Kaposi's sarcoma (C46) ICD-10-CM
The C46 code range covers kaposi's sarcoma with 12 ICD-10-CM diagnosis codes. 10 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Code First
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
- any human immunodeficiency virus [HIV] disease B20
Codes in the C46 Range 12 codes · 10 billable
- C46 Kaposi's sarcomaNon-billable
- C46.0 Kaposi's sarcoma of skin
- C46.1 Kaposi's sarcoma of soft tissue
- C46.2 Kaposi's sarcoma of palate
- C46.3 Kaposi's sarcoma of lymph nodes
- C46.4 Kaposi's sarcoma of gastrointestinal sites
- C46.5 Kaposi's sarcoma of lungNon-billable
- C46.50 Kaposi's sarcoma of unspecified lung
- C46.51 Kaposi's sarcoma of right lung
- C46.52 Kaposi's sarcoma of left lung
- C46.7 Kaposi's sarcoma of other sites
- C46.9 Kaposi's sarcoma, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the C46 range.
Digestive System Kaposi Sarcoma
A Kaposi sarcoma arising from the digestive system.
Kaposi Sarcoma of the Lymph Nodes
A Kaposi sarcoma affecting the lymph nodes.
Lung Kaposi Sarcoma
A Kaposi sarcoma arising from the lung.
Palate Kaposi Sarcoma
Kaposi sarcoma arising from the palate.
Sarcoma, Kaposi
A multicentric, malignant neoplastic vascular proliferation characterized by the development of bluish-red cutaneous nodules, usually on the lower extremities, most often on the toes or feet, and slowly increasing in size and number and spreading to more proximal areas. The tumors have endothelium-lined channels and vascular spaces admixed with variably sized aggregates of spindle-shaped cells, and often remain confined to the skin and subcutaneous tissue, but widespread visceral involvement may occur. Kaposi's sarcoma occurs spontaneously in Jewish and Italian males in Europe and the United States. An aggressive variant in young children is endemic in some areas of Africa. A third form occurs in about 0.04% of kidney transplant patients. There is also a high incidence in AIDS patients. (From Dorland, 27th ed & Holland et al., Cancer Medicine, 3d ed, pp2105-7) HHV-8 is the suspected cause.
Skin Kaposi Sarcoma
A Kaposi sarcoma arising from the skin. It presents with patches, plaques, or nodules.
About the C46 Code Range
Kaposi's sarcoma is a malignant growth involving blood vessels. It often forms bluish-red skin nodules but can also involve internal organs.
Within C46, subdivisions distinguish skin, soft tissue, palate, lymph nodes, gastrointestinal sites, lung, other sites, and an unspecified site. The lung subdivision separates unspecified lung from right and left lung.
Questions About This Page
How many billable codes are in the C46 range?
Of the 12 codes in this range, 10 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the C46 range classify?
The range classifies kaposi's sarcoma. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
