Congenital syphilis (A50) ICD-10-CM
The A50 code range covers congenital syphilis with 38 ICD-10-CM diagnosis codes. 33 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Codes in the A50 Range 38 codes · 33 billable
- A50 Congenital syphilisNon-billable
- A50.0 Early congenital syphilis, symptomaticNon-billable
- A50.01 Early congenital syphilitic oculopathy
- A50.02 Early congenital syphilitic osteochondropathy
- A50.03 Early congenital syphilitic pharyngitis
- A50.04 Early congenital syphilitic pneumonia
- A50.05 Early congenital syphilitic rhinitis
- A50.06 Early cutaneous congenital syphilis
- A50.07 Early mucocutaneous congenital syphilis
- A50.08 Early visceral congenital syphilis
- A50.09 Other early congenital syphilis, symptomatic
- A50.1 Early congenital syphilis, latent
- A50.2 Early congenital syphilis, unspecified
- A50.3 Late congenital syphilitic oculopathyNon-billable
- A50.30 Late congenital syphilitic oculopathy, unspecified
- A50.31 Late congenital syphilitic interstitial keratitis
- A50.32 Late congenital syphilitic chorioretinitis
- A50.39 Other late congenital syphilitic oculopathy
- A50.4 Late congenital neurosyphilis [juvenile neurosyphilis]Non-billable
- A50.40 Late congenital neurosyphilis, unspecified
- A50.41 Late congenital syphilitic meningitis
- A50.42 Late congenital syphilitic encephalitis
- A50.43 Late congenital syphilitic polyneuropathy
- A50.44 Late congenital syphilitic optic nerve atrophy
- A50.45 Juvenile general paresis
- A50.49 Other late congenital neurosyphilis
- A50.5 Other late congenital syphilis, symptomaticNon-billable
- A50.51 Clutton's joints
- A50.52 Hutchinson's teeth
- A50.53 Hutchinson's triad
- A50.54 Late congenital cardiovascular syphilis
- A50.55 Late congenital syphilitic arthropathy
- A50.56 Late congenital syphilitic osteochondropathy
- A50.57 Syphilitic saddle nose
- A50.59 Other late congenital syphilis, symptomatic
- A50.6 Late congenital syphilis, latent
- A50.7 Late congenital syphilis, unspecified
- A50.9 Congenital syphilis, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the A50 range.
Longitudinal Studies
Studies in which variables relating to an individual or group of individuals are assessed over a period of time.
Neurosyphilis
Infections of the central nervous system caused by TREPONEMA PALLIDUM which present with a variety of clinical syndromes. The initial phase of infection usually causes a mild or asymptomatic meningeal reaction. The meningovascular form may present acutely as BRAIN INFARCTION. The infection may also remain subclinical for several years. Late syndromes include general paresis; TABES DORSALIS; meningeal syphilis; syphilitic OPTIC ATROPHY; and spinal syphilis. General paresis is characterized by progressive DEMENTIA; DYSARTHRIA; TREMOR; MYOCLONUS; SEIZURES; and Argyll-Robertson pupils. (Adams et al., Principles of Neurology, 6th ed, pp722-8)
Syphilis
A contagious venereal disease caused by the spirochete TREPONEMA PALLIDUM.
Syphilis Serodiagnosis
Serologic tests for syphilis.
Syphilis, Cardiovascular
Cardiovascular manifestations of SYPHILIS, an infection of TREPONEMA PALLIDUM. In the late stage of syphilis, sometimes 20-30 years after the initial infection, damages are often seen in the blood vessels including the AORTA and the AORTIC VALVE. Clinical signs include syphilitic aortitis, aortic insufficiency, or aortic ANEURYSM.
Syphilis, Congenital
Syphilis acquired in utero and manifested by any of several characteristic tooth (Hutchinson's teeth) or bone malformations and by active mucocutaneous syphilis at birth or shortly thereafter. Ocular and neurologic changes may also occur.
Syphilis, Cutaneous
Cutaneous lesions arising from infection with Treponema pallidum. In the primary stage, 18-21 days following infection, one or more chancres appear. If untreated, the subsequent stages of the disease appear as syphilids. These eruptions are superficial, nondestructive, exanthematic, transient, macular roseolas that may later be maculopapular or papular polymorphous or scaly, pustular, pigmented eruptions.(Arnold, Odom, and James, Andrew's Diseases of the Skin, 8th ed, p409)
Syphilis, Latent
The stage of syphilis that occurs following the primary (CHANCRE) and secondary stages. The patient is asymptomatic at the latent stage but remains seropositive for the SPIROCHETE.
Tabes Dorsalis
Parenchymatous NEUROSYPHILIS marked by slowly progressive degeneration of the posterior columns, posterior roots, and ganglia of the spinal cord. The condition tends to present 15 to 20 years after the initial infection and is characterized by lightening-like pains in the lower extremities, URINARY INCONTINENCE; ATAXIA; severely impaired position and vibratory sense, abnormal gait (see GAIT DISORDERS, NEUROLOGIC), OPTIC ATROPHY; Argyll-Robertson pupils, hypotonia, hyperreflexia, and trophic joint degeneration (Charcot's Joint; see ARTHROPATHY, NEUROGENIC). (From Adams et al., Principles of Neurology, 6th ed, p726)
Treponema pallidum
The causative agent of venereal and non-venereal syphilis as well as yaws.
About the A50 Code Range
ICD-10 code A50 designates congenital syphilis, an infection passed from a pregnant person to their baby. This section includes detailed codes distinguishing early and late stages, symptomatic and latent forms, and specific complications affecting eyes, bones, skin, and the nervous system.
The ICD-10 code for congenital syphilis covers conditions like early congenital syphilitic oculopathy (also known as syphilitic chorioretinitis), osteochondropathy (including arthritis caused by Spirochaetales), and respiratory forms such as syphilitic pneumonia and rhinitis. Late congenital syphilis codes account for ocular issues like interstitial keratitis, neurological diseases including neurosyphilis and juvenile general paresis (taboparesis), as well as classic signs like Hutchinson’s teeth and Clutton’s joints. Recognizing synonyms such as "syphilitic choroiditis" or "moon’s molar teeth" helps link clinical findings to the correct codes. These codes assist healthcare providers and coders in accurately identifying and documenting the wide range of manifestations of congenital syphilis for diagnosis and treatment purposes.
Questions About This Page
How many billable codes are in the A50 range?
Of the 38 codes in this range, 33 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the A50 range classify?
The range classifies congenital syphilis. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
