Viral and prion infections of the central nervous system (A80-A89)
ICD-10 codes A80-A89 cover viral and prion infections affecting the central nervous system (CNS), including poliomyelitis, rabies, various viral encephalitides, meningitis, and rare prion diseases. These codes are used to specify different types of CNS infections caused by viruses or prions, facilitating accurate diagnosis and proper medical record documentation.
This range includes acute and paralytic forms of poliomyelitis (codes A80.0-A80.9), helping differentiate vaccine-associated versus wild virus cases. The atypical virus infections subsection (A81) encompasses prion diseases such as Creutzfeldt-Jakob disease and Gerstmann-Straussler-Scheinker syndrome, alongside subacute sclerosing panencephalitis and progressive multifocal leukoencephalopathy. Rabies virus infections are detailed under A82, while mosquito-borne viral encephalitis such as Japanese and St. Louis encephalitis appear in A83. Tick-borne encephalitis viruses like Far Eastern and Central European types are found in A84. Other viral encephalitides, not elsewhere classified, fall under A85, with viral meningitis codes in A87. Lastly, A88 and A89 capture other specified or unspecified viral CNS infections, including rare presentations like enteroviral exanthematous fever and epidemic vertigo. The use of synonyms linked to each code aids coders in selecting the most precise diagnosis from terms like "infantile paralysis" for poliomyelitis or "variant Creutzfeldt-Jakob disease" for prion disorders, improving clinical clarity and billing accuracy.
- Acute poliomyelitis (A80)
- Atypical virus infections of central nervous system (A81)
- Rabies (A82)
- Mosquito-borne viral encephalitis (A83)
- Tick-borne viral encephalitis (A84)
- Other viral encephalitis, not elsewhere classified (A85)
- Unspecified viral encephalitis (A86)
- Viral meningitis (A87)
- Other viral infections of central nervous system, not elsewh
- Unspecified viral infection of central nervous system (A89)
Certain infectious and parasitic diseases (A00–B99)
Viral and prion infections of the central nervous system (A80-A89)
A80 Acute poliomyelitis
- A80.0 Acute paralytic poliomyelitis, vaccine-associated
- A80.1 Acute paralytic poliomyelitis, wild virus, imported
- A80.2 Acute paralytic poliomyelitis, wild virus, indigenous
A80.3 Acute paralytic poliomyelitis, other and unspecified
- A80.30 Acute paralytic poliomyelitis, unspecified
- A80.39 Other acute paralytic poliomyelitis
- A80.4 Acute nonparalytic poliomyelitis
- A80.9 Acute poliomyelitis, unspecified
Acute poliomyelitis (A80)
A81 Atypical virus infections of central nervous system
A81.0 Creutzfeldt-Jakob disease
- A81.00 Creutzfeldt-Jakob disease, unspecified
- A81.01 Variant Creutzfeldt-Jakob disease
- A81.09 Other Creutzfeldt-Jakob disease
- A81.1 Subacute sclerosing panencephalitis
- A81.2 Progressive multifocal leukoencephalopathy
A81.8 Other atypical virus infections of central nervous system
- A81.81 Kuru
- A81.82 Gerstmann-Straussler-Scheinker syndrome
- A81.83 Fatal familial insomnia
- A81.89 Other atypical virus infections of central nervous system
- A81.9 Atypical virus infection of central nervous system, unspecified
Atypical virus infections of central nervous system (A81)
A82 Rabies
- A82.0 Sylvatic rabies
- A82.1 Urban rabies
- A82.9 Rabies, unspecified
Rabies (A82)
A83 Mosquito-borne viral encephalitis
- A83.0 Japanese encephalitis
- A83.1 Western equine encephalitis
- A83.2 Eastern equine encephalitis
- A83.3 St Louis encephalitis
- A83.4 Australian encephalitis
- A83.5 California encephalitis
- A83.6 Rocio virus disease
- A83.8 Other mosquito-borne viral encephalitis
- A83.9 Mosquito-borne viral encephalitis, unspecified
Mosquito-borne viral encephalitis (A83)
A84 Tick-borne viral encephalitis
- A84.0 Far Eastern tick-borne encephalitis [Russian spring-summer encephalitis]
- A84.1 Central European tick-borne encephalitis
A84.8 Other tick-borne viral encephalitis
- A84.81 Powassan virus disease
- A84.89 Other tick-borne viral encephalitis
- A84.9 Tick-borne viral encephalitis, unspecified
Tick-borne viral encephalitis (A84)
- A86 Unspecified viral encephalitis
Unspecified viral encephalitis (A86)
A88 Other viral infections of central nervous system, not elsewhere classified
- A88.0 Enteroviral exanthematous fever [Boston exanthem]
- A88.1 Epidemic vertigo
- A88.8 Other specified viral infections of central nervous system
Other viral infections of central nervous system, not elsewhere classified (A88)
- A89 Unspecified viral infection of central nervous system
Unspecified viral infection of central nervous system (A89)
Instructional Notations
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
