Congenital syphilis (A50) ICD-10-CM
The A50 code range covers congenital syphilis with 38 ICD-10-CM diagnosis codes. 33 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Codes in the A50 Range 38 codes · 33 billable
- A50 Congenital syphilisNon-billable
- A50.0 Early congenital syphilis, symptomaticNon-billable
- A50.01 Early congenital syphilitic oculopathy
- A50.02 Early congenital syphilitic osteochondropathy
- A50.03 Early congenital syphilitic pharyngitis
- A50.04 Early congenital syphilitic pneumonia
- A50.05 Early congenital syphilitic rhinitis
- A50.06 Early cutaneous congenital syphilis
- A50.07 Early mucocutaneous congenital syphilis
- A50.08 Early visceral congenital syphilis
- A50.09 Other early congenital syphilis, symptomatic
- A50.1 Early congenital syphilis, latent
- A50.2 Early congenital syphilis, unspecified
- A50.3 Late congenital syphilitic oculopathyNon-billable
- A50.30 Late congenital syphilitic oculopathy, unspecified
- A50.31 Late congenital syphilitic interstitial keratitis
- A50.32 Late congenital syphilitic chorioretinitis
- A50.39 Other late congenital syphilitic oculopathy
- A50.4 Late congenital neurosyphilis [juvenile neurosyphilis]Non-billable
- A50.40 Late congenital neurosyphilis, unspecified
- A50.41 Late congenital syphilitic meningitis
- A50.42 Late congenital syphilitic encephalitis
- A50.43 Late congenital syphilitic polyneuropathy
- A50.44 Late congenital syphilitic optic nerve atrophy
- A50.45 Juvenile general paresis
- A50.49 Other late congenital neurosyphilis
- A50.5 Other late congenital syphilis, symptomaticNon-billable
- A50.51 Clutton's joints
- A50.52 Hutchinson's teeth
- A50.53 Hutchinson's triad
- A50.54 Late congenital cardiovascular syphilis
- A50.55 Late congenital syphilitic arthropathy
- A50.56 Late congenital syphilitic osteochondropathy
- A50.57 Syphilitic saddle nose
- A50.59 Other late congenital syphilis, symptomatic
- A50.6 Late congenital syphilis, latent
- A50.7 Late congenital syphilis, unspecified
- A50.9 Congenital syphilis, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the A50 range.
Syphilis, Congenital
Syphilis acquired in utero and manifested by any of several characteristic tooth (Hutchinson's teeth) or bone malformations and by active mucocutaneous syphilis at birth or shortly thereafter. Ocular and neurologic changes may also occur.
About the A50 Code Range
Congenital syphilis is syphilis acquired before birth. The codes separate early and late disease, then distinguish symptomatic, latent, and unspecified forms.
Early disease appears under symptomatic A50.0, latent A50.1, and unspecified A50.2. Symptomatic subdivisions identify affected eyes, bones, throat, lungs, nose, skin, or internal organs.
Late disease separates eye conditions under A50.3, nervous system conditions under A50.4, and other symptomatic conditions under A50.5. The remaining codes identify latent or unspecified late disease, or congenital syphilis with no early or late designation.
Questions About This Page
How many billable codes are in the A50 range?
Of the 38 codes in this range, 33 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the A50 range classify?
The range classifies congenital syphilis. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
