2026 ICD-10-CM Diagnosis Code A50.49Other late congenital neurosyphilis

ICD-10-CM Codes›A00–B99›A50-A64›A50

ICD-10-CM A50.49
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

A50.49 is a billable ICD-10-CM diagnosis code for other late congenital neurosyphilis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as acquired syphilis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Perinatal infections and Sexually transmitted infections (excluding HIV and hepatitis).

Code Identity

ICD-10-CM Code
A50.49
Billable Status
Yes — Valid for Submission
Code Describes
Other late congenital neurosyphilis
Short Description
Other late congenital neurosyphilis
Same as the full description in the CMS dataset.
Parent Code
A50.4
Late congenital neurosyphilis [juvenile neurosyphilis]

Code Classification

ChapterA00–B99Certain infectious and parasitic diseases
SectionA50-A64Infections with a predominantly sexual mode of transmission
CategoryA50Congenital syphilis
This CodeA50.49Other late congenital neurosyphilis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acquired syphilis
  • Juvenile tabes dorsalis
  • Late quaternary neurosyphilis
  • Sensorineural deafness due to late congenital syphilis
  • Spastic spinal syphilitic paralysis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Juvenile tabes dorsalis

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
      • in (due to)
        • neurosyphilis
          • juvenile
    • Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
      • in (due to)
        • neurosyphilis
          • juvenile
            • with behavioral disturbance
    • Hydrocephalus(acquired) (external) (internal) (malignant) (recurrent)
      • syphilitic, congenital
    • Meningoencephalocele
      • syphilitic
        • congenital
    • Palsy
      • cerebral (congenital)
        • syphilitic
          • congenital
    • Tabes, tabetic
      • dorsalis
        • juvenile
    • Tabes, tabetic
      • juvenile

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR PNL009
Perinatal infections
Default principal diagnosis: inpatient Yes · outpatient Yes
CCSR INF010
Sexually transmitted infections (excluding HIV and hepatitis)
Default principal diagnosis: inpatient No · outpatient No

Patient EducationClinical

Syphilis

Syphilis is a sexually transmitted infection (STI) caused by bacteria. It infects the genital area, lips, mouth, or anus of both men and women. You usually get syphilis from sexual contact with someone who has it. It can also pass from mother to baby during pregnancy.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert A50.49 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
090.49 Juvenile neurosyph NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About A50.49Overview

Is A50.49 (Late congenital neurosyphilis [juvenile neurosyphilis]) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other late congenital neurosyphilis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of A50.49?

Under the General Equivalence Mappings, other late congenital neurosyphilis converts to ICD-9-CM 090.49 (juvenile neurosyph NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.