable Status
Yes — Valid for Submission
Code Describes
Malignant neoplasm of peripheral nerves and autonomic nervous system, unspecified
Short Description
Malig neoplasm of prph nerves and autonm nervous sys, unsp
Parent Code
C47
Malignant neoplasm of peripheral nerves and autonomic nervous system

Code Classification

ChapterC00–D49Neoplasms
SectionC45-C49Malignant neoplasms of mesothelial and soft tissue
CategoryC47Malignant neoplasm of peripheral nerves and autonomic nervous system
This CodeC47.9Malignant neoplasm of peripheral nerves and autonomic nervous system, unspecified

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Epithelioid malignant nerve sheath tumor
  • Ganglioneuroblastoma
  • Glandular malignant peripheral nerve sheath tumor
  • Hirschsprung disease, ganglioneuroblastoma syndrome
  • Malignant infiltration of peripheral nerve plexus
  • Malignant neoplasm of nerve sheath origin
  • Malignant neoplasm of peripheral nerve
  • Malignant neoplasm of peripheral nerves and autonomic nervous system
  • Malignant neoplasm of spinal nerve and sheath
  • Malignant peripheral nerve sheath neoplasm of peripheral nerve of lumbar spine
  • Malignant peripheral nerve sheath tumor
  • Malignant peripheral nerve sheath tumor with perineurial differentiation
  • Malignant Triton tumor
  • Medulloepithelioma
  • Melanotic malignant nerve sheath tumor
  • Metastatic ganglioneuroblastoma
  • Neoplasm of autonomic nerve
  • Neoplasm of spinal nerve and sheath
  • Primary epithelioid malignant nerve sheath tumor
  • Primary ganglioneuroblastoma
  • Primary glandular malignant peripheral nerve sheath tumor
  • Primary malignant neoplasm of peripheral nerve
  • Primary malignant neoplasm of peripheral nerves and peripheral autonomic nervous system
  • Primary malignant nerve sheath neoplasm of autonomic nerve
  • Primary malignant nerve sheath neoplasm of peripheral nervous system structure
  • Primary malignant neuroepitheliomatous neoplasm of autonomic nervous system
  • Primary malignant neuroepitheliomatous neoplasm of peripheral nerve
  • Primary malignant peripheral nerve sheath tumor
  • Primary malignant peripheral nerve sheath tumor with perineurial differentiation
  • Primary malignant Triton tumor
  • Primary medulloepithelioma
  • Primary melanotic malignant nerve sheath tumor
  • Primary primitive neuroectodermal tumor

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Malignant neoplasm of unspecified site of peripheral nerves and autonomic nervous system

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO049
Nervous system cancers - all other types
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Ganglioneuroblastoma

    a moderately malignant neoplasm composed of primitive neuroectodermal cells dispersed in myxomatous or fibrous stroma intermixed with mature ganglion cells. it may undergo transformation into a neuroblastoma. it arises from the sympathetic trunk or less frequently from the adrenal medulla, cerebral cortex, and other locations. cervical ganglioneuroblastomas may be associated with horner syndrome and the tumor may occasionally secrete vasoactive intestinal peptide, resulting in chronic diarrhea.

  • Horner Syndrome

    a syndrome associated with defective sympathetic innervation to one side of the face, including the eye. clinical features include miosis; mild blepharoptosis; and hemifacial anhidrosis (decreased sweating)(see hypohidrosis). lesions of the brain stem; cervical spinal cord; first thoracic nerve root; apex of the lung; carotid artery; cavernous sinus; and apex of the orbit may cause this condition. (from miller et al., clinical neuro-ophthalmology, 4th ed, pp500-11)

Table of NeoplasmsClinical

Anatomical sites in the Table of Neoplasms that reference this code family.

SiteMalig.
Primary		Malig.
Secondary		Ca
in situ		BenignUncertainUnspec.
ganglia [See Also: Neoplasm, nerve, peripheral]C47.9C79.89–D36.10D48.2D49.2
nerve (ganglion)C47.9C79.89–D36.10D48.2D49.2
nerve (ganglion) › autonomic NEC [See Also: Neoplasm, nerve, peripheral]C47.9C79.89–D36.10D48.2D49.2
nerve (ganglion) › ganglion NEC [See Also: Neoplasm, nerve, peripheral]C47.9C79.89–D36.10D48.2D49.2
nerve (ganglion) › parasympathetic NECC47.9C79.89–D36.10D48.2D49.2
nerve (ganglion) › peripheral NECC47.9C79.89–D36.10D48.2D49.2
nerve (ganglion) › peripheral NEC › extremityC47.9C79.89–D36.10D48.2D49.2
nerve (ganglion) › peripheral NEC › limb NECC47.9C79.89–D36.10D48.2D49.2
nerve (ganglion) › spinal NECC47.9C79.89–D36.10D48.2D49.2
nerve (ganglion) › sympathetic NEC [See Also: Neoplasm, nerve, peripheral]C47.9C79.89–D36.10D48.2D49.2
peripheral nerve NECC47.9C79.89–D36.10D48.2D49.2
spine, spinal (column) › nerve (root)C47.9C79.89–D36.10D48.2D49.2
spine, spinal (column) › rootC47.9C79.89–D36.10D48.2D49.2
sympathetic nerve or nervous system NECC47.9C79.89–D36.10D48.2D49.2

Patient EducationClinical

Autonomic Nervous System Disorders

Your autonomic nervous system is the part of your nervous system that controls involuntary actions, such as the beating of your heart and the widening or narrowing of your blood vessels. When something goes wrong in this system, it can cause serious problems, including:

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert C47.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
171.9 Mal neo soft tissue NOS
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About C47.9Overview

Is C47.9 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report malignant neoplasm of peripheral nerves and autonomic nervous system, unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does C47.9 group to?

When malignant neoplasm of peripheral nerves and autonomic nervous system, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 542, 543, 544, with relative weights from 0.7546 to 1.7665 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of C47.9?

Under the General Equivalence Mappings, malignant neoplasm of peripheral nerves and autonomic nervous system, unspecified converts to ICD-9-CM 171.9 (mal neo soft tissue NOS). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.