Kaposi's sarcoma (C46) ICD-10-CM
The C46 code range covers kaposi's sarcoma with 12 ICD-10-CM diagnosis codes. 10 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Code First
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
- any human immunodeficiency virus [HIV] disease B20
Codes in the C46 Range 12 codes · 10 billable
- C46 Kaposi's sarcomaNon-billable
- C46.0 Kaposi's sarcoma of skin
- C46.1 Kaposi's sarcoma of soft tissue
- C46.2 Kaposi's sarcoma of palate
- C46.3 Kaposi's sarcoma of lymph nodes
- C46.4 Kaposi's sarcoma of gastrointestinal sites
- C46.5 Kaposi's sarcoma of lungNon-billable
- C46.50 Kaposi's sarcoma of unspecified lung
- C46.51 Kaposi's sarcoma of right lung
- C46.52 Kaposi's sarcoma of left lung
- C46.7 Kaposi's sarcoma of other sites
- C46.9 Kaposi's sarcoma, unspecified
About the C46 Code Range
Kaposi's sarcoma ICD-10 codes (C46 series) are specifically used to classify and document various forms of Kaposi's sarcoma, a cancer that affects blood vessel cells and commonly appears in the skin, lymph nodes, and internal organs.
These codes cover distinct locations of Kaposi's sarcoma, such as C46.0 for skin (also known as primary Kaposi sarcoma of skin or soft tissue), C46.1 for soft tissue, and C46.2 for palate. The classification extends to internal sites like C46.3 for lymph nodes, C46.4 for gastrointestinal sites (including stomach, colon, and rectum), and C46.5 and its subcodes for lung involvement. Additionally, C46.7 designates Kaposi's sarcoma at other less common sites such as the eyelid, conjunctiva, and oral cavity. The unspecified code C46.9 covers cases when the location is not documented or when multiple organs are involved, including various clinical forms like endemic or AIDS-related Kaposi’s sarcoma. Medical coders use these precise ICD-10 codes to document and differentiate Kaposi's sarcoma presentations, ensuring accurate diagnosis and treatment tracking.
Questions About This Page
How many billable codes are in the C46 range?
Of the 12 codes in this range, 10 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the C46 range classify?
The range classifies kaposi's sarcoma. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
