2026 ICD-10-CM Diagnosis Code Q89.01Asplenia (congenital)

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q89

ICD-10-CM Q89.01
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q89.01 is a billable ICD-10-CM diagnosis code for asplenia (congenital). It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 814 through 816. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q89.01
Billable Status
Yes — Valid for Submission
Code Describes
Asplenia (congenital)
Short Description
Asplenia (congenital)
Same as the full description in the CMS dataset.
Parent Code
Q89.0
Congenital absence and malformations of spleen

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ89Other congenital malformations, not elsewhere classified
This CodeQ89.01Asplenia (congenital)

Present on Admission (POA)Billing

Q89.01 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Agenesis of spleen
  • Aplasia of spleen
  • Asplenia
  • Congenital absence of spleen
  • Congenital diaphragmatic hernia
  • Congenital miosis
  • Congenital short bowel syndrome
  • Constricted pupil
  • Diaphragmatic hernia, short bowel, asplenia syndrome
  • Familial isolated congenital asplenia
  • Functional asplenia
  • Short bowel syndrome
  • Spleen absent
  • Thrombocytopathy, asplenia and miosis

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Absence(of) (organ or part) (complete or partial)
      • spleen (congenital)
    • Agenesis
      • spleen
    • Anomaly, anomalous(congenital) (unspecified type)
      • spleen
        • agenesis
    • Aplasia
      • spleen
    • Asplenia(congenital)
    • Ivemark's syndrome(asplenia with congenital heart disease)
    • Syndrome
      • Ivemark's
    • Syndrome
      • splenic
        • agenesis

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Short Bowel Syndrome

    a malabsorption syndrome resulting from extensive operative resection of the small intestine, the absorptive region of the gastrointestinal tract.

  • Congenital Diaphragmatic Hernia

    diaphragmatic hernia that is present at birth.

  • Short Bowel Syndrome

    malabsorption that results from the removal of a large segment of the small intestine or, less frequently, from the complete dysfunction of a large portion of the small intestine. signs and symptoms include diarrhea, steatorrhea, and weight loss.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q89.01 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
759.0 Anomalies of spleen
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q89.01Overview

Is Q89.01 (Congenital absence and malformations of spleen) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report asplenia (congenital) on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q89.01 group to?

When asplenia (congenital) is the principal diagnosis on an inpatient stay, it groups to MS-DRG 814, 815, 816, with relative weights from 0.6320 to 2.1267 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q89.01 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for asplenia (congenital) on inpatient claims.

What is the ICD-9 equivalent of Q89.01?

Under the General Equivalence Mappings, asplenia (congenital) converts to ICD-9-CM 759.0 (anomalies of spleen). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.